Congenital malformations of great arteries (Q25) ICD-10-CM
The Q25 code range covers congenital malformations of great arteries with 26 ICD-10-CM diagnosis codes. 22 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q25 Range 26 codes · 22 billable
- Q25 Congenital malformations of great arteriesNon-billable
- Q25.0 Patent ductus arteriosus
- Q25.1 Coarctation of aorta
- Q25.2 Atresia of aortaNon-billable
- Q25.21 Interruption of aortic arch
- Q25.29 Other atresia of aorta
- Q25.3 Supravalvular aortic stenosis
- Q25.4 Other congenital malformations of aortaNon-billable
- Q25.40 Congenital malformation of aorta unspecified
- Q25.41 Absence and aplasia of aorta
- Q25.42 Hypoplasia of aorta
- Q25.43 Congenital aneurysm of aorta
- Q25.44 Congenital dilation of aorta
- Q25.45 Double aortic arch
- Q25.46 Tortuous aortic arch
- Q25.47 Right aortic arch
- Q25.48 Anomalous origin of subclavian artery
- Q25.49 Other congenital malformations of aorta
- Q25.5 Atresia of pulmonary artery
- Q25.6 Stenosis of pulmonary artery
- Q25.7 Other congenital malformations of pulmonary arteryNon-billable
- Q25.71 Coarctation of pulmonary artery
- Q25.72 Congenital pulmonary arteriovenous malformation
- Q25.79 Other congenital malformations of pulmonary artery
- Q25.8 Other congenital malformations of other great arteries
- Q25.9 Congenital malformation of great arteries, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q25 range.
Endarteritis
Inflammation of the inner endothelial lining (TUNICA INTIMA) of an artery.
Prune Belly Syndrome
A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin.
Tetralogy of Fallot
A combination of congenital heart defects consisting of four key features including VENTRICULAR SEPTAL DEFECTS; PULMONARY STENOSIS; RIGHT VENTRICULAR HYPERTROPHY; and a dextro-positioned AORTA. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing CYANOSIS.
Tunica Intima
The innermost layer of an artery or vein, made up of one layer of endothelial cells and supported by an internal elastic lamina.
About the Q25 Code Range
The ICD-10 code section Q25 is designated for congenital malformations of the great arteries, which include various structural heart defects present from birth affecting the aorta and pulmonary arteries. These codes are used to classify specific anomalies such as patent ductus arteriosus, coarctation of the aorta, and atresia or stenosis of the aorta and pulmonary arteries.
The ICD-10 code for congenital malformations of great arteries covers distinct conditions. For example, Q25.0 is specifically used for patent ductus arteriosus, a condition also known by synonyms like familial patent arterial duct and delayed closure of patent arterial duct. Q25.1 identifies coarctation of aorta, including variants such as preductal coarctation. Atresia and stenosis of the aorta and pulmonary artery are coded under Q25.2, Q25.3, Q25.5, and Q25.6. Other codes in this section, such as Q25.45 for double aortic arch or Q25.47 for right aortic arch, help capture more complex or uncommon malformations. These precise codes assist medical coders in accurately identifying congenital heart defects that influence diagnosis, treatment, and medical records, ensuring alignment with clinical terminology including common synonyms like ductus arteriosus aneurysm or interrupted aortic arch.
Questions About This Page
How many billable codes are in the Q25 range?
Of the 26 codes in this range, 22 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q25 range classify?
The range classifies congenital malformations of great arteries. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
