Systemic atrophies primarily affecting the central nervous system (G10-G14)
ICD-10 codes G10 through G14 cover systemic atrophies mainly affecting the central nervous system. This grouping includes hereditary neurodegenerative diseases such as Huntington's disease, various hereditary ataxias, spinal muscular atrophies, and postpolio syndrome, all characterized by progressive loss of nervous system function.
The range starts with G10 for Huntington's disease, also known as Huntington chorea or dementia due to genetic disease. Codes from G11 address hereditary ataxias, including Friedreich ataxia (G11.11), congenital nonprogressive ataxia, and episodic ataxias, highlighting conditions with impaired muscle coordination. G12 focuses on spinal muscular atrophies and related syndromes such as Werdnig-Hoffman disease (G12.0), amyotrophic lateral sclerosis (G12.21), and motor neuron diseases, involving progressive muscle weakness. The G13 codes refer to systemic CNS atrophies linked to other diseases, like paraneoplastic cerebellar degeneration. Finally, G14 represents postpolio syndrome, a delayed complication seen after poliomyelitis. These codes assist healthcare providers and coders in accurately identifying and tracking hereditary and systemic neurodegenerative disorders affecting the brain and spinal cord.
Diseases of the nervous system (G00–G99)
Systemic atrophies primarily affecting the central nervous system (G10-G14)
- G10 Huntington's disease
Huntington's disease (G10)
G11 Hereditary ataxia
- G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
- G11.10 Early-onset cerebellar ataxia, unspecified
- G11.11 Friedreich ataxia
- G11.19 Other early-onset cerebellar ataxia
- G11.2 Late-onset cerebellar ataxia
- G11.3 Cerebellar ataxia with defective DNA repair
- G11.4 Hereditary spastic paraplegia
- G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
- G11.6 Leukodystrophy with vanishing white matter disease
- G11.8 Other hereditary ataxias
- G11.9 Hereditary ataxia, unspecified
Hereditary ataxia (G11)
G13 Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
- G13.0 Paraneoplastic neuromyopathy and neuropathy
- G13.1 Other systemic atrophy primarily affecting central nervous system in neoplastic disease
- G13.2 Systemic atrophy primarily affecting the central nervous system in myxedema
- G13.8 Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere (G13)
- G14 Postpolio syndrome
Postpolio syndrome (G14)
