Congenital malformations of aortic and mitral valves (Q23) ICD-10-CM
The Q23 code range covers congenital malformations of aortic and mitral valves with 11 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the Q23 Range 11 codes · 9 billable
- Q23 Congenital malformations of aortic and mitral valvesNon-billable
- Q23.0 Congenital stenosis of aortic valve
- Q23.1 Congenital insufficiency of aortic valve
- Q23.2 Congenital mitral stenosis
- Q23.3 Congenital mitral insufficiency
- Q23.4 Hypoplastic left heart syndrome
- Q23.8 Other congenital malformations of aortic and mitral valvesNon-billable
- Q23.81 Bicuspid aortic valve
- Q23.82 Congenital mitral valve cleft leaflet
- Q23.88 Other congenital malformations of aortic and mitral valves
- Q23.9 Congenital malformation of aortic and mitral valves, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q23 range.
Bicuspid Aortic Valve Disease
Congenital heart valve defects where the AORTIC VALVE has two instead of normal three cusps. It is often associated with AORTIC REGURGITATION and AORTIC INSUFFICIENCY.
Congenital Aortic Valve Insufficiency
Dysfunction of the aortic valve characterized by incomplete valve closure that is present at birth.
Congenital Aortic Valve Stenosis
Aortic valve stenosis that is present at birth.
Congenital Mitral Insufficiency
Mitral valve insufficiency that is present at birth.
Congenital Mitral Stenosis
Mitral valve stenosis that is present at birth.
Hypoplastic Left Heart Syndrome
A condition caused by underdevelopment of the whole left half of the heart. It is characterized by hypoplasia of the left cardiac chambers (HEART ATRIUM; HEART VENTRICLE), the AORTA, the AORTIC VALVE, and the MITRAL VALVE. Severe symptoms appear in early infancy when DUCTUS ARTERIOSUS closes.
Quadricuspid Aortic Valve
Congenital malformation where the AORTIC VALVE has four instead of three cusps. It is often associated with AORTIC REGURGITATION and AORTIC VALVE STENOSIS.
About the Q23 Code Range
These conditions are present at birth and affect the aortic or mitral valves, or involve an underdeveloped left side of the heart.
Q23.0 and Q23.2 distinguish aortic from mitral valve stenosis, or narrowing. Q23.1 and Q23.3 make the same valve distinction for insufficiency, when a valve does not close fully. Q23.4 identifies hypoplastic left heart syndrome.
Q23.8 groups other valve malformations, with subdivisions for a bicuspid aortic valve, a cleft mitral valve leaflet, and other malformations. Q23.9 identifies an unspecified malformation.
Questions About This Page
How many billable codes are in the Q23 range?
Of the 11 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q23 range classify?
The range classifies congenital malformations of aortic and mitral valves. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
