G11.11 - Friedreich ataxia
| ICD-10: | G11.11 |
| Short Description: | Friedreich ataxia |
| Long Description: | Friedreich ataxia |
| Status: | Valid for Submission |
| Version: | ICD-10-CM 2023 |
| Code Classification: |
G11.11 is a billable ICD-10 code used to specify a medical diagnosis of friedreich ataxia. The code is valid during the fiscal year 2023 from October 01, 2022 through September 30, 2023 for the submission of HIPAA-covered transactions.
Approximate Synonyms
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Cardiomyopathy in Friedreich's ataxia
- Dilated cardiomyopathy due to Friedreich's ataxia
- Friedreich's ataxia
- Hypertrophic cardiomyopathy due to Friedreich ataxia
Clinical Information
- Friedreich Ataxia-. an autosomal recessive disease, usually of childhood onset, characterized pathologically by degeneration of the spinocerebellar tracts, posterior columns, and to a lesser extent the corticospinal tracts. clinical manifestations include gait ataxia, pes cavus, speech impairment, lateral curvature of spine, rhythmic head tremor, kyphoscoliosis, congestive heart failure (secondary to a cardiomyopathy), and lower extremity weakness. most forms of this condition are associated with a mutation in a gene on chromosome 9, at band q13, which codes for the mitochondrial protein frataxin. (from adams et al., principles of neurology, 6th ed, p1081; n engl j med 1996 oct 17;335(16):1169-75) the severity of friedreich ataxia associated with expansion of gaa repeats in the first intron of the frataxin gene correlates with the number of trinucleotide repeats. (from durr et al, n engl j med 1996 oct 17;335(16):1169-75)
Tabular List of Diseases and Injuries
The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to this diagnosis code:
Inclusion Terms
Inclusion TermsThese terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Autosomal recessive Friedreich ataxia
- Friedreich ataxia with retained reflexes
Index to Diseases and Injuries References
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for this diagnosis code are found in the injuries and diseases index:
- - Ataxia, ataxy, ataxic - R27.0
- - autosomal recessive Friedreich - G11.11
- - Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes) - G11.11
- - hereditary - G11.9
- - spinal (Friedreich's) - G11.11
- - spinal
- - hereditary (Friedreich's) - G11.11
- - Cardiomyopathy (familial) (idiopathic) - I42.9
- - due to
- - Friedreich's ataxia - G11.11
- - due to
- - Disease, diseased - See Also: Syndrome;
- - Friedreich's
- - combined systemic or ataxia - G11.11
- - Friedreich's
- - Friedreich's
- - ataxia - G11.11
- - combined systemic disease - G11.11
- - sclerosis (cerebellum) (spinal cord) - G11.11
- - Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) - See Also: Cardiomyopathy; - I42.9
- - in (due to)
- - Friedreich's ataxia - G11.11
- - in (due to)
- - Sclerosis, sclerotic
- - Friedreich's (spinal cord) - G11.11
- - hereditary
- - spinal (Friedreich's ataxia) - G11.11
- - spinal (cord) (progressive) - G95.89
- - hereditary (Friedreich's) (mixed form) - G11.11
Replacement Code
G1111 replaces the following previously assigned ICD-10 code(s):
- G11.1 - Early-onset cerebellar ataxia
Code History
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - Code Added, effective from 10/1/2020 through 9/30/2021