Huntington's disease (G10)

ICD-10 code G10 is used specifically for diagnosing and documenting Huntington's disease, a genetic neurological disorder characterized by progressive movement, cognitive, and psychiatric symptoms.

This code covers all variations of Huntington's disease, including Juvenile onset and Late onset forms, as well as related conditions commonly referred to as Huntington's chorea or dementia due to Huntington chorea. It also includes atypical presentations like the akinetic-rigid type and Huntington disease-like syndromes, such as Huntington disease-like 2. Recognizing these synonyms helps clarify coding when faced with descriptors like dementia due to genetic disease or altered behavior linked to Huntington’s dementia. Medical coders should apply G10 when the patient's diagnosis reflects any hereditary nervous system disorder matching these terms, ensuring precise capture of this specific condition in health records and billing.

Instructional Notations

Inclusion Terms

These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.

  • Huntington's chorea
  • Huntington's dementia

Use Additional Code

The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.