Valid for Submission
R27.0 is a billable diagnosis code used to specify a medical diagnosis of ataxia, unspecified. The code R27.0 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions.
The ICD-10-CM code R27.0 might also be used to specify conditions or terms like abetalipoproteinemia, acquired ataxia, acute cerebellar ataxia due to varicella, arms ataxic, ataxia , ataxia co-occurrent and due to abetalipoproteinemia, etc.
Unspecified diagnosis codes like R27.0 are acceptable when clinical information is unknown or not available about a particular condition. Although a more specific code is preferable, unspecified codes should be used when such codes most accurately reflect what is known about a patient's condition. Specific diagnosis codes should not be used if not supported by the patient's medical record.
According to ICD-10-CM guidelines this code should not to be used as a principal diagnosis code when a related definitive diagnosis has been established.
Tabular List of Diseases and Injuries
The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code R27.0:
Type 1 ExcludesType 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- ataxia following cerebrovascular disease (I69. with final characters -93)
Index to Diseases and Injuries
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code R27.0 are found in the index:
- - Ataxia, ataxy, ataxic - R27.0
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Acquired ataxia
- Acute cerebellar ataxia due to varicella
- Arms ataxic
- Ataxia co-occurrent and due to abetalipoproteinemia
- Ataxia co-occurrent and due to cerebrotendinous xanthomatosis
- Ataxia co-occurrent and due to phytanic acid storage disease
- Ataxia with vitamin E deficiency
- Ataxic hemiparesis
- Benign paroxysmal tonic upgaze of childhood with ataxia
- Cerebellar ataxia due to toxin
- Cholestanol storage disease
- Disorder of cholesterol catabolism
- Disorder of cholesterol metabolism
- Drug-induced cerebellar ataxia
- HSMN IV
- Intermittent ataxia
- Legs ataxic
- Motor ataxia
- Muscular atrophy, ataxia, retinitis pigmentosa, and diabetes mellitus
- Neurogenic muscle weakness, ataxia and retinitis pigmentosa
- Nutritional ataxic neuropathy
- O/E - arms ataxic
- O/E - ataxia
- O/E - legs ataxic
- Oral motor ataxia
- Progressive myoclonus epilepsy with ataxia
- Secondary cerebellar degeneration
- Secondary cerebellar degeneration
- Sensory ataxia
- Single limb ataxia
- Static ataxia
- Synthetic defect of bile acids
- Truncal ataxia
- ATAXINS-. a family of predominantly nuclear proteins that regulate gene transcription and protein degradation. the expansion of cag trinucleotide repeats in genes that encode ataxins is associated with spinocerebellar ataxias sca. in sca patients the number of cag repeats correlates with the severity of disease and inversely correlates with the age of disease onset.
- ATAXIA-. impairment of the ability to perform smoothly coordinated voluntary movements. this condition may affect the limbs trunk eyes pharynx larynx and other structures. ataxia may result from impaired sensory or motor function. sensory ataxia may result from posterior column injury or peripheral nerve diseases. motor ataxia may be associated with cerebellar diseases; cerebral cortex diseases; thalamic diseases; basal ganglia diseases; injury to the red nucleus; and other conditions.
- ATAXIA TELANGIECTASIA-. an autosomal recessive inherited disorder characterized by choreoathetosis beginning in childhood progressive cerebellar ataxia; telangiectasis of conjunctiva and skin; dysarthria; b and t cell immunodeficiency and radiosensitivity to ionizing radiation. affected individuals are prone to recurrent sinobronchopulmonary infections lymphoreticular neoplasms and other malignancies. serum alpha fetoproteins are usually elevated. menkes textbook of child neurology 5th ed p688 the gene for this disorder atm encodes a cell cycle checkpoint protein kinase and has been mapped to chromosome 11 11q22 q23.
- CEREBELLAR ATAXIA-. incoordination of voluntary movements that occur as a manifestation of cerebellar diseases. characteristic features include a tendency for limb movements to overshoot or undershoot a target dysmetria a tremor that occurs during attempted movements intention tremor impaired force and rhythm of diadochokinesis rapidly alternating movements and gait ataxia. from adams et al. principles of neurology 6th ed p90
- MYOCLONIC CEREBELLAR DYSSYNERGIA-. a condition marked by progressive cerebellar ataxia combined with myoclonus usually presenting in the third decade of life or later. additional clinical features may include generalized and focal seizures spasticity and dyskinesias. autosomal recessive and autosomal dominant patterns of inheritance have been reported. pathologically the dentate nucleus and brachium conjunctivum of the cerebellum are atrophic with variable involvement of the spinal cord cerebellar cortex and basal ganglia. from joynt clinical neurology 1991 ch37 pp60 1
- FELINE PANLEUKOPENIA-. a highly contagious dna virus infection of the cat family characterized by fever enteritis and bone marrow changes. it is also called feline ataxia feline agranulocytosis feline infectious enteritis cat fever cat plague and show fever. it is caused by feline panleukopenia virus or the closely related mink enteritis virus or canine parvovirus.
- FRIEDREICH ATAXIA-. an autosomal recessive disease usually of childhood onset characterized pathologically by degeneration of the spinocerebellar tracts posterior columns and to a lesser extent the corticospinal tracts. clinical manifestations include gait ataxia pes cavus speech impairment lateral curvature of spine rhythmic head tremor kyphoscoliosis congestive heart failure secondary to a cardiomyopathy and lower extremity weakness. most forms of this condition are associated with a mutation in a gene on chromosome 9 at band q13 which codes for the mitochondrial protein frataxin. from adams et al. principles of neurology 6th ed p1081; n engl j med 1996 oct 17;33516:1169 75 the severity of friedreich ataxia associated with expansion of gaa repeats in the first intron of the frataxin gene correlates with the number of trinucleotide repeats. from durr et al n engl j med 1996 oct 17;33516:1169 75
- OLIVOPONTOCEREBELLAR ATROPHIES-. a group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the cerebellum; pons; and inferior olivary nuclei. additional clinical features may include muscle rigidity; nystagmus pathologic; retinal degeneration; muscle spasticity; dementia; urinary incontinence; and ophthalmoplegia. the familial form has an earlier onset second decade and may feature spinal cord atrophy. the sporadic form tends to present in the fifth or sixth decade and is considered a clinical subtype of multiple system atrophy. from adams et al. principles of neurology 6th ed p1085
- SPINOCEREBELLAR DEGENERATIONS-. a heterogenous group of degenerative syndromes marked by progressive cerebellar dysfunction either in isolation or combined with other neurologic manifestations. sporadic and inherited subtypes occur. inheritance patterns include autosomal dominant autosomal recessive and x linked.
- SWAYBACK-. congenital locomotor ataxia of lambs thought to be associated with copper deficiency. it is characterized clinically by progressive incoordination of the hind limbs and pathologically by disruption of neuron and myelin development in the central nervous system. it is caused by a deficiency of metabolizable copper in the ewe during the last half of her pregnancy. dorland 28th ed; stedman 26th ed
- TABES DORSALIS-. parenchymatous neurosyphilis marked by slowly progressive degeneration of the posterior columns posterior roots and ganglia of the spinal cord. the condition tends to present 15 to 20 years after the initial infection and is characterized by lightening like pains in the lower extremities urinary incontinence; ataxia; severely impaired position and vibratory sense abnormal gait see gait disorders neurologic optic atrophy; argyll robertson pupils hypotonia hyperreflexia and trophic joint degeneration charcot's joint; see arthropathy neurogenic. from adams et al. principles of neurology 6th ed p726
- PYRUVATE CARBOXYLASE DEFICIENCY DISEASE-. an autosomal recessive metabolic disorder caused by absent or decreased pyruvate carboxylase activity the enzyme that regulates gluconeogenesis lipogenesis and neurotransmitter synthesis. clinical manifestations include lactic acidosis seizures respiratory distress marked psychomotor delay periodic hypoglycemia and hypotonia. the clinical course may be similar to leigh disease. from am j hum genet 1998 jun;626:1312 9
- PYRUVATE DEHYDROGENASE COMPLEX DEFICIENCY DISEASE-. an inherited metabolic disorder caused by deficient enzyme activity in the pyruvate dehydrogenase complex resulting in deficiency of acetyl coa and reduced synthesis of acetylcholine. two clinical forms are recognized: neonatal and juvenile. the neonatal form is a relatively common cause of lactic acidosis in the first weeks of life and may also feature an erythematous rash. the juvenile form presents with lactic acidosis alopecia intermittent ataxia; seizures; and an erythematous rash. from j inherit metab dis 1996;194:452 62 autosomal recessive and x linked forms are caused by mutations in the genes for the three different enzyme components of this multisubunit pyruvate dehydrogenase complex. one of the mutations at xp22.2 p22.1 in the gene for the e1 alpha component of the complex leads to leigh disease.
- MACHADO JOSEPH DISEASE-. a dominantly inherited ataxia first described in people of azorean and portuguese descent and subsequently identified in brazil japan china and australia. this disorder is classified as one of the spinocerebellar ataxias type 3 and has been associated with a mutation of the mjd1 gene on chromosome 14. clinical features include progressive ataxia dysarthria postural instability nystagmus eyelid retraction and facial fasciculations. dystonia is prominent in younger patients referred to as type i machado joseph disease. type ii features ataxia and ocular signs; type iii features muscular atrophy and a sensorimotor neuropathy; and type iv features extrapyramidal signs combined with a sensorimotor neuropathy. from clin neurosci 1995;31:17 22; ann neurol 1998 mar;433:288 96
- MYOCLONIC EPILEPSIES PROGRESSIVE-. a heterogeneous group of primarily familial epilepsy disorders characterized by myoclonic seizures tonic clonic seizures ataxia progressive intellectual deterioration and neuronal degeneration. these include lafora disease; merrf syndrome; neuronal ceroid lipofuscinosis; sialidosis see mucolipidoses and unverricht lundborg syndrome.
- GAIT ATAXIA-. impairment of the ability to coordinate the movements required for normal ambulation walking which may result from impairments of motor function or sensory feedback. this condition may be associated with brain diseases including cerebellar diseases and basal ganglia diseases; spinal cord diseases; or peripheral nervous system diseases.
- SPINOCEREBELLAR ATAXIAS-. a group of dominantly inherited predominately late onset cerebellar ataxias which have been divided into multiple subtypes based on clinical features and genetic mapping. progressive ataxia is a central feature of these conditions and in certain subtypes polyneuropathy; dysarthria; visual loss; and other disorders may develop. from joynt clinical neurology 1997 ch65 pp 12 17; j neuropathol exp neurol 1998 jun;576:531 43
- NIJMEGEN BREAKAGE SYNDROME-. a chromosome instability syndrome resulting from a defective response to dna double strand breaks. in addition to characteristic facies and microcephaly patients have a range of findings including radiosensitivity immunodeficiency increased cancer risk and growth retardation. causative mutations occur in the nbs1 gene located on human chromosome 8q21. nbs1 codes for nibrin the key regulator protein of the r/m/n rad50/mre11/nbs1 protein complex which senses and mediates cellular response to dna damage caused by ionizing radiation.
- ATAXIA TELANGIECTASIA MUTATED PROTEINS-. a group of protein serine threonine kinases which activate critical signaling cascades in double strand breaks apoptosis and genotoxic stress such as ionizing ultraviolet a light thereby acting as a dna damage sensor. these proteins play a role in a wide range of signaling mechanisms in cell cycle control.
Convert R27.0 to ICD-9 Code
The General Equivalency Mapping (GEM) crosswalk indicates an approximate mapping between the ICD-10 code R27.0 its ICD-9 equivalent. The approximate mapping means there is not an exact match between the ICD-10 code and the ICD-9 code and the mapped code is not a precise representation of the original code.
Information for Patients
Movement disorders are neurologic conditions that cause problems with movement, such as
- Increased movement that can be voluntary (intentional) or involuntary (unintended)
- Decreased or slow voluntary movement
There are many different movement disorders. Some of the more common types include
- Ataxia, the loss of muscle coordination
- Dystonia, in which involuntary contractions of your muscles cause twisting and repetitive movements. The movements can be painful.
- Huntington's disease, an inherited disease that causes nerve cells in certain parts of the brain to waste away. This includes the nerve cells that help to control voluntary movement.
- Parkinson's disease, which is disorder that slowly gets worse over time. It causes tremors, slowness of movement, and trouble walking.
- Tourette syndrome, a condition which causes people to make sudden twitches, movements, or sounds (tics)
- Tremor and essential tremor, which cause involuntary trembling or shaking movements. The movements may be in one or more parts of your body.
Causes of movement disorders include
- Damage to the brain, spinal cord, or peripheral nerves
- Metabolic disorders
- Stroke and vascular diseases
Treatment varies by disorder. Medicines can cure some disorders. Others get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms and relieve pain.
- Angelman syndrome (Medical Encyclopedia)
- Chronic motor tic disorder (Medical Encyclopedia)
- Facial tics (Medical Encyclopedia)
- Movement - uncontrollable (Medical Encyclopedia)
- Movement - uncontrolled or slow (Medical Encyclopedia)
- Movement - uncoordinated (Medical Encyclopedia)
- Movement - unpredictable or jerky (Medical Encyclopedia)
- Neurodegeneration with brain iron accumulation (NBIA) (Medical Encyclopedia)
- Tardive dyskinesia (Medical Encyclopedia)