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  3. Q00-Q99
  4. Q20-Q28
  5. Other congenital malformations of circulatory system (Q28)

Other congenital malformations of circulatory system (Q28)

The ICD-10 code section Q28 covers a group of rare, congenital malformations affecting the circulatory system beyond the more common heart defects. These codes are used to classify specific abnormalities in blood vessels, including arteries and veins located in the neck, brain, and trunk.

This section includes distinct codes for conditions such as Q28.0 for arteriovenous malformations of precerebral vessels and Q28.2 for cerebral arteriovenous malformations; also known by terms like vein of Galen malformation or congenital cerebral arteriovenous fistula. The code Q28.1 identifies other malformations of precerebral vessels, which may involve anomalies such as congenital aneurysms or unusual carotid artery formations. Q28.3 addresses various cerebral vessel malformations, including persistent embryonic arteries and congenital aneurysms. Additionally, Q28.8 covers other specified congenital circulatory malformations such as venous-lymphatic malformations and abnormalities of arterial ligaments, while Q28.9 is used for unspecified congenital circulatory malformations. Understanding these codes helps medical coders accurately document complex vascular congenital anomalies beyond standard cardiac defects, aiding in precise diagnosis and treatment planning.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • congenital aneurysm NOS Q27.8
  • congenital coronary aneurysm Q24.5
  • ruptured cerebral arteriovenous malformation I60.8
  • ruptured malformation of precerebral vessels I72.0

Type 2 Excludes

A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  • congenital peripheral aneurysm Q27.8
  • congenital pulmonary aneurysm Q25.79
  • congenital retinal aneurysm Q14.1

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Tetralogy of Fallot

A combination of congenital heart defects consisting of four key features including VENTRICULAR SEPTAL DEFECTS; PULMONARY STENOSIS; RIGHT VENTRICULAR HYPERTROPHY; and a dextro-positioned AORTA. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing CYANOSIS.