2026 ICD-10-CM Diagnosis Code G11.4Hereditary spastic paraplegia

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G11.4 is a billable ICD-10-CM diagnosis code for hereditary spastic paraplegia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G11.4
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary spastic paraplegia
Short Description
Hereditary spastic paraplegia
Same as the full description in the CMS dataset.
Parent Code
G11
Hereditary ataxia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11.4Hereditary spastic paraplegia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal dominant hereditary spastic paraplegia
  • Autosomal dominant spastic ataxia type 1
  • Autosomal dominant spastic paraplegia type 10
  • Autosomal dominant spastic paraplegia type 12
  • Autosomal dominant spastic paraplegia type 13
  • Autosomal dominant spastic paraplegia type 17
  • Autosomal dominant spastic paraplegia type 19
  • Autosomal dominant spastic paraplegia type 29
  • Autosomal dominant spastic paraplegia type 3
  • Autosomal dominant spastic paraplegia type 31
  • Autosomal dominant spastic paraplegia type 36
  • Autosomal dominant spastic paraplegia type 37
  • Autosomal dominant spastic paraplegia type 38
  • Autosomal dominant spastic paraplegia type 4
  • Autosomal dominant spastic paraplegia type 41
  • Autosomal dominant spastic paraplegia type 42
  • Autosomal dominant spastic paraplegia type 6
  • Autosomal dominant spastic paraplegia type 73
  • Autosomal dominant spastic paraplegia type 8
  • Autosomal dominant spastic paraplegia type 9A
  • Autosomal dominant spastic paraplegia type 9B
  • Autosomal recessive cerebellar ataxia with late-onset spasticity
  • Autosomal recessive complex spastic paraplegia due to Kennedy pathway dysfunction
  • Autosomal recessive hereditary spastic paraplegia
  • Autosomal recessive spastic ataxia of Charlevoix-Saguenay
  • Autosomal recessive spastic ataxia with leukoencephalopathy
  • Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
  • Autosomal recessive spastic paraplegia type 11
  • Autosomal recessive spastic paraplegia type 14
  • Autosomal recessive spastic paraplegia type 15
  • Autosomal recessive spastic paraplegia type 18
  • Autosomal recessive spastic paraplegia type 21
  • Autosomal recessive spastic paraplegia type 23
  • Autosomal recessive spastic paraplegia type 24
  • Autosomal recessive spastic paraplegia type 25
  • Autosomal recessive spastic paraplegia type 26
  • Autosomal recessive spastic paraplegia type 27
  • Autosomal recessive spastic paraplegia type 28
  • Autosomal recessive spastic paraplegia type 32
  • Autosomal recessive spastic paraplegia type 35
  • Autosomal recessive spastic paraplegia type 39
  • Autosomal recessive spastic paraplegia type 43
  • Autosomal recessive spastic paraplegia type 44
  • Autosomal recessive spastic paraplegia type 45
  • Autosomal recessive spastic paraplegia type 46
  • Autosomal recessive spastic paraplegia type 48
  • Autosomal recessive spastic paraplegia type 53
  • Autosomal recessive spastic paraplegia type 54
  • Autosomal recessive spastic paraplegia type 55
  • Autosomal recessive spastic paraplegia type 56
  • Autosomal recessive spastic paraplegia type 57
  • Autosomal recessive spastic paraplegia type 58
  • Autosomal recessive spastic paraplegia type 59
  • Autosomal recessive spastic paraplegia type 5A
  • Autosomal recessive spastic paraplegia type 60
  • Autosomal recessive spastic paraplegia type 61
  • Autosomal recessive spastic paraplegia type 62
  • Autosomal recessive spastic paraplegia type 63
  • Autosomal recessive spastic paraplegia type 64
  • Autosomal recessive spastic paraplegia type 66
  • Autosomal recessive spastic paraplegia type 67
  • Autosomal recessive spastic paraplegia type 69
  • Autosomal recessive spastic paraplegia type 70
  • Autosomal recessive spastic paraplegia type 71
  • Autosomal recessive spastic paraplegia type 74
  • Autosomal recessive spastic paraplegia type 75
  • Autosomal recessive spastic paraplegia type 76
  • Autosomal recessive spastic paraplegia type 77
  • Autosomal recessive spastic paraplegia type 78
  • Autosomal recessive spastic paraplegia type 9B
  • Autosomal spastic paraplegia type 30
  • Autosomal spastic paraplegia type 72
  • Bedouin spastic ataxia syndrome
  • Bilateral lower limb ataxia
  • Choreoathetosis
  • Chronic deafness
  • Complicated hereditary spastic paraplegia
  • Congenital miosis
  • Constricted pupil
  • Disorder of glutamine metabolism
  • Distal spinal muscular atrophy
  • Dystonia due to hereditary spastic paraplegia
  • Early-onset progressive encephalopathy, spastic ataxia, distal spinal muscular atrophy syndrome
  • Early-onset spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Fryns macrocephaly
  • Hereditary sensory and autonomic neuropathy with spastic paraplegia
  • Hereditary spastic paraplegia
  • Infantile ascending hereditary spastic paralysis
  • Kyphoscoliosis, lateral tongue atrophy, hereditary spastic paraplegia syndrome
  • Macular corneal dystrophy
  • Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial disease
  • Motor neuron disease due to hereditary spastic paraplegia
  • MT-ATP6-related mitochondrial spastic paraplegia
  • Palmoplantar keratoderma, spastic paralysis syndrome
  • Parkinsonism due to hereditary spastic paraplegia
  • Parkinsonism due to heredodegenerative disorder
  • Paroxysmal choreoathetosis
  • Paroxysmal dystonia
  • Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
  • Progressive muscular atrophy
  • Punctate palmoplantar keratoderma
  • Pure hereditary spastic paraplegia
  • Second cranial nerve finding
  • Severe intellectual disability and progressive spastic paraplegia
  • Spastic ataxia with congenital miosis
  • Spastic ataxia, dysarthria due to glutaminase deficiency
  • Spastic paraparesis
  • Spastic paraparesis and deafness
  • Spastic paraparesis, cataracts, speech delay syndrome
  • Spastic paraplegia type 7
  • Spastic paraplegia with Paget disease of bone syndrome
  • Spastic paraplegia with precocious puberty syndrome
  • Spastic paraplegia, facial cutaneous lesion syndrome
  • Spastic paraplegia, glaucoma, intellectual disability syndrome
  • Spastic paraplegia, intellectual disability, nystagmus, obesity syndrome
  • Spastic paraplegia, nephritis, deafness syndrome
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Spastic paraplegia, optic atrophy, neuropathy syndrome
  • Spastic paraplegia, severe developmental delay, epilepsy syndrome
  • SPOAN and SPOAN-related disorder
  • X-linked complex hereditary spastic paraplegia
  • X-linked hereditary spastic paraplegia
  • X-linked pure hereditary spastic paraplegia
  • X-linked spastic paraplegia type 16
  • X-linked spastic paraplegia type 2
  • X-linked spastic paraplegia type 34

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Ataxia, ataxy, ataxic
      • hereditary
        • spastic
    • Ataxia, ataxy, ataxic
      • spastic hereditary
    • Paralysis, paralytic(complete) (incomplete)
      • familial (recurrent) (periodic)
        • spastic
    • Paralysis, paralytic(complete) (incomplete)
      • spastic
        • familial
    • Paralysis, paralytic(complete) (incomplete)
      • spastic
        • hereditary
    • Paraplegia(lower)
      • familial spastic
    • Paraplegia(lower)
      • hereditary, spastic
    • Paraplegia(lower)
      • spastic
        • hereditary

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Macular Corneal Dystrophy

    a stromal corneal dystrophy, with autosomal recessive inheritance, that is caused by lack of or abnormal keratan sulfate.

  • Progressive Muscular Atrophy

    a rare, milder form of amyotrophic lateral sclerosis. it is characterized by a slowly progressive clinical course. signs and symptoms include muscle weakness, atrophy, and fasciculation.

  • Congenital Macular Corneal Dystrophy

    early onset macular corneal dystrophy, typically occurring in childhood.

Patient EducationClinical

Neuromuscular Disorders

Neuromuscular disorders affect your neuromuscular system. They can cause problems with:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G11.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
334.1 Hered spastic paraplegia
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G11.4Overview

Is G11.4 (Hereditary ataxia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary spastic paraplegia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G11.4?

Under the General Equivalence Mappings, hereditary spastic paraplegia converts to ICD-9-CM 334.1 (hered spastic paraplegia). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.