2021 ICD-10-CM Code Q26

Congenital malformations of great veins

Version 2021
Non-Billable Code

Not Valid for Submission

Q26 is a "header" nonspecific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of congenital malformations of great veins. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

ICD-10:Q26
Short Description:Congenital malformations of great veins
Long Description:Congenital malformations of great veins

Code Classification

Specific Coding for Congenital malformations of great veins

Header codes like Q26 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for congenital malformations of great veins:

  • Q26.0 - Congenital stenosis of vena cava
  • Q26.1 - Persistent left superior vena cava
  • Q26.2 - Total anomalous pulmonary venous connection
  • Q26.3 - Partial anomalous pulmonary venous connection
  • Q26.4 - Anomalous pulmonary venous connection, unspecified
  • Q26.5 - Anomalous portal venous connection
  • Q26.6 - Portal vein-hepatic artery fistula
  • Q26.8 - Other congenital malformations of great veins
  • Q26.9 - Congenital malformation of great vein, unspecified

Information for Patients


Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute


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Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)