Other congenital malformations of circulatory system (Q28) ICD-10-CM
The Q28 code range covers other congenital malformations of circulatory system with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- congenital aneurysm NOS Q27.8
- congenital coronary aneurysm Q24.5
- ruptured cerebral arteriovenous malformation I60.8
- ruptured malformation of precerebral vessels I72.0
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the Q28 Range 7 codes · 6 billable
- Q28 Other congenital malformations of circulatory systemNon-billable
- Q28.0 Arteriovenous malformation of precerebral vessels
- Q28.1 Other malformations of precerebral vessels
- Q28.2 Arteriovenous malformation of cerebral vessels
- Q28.3 Other malformations of cerebral vessels
- Q28.8 Other specified congenital malformations of circulatory system
- Q28.9 Congenital malformation of circulatory system, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q28 range.
Tetralogy of Fallot
A combination of congenital heart defects consisting of four key features including VENTRICULAR SEPTAL DEFECTS; PULMONARY STENOSIS; RIGHT VENTRICULAR HYPERTROPHY; and a dextro-positioned AORTA. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing CYANOSIS.
About the Q28 Code Range
The ICD-10 code section Q28 covers a group of rare, congenital malformations affecting the circulatory system beyond the more common heart defects. These codes are used to classify specific abnormalities in blood vessels, including arteries and veins located in the neck, brain, and trunk.
This section includes distinct codes for conditions such as Q28.0 for arteriovenous malformations of precerebral vessels and Q28.2 for cerebral arteriovenous malformations—also known by terms like vein of Galen malformation or congenital cerebral arteriovenous fistula. The code Q28.1 identifies other malformations of precerebral vessels, which may involve anomalies such as congenital aneurysms or unusual carotid artery formations. Q28.3 addresses various cerebral vessel malformations, including persistent embryonic arteries and congenital aneurysms. Additionally, Q28.8 covers other specified congenital circulatory malformations such as venous-lymphatic malformations and abnormalities of arterial ligaments, while Q28.9 is used for unspecified congenital circulatory malformations. Understanding these codes helps medical coders accurately document complex vascular congenital anomalies beyond standard cardiac defects, aiding in precise diagnosis and treatment planning.
Questions About This Page
How many billable codes are in the Q28 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q28 range classify?
The range classifies other congenital malformations of circulatory system. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
