Other congenital malformations of peripheral vascular system (Q27) ICD-10-CM
The Q27 code range covers other congenital malformations of peripheral vascular system with 14 ICD-10-CM diagnosis codes. 12 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the Q27 Range 14 codes · 12 billable
- Q27 Other congenital malformations of peripheral vascular systemNon-billable
- Q27.0 Congenital absence and hypoplasia of umbilical artery
- Q27.1 Congenital renal artery stenosis
- Q27.2 Other congenital malformations of renal artery
- Q27.3 Arteriovenous malformation (peripheral)Non-billable
- Q27.30 Arteriovenous malformation, site unspecified
- Q27.31 Arteriovenous malformation of vessel of upper limb
- Q27.32 Arteriovenous malformation of vessel of lower limb
- Q27.33 Arteriovenous malformation of digestive system vessel
- Q27.34 Arteriovenous malformation of renal vessel
- Q27.39 Arteriovenous malformation, other site
- Q27.4 Congenital phlebectasia
- Q27.8 Other specified congenital malformations of peripheral vascular system
- Q27.9 Congenital malformation of peripheral vascular system, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q27 range.
Single Umbilical Artery
Congenital abnormality where one, instead of the usual two, UMBILICAL ARTERY connects the fetus to the placenta.
Umbilical Arteries
Specialized arterial vessels in the umbilical cord. They carry waste and deoxygenated blood from the FETUS to the mother via the PLACENTA. In humans, there are usually two umbilical arteries but sometimes one.
About the Q27 Code Range
ICD-10 code Q27 covers a group of rare congenital malformations affecting the peripheral vascular system, which includes arteries and veins outside the heart and central vessels. These codes are used to classify conditions where the blood vessels are abnormally formed from birth, which can impact blood flow in limbs, kidneys, digestive organs, and the umbilical cord.
The category includes specific abnormalities like Q27.0 for congenital absence or underdevelopment of the umbilical artery, often known as single umbilical artery. Q27.1 and Q27.2 address congenital stenosis or malformations of the renal arteries, crucial for kidney circulation. Codes in the Q27.3 series describe various arteriovenous malformations (AVMs) in peripheral vessels, with sites detailed from limbs (upper limb, Q27.31; lower limb, Q27.32) to renal vessels (Q27.34) and digestive system vessels (Q27.33). Other specified vascular anomalies, including vascular rings or unusual arterial origins, fall under Q27.8. If the exact site or nature is not specified, Q27.9 is used. Recognizing these coding options helps clinicians and coders accurately document congenital vascular anomalies, improving patient care and research on peripheral vascular malformations.
Questions About This Page
How many billable codes are in the Q27 range?
Of the 14 codes in this range, 12 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q27 range classify?
The range classifies other congenital malformations of peripheral vascular system. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
