2027 ICD-10-CM Diagnosis Code Q25Congenital malformations of great arteries

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25 is a non-billable ICD-10-CM category code for congenital malformations of great arteries, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q25.0, Q25.1, Q25.21, and Q25.29.

Code Identity

ICD-10-CM Code
Q25
Billable Status
No — Non-Billable Category
Code Describes
Congenital malformations of great arteries
Short Description
Congenital malformations of great arteries
Same as the full description in the CMS dataset.
Chapter
Q20-Q28
Congenital malformations of the circulatory system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25Congenital malformations of great arteries

Specific Coding for Congenital malformations of great arteriesOverview

Non-specific codes like Q25 require more characters. Use one of these billable codes instead:

  • Use Q25.0 for Patent ductus arteriosus

  • Use Q25.1 for Coarctation of aorta

  • Q25.2 for Atresia of aorta

  • Use Q25.21 for Interruption of aortic arch

  • Use Q25.29 for Other atresia of aorta

  • Use Q25.3 for Supravalvular aortic stenosis

  • Q25.4 for Other congenital malformations of aorta

  • Use Q25.40 for Congenital malformation of aorta unspecified

  • Use Q25.41 for Absence and aplasia of aorta

  • Use Q25.42 for Hypoplasia of aorta

  • Use Q25.43 for Congenital aneurysm of aorta

  • Use Q25.44 for Congenital dilation of aorta

  • Use Q25.45 for Double aortic arch

  • Use Q25.46 for Tortuous aortic arch

  • Use Q25.47 for Right aortic arch

  • Use Q25.48 for Anomalous origin of subclavian artery

  • Use Q25.49 for Other congenital malformations of aorta

  • Use Q25.5 for Atresia of pulmonary artery

  • Use Q25.6 for Stenosis of pulmonary artery

  • Q25.7 for Other congenital malformations of pulmonary artery

  • Use Q25.71 for Coarctation of pulmonary artery

  • Use Q25.72 for Congenital pulmonary arteriovenous malformation

  • Use Q25.79 for Other congenital malformations of pulmonary artery

  • Use Q25.8 for Other congenital malformations of other great arteries

  • Use Q25.9 for Congenital malformation of great arteries, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25Overview

What is the ICD-10 code for congenital malformations of great arteries?

Q25 is the ICD-10-CM category for congenital malformations of great arteries, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q25 (Congenital malformations of great arteries) a billable code?

No. This is a category header that groups the codes for congenital malformations of great arteries, and headers cannot be submitted on claims. Claims for congenital malformations of great arteries need a more specific code from this category, such as Q25.0, Q25.1, and Q25.21.