Other congenital malformations of peripheral vascular system (Q27)
ICD-10 code Q27 covers a group of rare congenital malformations affecting the peripheral vascular system, which includes arteries and veins outside the heart and central vessels. These codes are used to classify conditions where the blood vessels are abnormally formed from birth, which can impact blood flow in limbs, kidneys, digestive organs, and the umbilical cord.
The category includes specific abnormalities like Q27.0 for congenital absence or underdevelopment of the umbilical artery, often known as single umbilical artery. Q27.1 and Q27.2 address congenital stenosis or malformations of the renal arteries, crucial for kidney circulation. Codes in the Q27.3 series describe various arteriovenous malformations (AVMs) in peripheral vessels, with sites detailed from limbs (upper limb, Q27.31; lower limb, Q27.32) to renal vessels (Q27.34) and digestive system vessels (Q27.33). Other specified vascular anomalies, including vascular rings or unusual arterial origins, fall under Q27.8. If the exact site or nature is not specified, Q27.9 is used. Recognizing these coding options helps clinicians and coders accurately document congenital vascular anomalies, improving patient care and research on peripheral vascular malformations.
Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Congenital malformations of the circulatory system (Q20-Q28)
Q27 Other congenital malformations of peripheral vascular system
- Q27.0 Congenital absence and hypoplasia of umbilical artery
- Q27.1 Congenital renal artery stenosis
- Q27.2 Other congenital malformations of renal artery
Q27.3 Arteriovenous malformation (peripheral)
- Q27.30 Arteriovenous malformation, site unspecified
- Q27.31 Arteriovenous malformation of vessel of upper limb
- Q27.32 Arteriovenous malformation of vessel of lower limb
- Q27.33 Arteriovenous malformation of digestive system vessel
- Q27.34 Arteriovenous malformation of renal vessel
- Q27.39 Arteriovenous malformation, other site
- Q27.4 Congenital phlebectasia
- Q27.8 Other specified congenital malformations of peripheral vascular system
- Q27.9 Congenital malformation of peripheral vascular system, unspecified
Other congenital malformations of peripheral vascular system (Q27)
Instructional Notations
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- anomalies of cerebral and precerebral vessels Q28.0 Q28.3
- anomalies of coronary vessels Q24.5
- anomalies of pulmonary artery Q25.5 Q25.7
- congenital retinal aneurysm Q14.1
- hemangioma and lymphangioma D18
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Single Umbilical Artery
Congenital abnormality where one, instead of the usual two, UMBILICAL ARTERY connects the fetus to the placenta.
Umbilical Arteries
Specialized arterial vessels in the umbilical cord. They carry waste and deoxygenated blood from the FETUS to the mother via the PLACENTA. In humans, there are usually two umbilical arteries but sometimes one.
