Congenital malformations of great arteries (Q25) ICD-10-CM
The Q25 code range covers congenital malformations of great arteries with 26 ICD-10-CM diagnosis codes. 22 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the Q25 Range 26 codes · 22 billable
- Q25 Congenital malformations of great arteriesNon-billable
- Q25.0 Patent ductus arteriosus
- Q25.1 Coarctation of aorta
- Q25.2 Atresia of aortaNon-billable
- Q25.21 Interruption of aortic arch
- Q25.29 Other atresia of aorta
- Q25.3 Supravalvular aortic stenosis
- Q25.4 Other congenital malformations of aortaNon-billable
- Q25.40 Congenital malformation of aorta unspecified
- Q25.41 Absence and aplasia of aorta
- Q25.42 Hypoplasia of aorta
- Q25.43 Congenital aneurysm of aorta
- Q25.44 Congenital dilation of aorta
- Q25.45 Double aortic arch
- Q25.46 Tortuous aortic arch
- Q25.47 Right aortic arch
- Q25.48 Anomalous origin of subclavian artery
- Q25.49 Other congenital malformations of aorta
- Q25.5 Atresia of pulmonary artery
- Q25.6 Stenosis of pulmonary artery
- Q25.7 Other congenital malformations of pulmonary arteryNon-billable
- Q25.71 Coarctation of pulmonary artery
- Q25.72 Congenital pulmonary arteriovenous malformation
- Q25.79 Other congenital malformations of pulmonary artery
- Q25.8 Other congenital malformations of other great arteries
- Q25.9 Congenital malformation of great arteries, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q25 range.
Aortic Coarctation
A birth defect characterized by the narrowing of the AORTA that can be of varying degree and at any point from the transverse arch to the iliac bifurcation. Aortic coarctation causes arterial HYPERTENSION before the point of narrowing and arterial HYPOTENSION beyond the narrowed portion.
Aortic Stenosis, Supravalvular
A pathological constriction occurring in the region above the AORTIC VALVE. It is characterized by restricted outflow from the LEFT VENTRICLE into the AORTA.
Ductus Arteriosus, Patent
A congenital heart defect characterized by the persistent opening of fetal DUCTUS ARTERIOSUS that connects the PULMONARY ARTERY to the descending aorta (AORTA, DESCENDING) allowing unoxygenated blood to bypass the lung and flow to the PLACENTA. Normally, the ductus is closed shortly after birth.
Right Aortic Arch
An anatomic abnormality that occurs during embryonic development, in which the aortic arch is right-sided.
About the Q25 Code Range
These conditions are present at birth and affect the great arteries, including the aorta and pulmonary artery.
The subdivisions separate a patent ductus arteriosus from malformations of the aorta, pulmonary artery, and other great arteries. The aortic codes distinguish coarctation, atresia, narrowing above the valve, and other malformations. Within Q25.2, the titles separate interruption of the aortic arch from other aortic atresia. Q25.4 has more specific codes for aortic absence, underdevelopment, dilation, arch differences, and an unusual origin of the subclavian artery. The pulmonary artery codes distinguish atresia, narrowing, and other malformations; Q25.9 leaves the great artery malformation unspecified.
Questions About This Page
How many billable codes are in the Q25 range?
Of the 26 codes in this range, 22 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q25 range classify?
The range classifies congenital malformations of great arteries. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
