2026 ICD-10-CM Diagnosis Code G11.8Other hereditary ataxias

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11.8
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G11.8 is a billable ICD-10-CM diagnosis code for other hereditary ataxias. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G11.8
Billable Status
Yes — Valid for Submission
Code Describes
Other hereditary ataxias
Short Description
Other hereditary ataxias
Same as the full description in the CMS dataset.
Parent Code
G11
Hereditary ataxia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11.8Other hereditary ataxias

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 4H leukodystrophy
  • Abnormal saccadic eye movement
  • Acute hepatic failure
  • Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome
  • Arts syndrome
  • Ataxia pancytopenia syndrome
  • Ataxia, photosensitivity, short stature syndrome
  • Autosomal dominant cerebellar ataxia type 2
  • Autosomal recessive cerebellar ataxia Beauce type
  • Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency
  • Autosomal recessive cerebellar ataxia with saccadic intrusion syndrome
  • Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX deficiency
  • Autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome
  • Autosomal recessive cerebelloparenchymal disorder type 3
  • Autosomal recessive spinocerebellar ataxia, blindness, deafness syndrome
  • Bailey-Cushing syndrome
  • CAMOS syndrome
  • Cerebellar ataxia Cayman type
  • Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome
  • CLCN2-related leukoencephalopathy
  • Congenital atrophy of optic nerve
  • Congenital cerebellar ataxia due to RNU12 mutation
  • Congenital non-progressive ataxia
  • Episodic ataxia
  • Episodic ataxia type 1
  • Episodic ataxia type 2
  • Episodic ataxia type 3
  • Episodic ataxia type 4
  • Episodic ataxia type 5
  • Episodic ataxia type 6
  • Episodic ataxia with slurred speech
  • Finding of intelligibility of articulation
  • Hereditary cerebellar atrophy
  • Intellectual disability, hyperkinetic movement, truncal ataxia syndrome
  • Jervis' syndrome
  • Late tooth eruption
  • Leukoencephalopathy, ataxia, hypodontia, hypomyelination syndrome
  • Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
  • Neuhauser Eichner Opitz syndrome
  • Neurodevelopmental delay, intellectual disability, ataxia, feeding difficulty syndrome
  • Non-progressive cerebellar ataxia
  • Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
  • Progressive truncal ataxia
  • Recessive mitochondrial ataxia syndrome
  • Richards-Rundle syndrome
  • Sanger-Brown cerebellar ataxia
  • Severe intellectual disability, agenesis of corpus callosum, facial dysmorphism, cerebellar ataxia syndrome
  • Slurred speech
  • Speech delay
  • Spinocerebellar ataxia dysmorphism syndrome
  • Spinocerebellar ataxia type 1
  • Spinocerebellar ataxia type 10
  • Spinocerebellar ataxia type 11
  • Spinocerebellar ataxia type 12
  • Spinocerebellar ataxia type 13
  • Spinocerebellar ataxia type 14
  • Spinocerebellar ataxia type 15/16
  • Spinocerebellar ataxia type 17
  • Spinocerebellar ataxia type 18
  • Spinocerebellar ataxia type 19
  • Spinocerebellar ataxia type 2
  • Spinocerebellar ataxia type 20
  • Spinocerebellar ataxia type 21
  • Spinocerebellar ataxia type 23
  • Spinocerebellar ataxia type 25
  • Spinocerebellar ataxia type 26
  • Spinocerebellar ataxia type 27
  • Spinocerebellar ataxia type 28
  • Spinocerebellar ataxia type 29
  • Spinocerebellar ataxia type 30
  • Spinocerebellar ataxia type 31
  • Spinocerebellar ataxia type 32
  • Spinocerebellar ataxia type 34
  • Spinocerebellar ataxia type 35
  • Spinocerebellar ataxia type 36
  • Spinocerebellar ataxia type 37
  • Spinocerebellar ataxia type 38
  • Spinocerebellar ataxia type 4
  • Spinocerebellar ataxia type 40
  • Spinocerebellar ataxia type 41
  • Spinocerebellar ataxia type 42
  • Spinocerebellar ataxia type 43
  • Spinocerebellar ataxia type 5
  • Spinocerebellar ataxia type 6
  • Spinocerebellar ataxia type 7
  • Spinocerebellar ataxia type 8
  • Spinocerebellar ataxia with axonal neuropathy type 1
  • Third cranial nerve finding
  • Truncal ataxia
  • Unintelligible articulation

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Ataxia, ataxy, ataxic
      • hereditary
        • specified NEC
    • Disease, diseased
      • spinocerebellar (hereditary)
        • specified NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Ataxin-7|ATXN7|Ataxin 7|Spinocerebellar Ataxia Type 7 Protein

    ataxin-7 (892 aa, ~95 kda) is encoded by the human atxn7 gene. this protein is involved in the regulation of histone acetylation and chromatin remodeling.

  • Spinocerebellar Ataxia Type 7

    an autosomal dominant inherited neurodegenerative disorder caused by mutations in the atxn7 gene. it is characterized by progressive cerebellar ataxia, including dysarthria and dysphagia, cone-rod and retinal dystrophy, and progressive central visual loss resulting in blindness.

Patient EducationClinical

Cerebellar Disorders

When you play the piano or hit a tennis ball you are activating the cerebellum. The cerebellum is the area of the brain that controls coordination and balance. Problems with the cerebellum include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G11.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
334.8 Spinocerebellar dis NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G11.8Overview

Is G11.8 (Hereditary ataxia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other hereditary ataxias on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G11.8?

Under the General Equivalence Mappings, other hereditary ataxias converts to ICD-9-CM 334.8 (spinocerebellar dis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.