2027 ICD-10-CM Diagnosis Code G11Hereditary ataxia

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G11 is a non-billable ICD-10-CM category code for hereditary ataxia, so it cannot be submitted on claims. Use a more specific code from this category instead, such as G11.0, G11.10, G11.11, and G11.19.

Code Identity

ICD-10-CM Code
G11
Billable Status
No — Non-Billable Category
Code Describes
Hereditary ataxia
Short Description
Hereditary ataxia
Same as the full description in the CMS dataset.
Chapter
G10-G14
Systemic atrophies primarily affecting the central nervous system

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11Hereditary ataxia

Specific Coding for Hereditary ataxiaOverview

Non-specific codes like G11 require more characters. Use one of these billable codes instead:

  • Use G11.0 for Congenital nonprogressive ataxia

  • G11.1 for Early-onset cerebellar ataxia

  • Use G11.10 for Early-onset cerebellar ataxia, unspecified

  • Use G11.11 for Friedreich ataxia

  • Use G11.19 for Other early-onset cerebellar ataxia

  • Use G11.2 for Late-onset cerebellar ataxia

  • Use G11.3 for Cerebellar ataxia with defective DNA repair

  • Use G11.4 for Hereditary spastic paraplegia

  • Use G11.5 for Hypomyelination - hypogonadotropic hypogonadism - hypodontia

  • Use G11.6 for Leukodystrophy with vanishing white matter disease

  • Use G11.8 for Other hereditary ataxias

  • Use G11.9 for Hereditary ataxia, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G11: its own notes plus those printed at Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

On G11 itself
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)
From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name G11, its category, or a range that includes it.

Excludes1 2

These codes carry an Excludes1 note naming G11: they are not reported together with it, unless the two conditions are unrelated.

  • R26 Abnormalities of gait and mobility
    hereditary ataxia (G11.-)
  • R27 Other lack of coordination
    hereditary ataxia (G11.-)

Patient EducationClinical

Cerebellar Disorders

When you play the piano or hit a tennis ball you are activating the cerebellum. The cerebellum is the area of the brain that controls coordination and balance. Problems with the cerebellum include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G11Overview

What is the ICD-10 code for hereditary ataxia?

G11 is the ICD-10-CM category for hereditary ataxia, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is G11 (Hereditary ataxia) a billable code?

No. This is a category header that groups the codes for hereditary ataxia, and headers cannot be submitted on claims. Claims for hereditary ataxia need a more specific code from this category, such as G11.0, G11.10, and G11.11.