2027 ICD-10-CM Diagnosis Code G11.4Hereditary spastic paraplegia

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11.4
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G11.4 is a billable ICD-10-CM diagnosis code for hereditary spastic paraplegia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 58 through 60. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 176 closely related codes. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

For Medicare Advantage risk adjustment, G11.4 maps to CMS-HCC Category 200 (Friedreich and Other Hereditary Ataxias; Huntington Disease) under the V28 model, adding a risk factor of about 0.279 for a community, non-dual, aged beneficiary in payment year 2027.

Code Identity

ICD-10-CM Code
G11.4
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary spastic paraplegia
Short Description
Hereditary spastic paraplegia
Same as the full description in the CMS dataset.
Parent Code
G11
Hereditary ataxia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11.4Hereditary spastic paraplegia

Medicare Risk Adjustment (HCC)Billing

G11.4 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.

CMS-HCC V28 Category (Payment Model)
HCC 200— Friedreich and Other Hereditary Ataxias; Huntington Disease
Payment HCC · PY 2027 one of 17 ICD-10-CM codes in this category
Risk Adjustment Factor (RAF) Weight
+0.279
community, non-dual, aged · ranges 0.000–0.428 across segments
Hierarchy
Top of its hierarchy
HCC 200 is not superseded by any other condition category
Prior Model (CMS-HCC V24)
HCC 72
V24 retired V28 pays 100% of MA risk scores since PY 2026
Other CMS Models
PACE (CMS-HCC V22): HCC 72 · ESRD (V21): HCC 72 · ESRD (V24): HCC 72
ESRD V21 weights: 0.102 dialysis, 0.256–0.456 functioning graft · ESRD V24 weights: 0.099 dialysis, 0.222–0.523 functioning graft
Part D (RxHCC)
Not mapped
G11.4 does not risk-adjust in the RxHCC prescription drug model

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal dominant hereditary spastic paraplegia
  • Autosomal dominant spastic ataxia type 1
  • Autosomal dominant spastic paraplegia type 10
  • Autosomal dominant spastic paraplegia type 12
  • Autosomal dominant spastic paraplegia type 13
  • Autosomal dominant spastic paraplegia type 17
  • Autosomal dominant spastic paraplegia type 19
  • Autosomal dominant spastic paraplegia type 29
  • Autosomal dominant spastic paraplegia type 3
  • Autosomal dominant spastic paraplegia type 31
  • Autosomal dominant spastic paraplegia type 36
  • Autosomal dominant spastic paraplegia type 37
  • Autosomal dominant spastic paraplegia type 38
  • Autosomal dominant spastic paraplegia type 4
  • Autosomal dominant spastic paraplegia type 41
  • Autosomal dominant spastic paraplegia type 42
  • Autosomal dominant spastic paraplegia type 6
  • Autosomal dominant spastic paraplegia type 73
  • Autosomal dominant spastic paraplegia type 79A
  • Autosomal dominant spastic paraplegia type 8
  • Autosomal dominant spastic paraplegia type 9A
  • Autosomal dominant spastic paraplegia type 9B
  • Autosomal recessive cerebellar ataxia with late-onset spasticity
  • Autosomal recessive complex spastic paraplegia due to Kennedy pathway dysfunction
  • Autosomal recessive hereditary spastic paraplegia
  • Autosomal recessive spastic ataxia of Charlevoix-Saguenay
  • Autosomal recessive spastic ataxia with leukoencephalopathy
  • Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
  • Autosomal recessive spastic paraplegia type 11
  • Autosomal recessive spastic paraplegia type 14
  • Autosomal recessive spastic paraplegia type 15
  • Autosomal recessive spastic paraplegia type 18
  • Autosomal recessive spastic paraplegia type 21
  • Autosomal recessive spastic paraplegia type 23
  • Autosomal recessive spastic paraplegia type 24
  • Autosomal recessive spastic paraplegia type 25
  • Autosomal recessive spastic paraplegia type 26
  • Autosomal recessive spastic paraplegia type 27
  • Autosomal recessive spastic paraplegia type 28
  • Autosomal recessive spastic paraplegia type 32
  • Autosomal recessive spastic paraplegia type 35
  • Autosomal recessive spastic paraplegia type 39
  • Autosomal recessive spastic paraplegia type 43
  • Autosomal recessive spastic paraplegia type 44
  • Autosomal recessive spastic paraplegia type 45
  • Autosomal recessive spastic paraplegia type 46
  • Autosomal recessive spastic paraplegia type 48
  • Autosomal recessive spastic paraplegia type 53
  • Autosomal recessive spastic paraplegia type 54
  • Autosomal recessive spastic paraplegia type 55
  • Autosomal recessive spastic paraplegia type 56
  • Autosomal recessive spastic paraplegia type 57
  • Autosomal recessive spastic paraplegia type 58
  • Autosomal recessive spastic paraplegia type 59
  • Autosomal recessive spastic paraplegia type 5A
  • Autosomal recessive spastic paraplegia type 60
  • Autosomal recessive spastic paraplegia type 61
  • Autosomal recessive spastic paraplegia type 62
  • Autosomal recessive spastic paraplegia type 63
  • Autosomal recessive spastic paraplegia type 64
  • Autosomal recessive spastic paraplegia type 66
  • Autosomal recessive spastic paraplegia type 67
  • Autosomal recessive spastic paraplegia type 69
  • Autosomal recessive spastic paraplegia type 70
  • Autosomal recessive spastic paraplegia type 71
  • Autosomal recessive spastic paraplegia type 74
  • Autosomal recessive spastic paraplegia type 75
  • Autosomal recessive spastic paraplegia type 76
  • Autosomal recessive spastic paraplegia type 77
  • Autosomal recessive spastic paraplegia type 78
  • Autosomal recessive spastic paraplegia type 9B
  • Autosomal spastic paraplegia type 30
  • Autosomal spastic paraplegia type 72
  • Bedouin spastic ataxia syndrome
  • Bilateral lower limb ataxia
  • Choreoathetosis
  • Complicated hereditary spastic paraplegia
  • Congenital miosis
  • Constricted pupil
  • Disorder of glutamine metabolism
  • Distal spinal muscular atrophy
  • Dystonia due to hereditary spastic paraplegia
  • Early-onset progressive encephalopathy, spastic ataxia, distal spinal muscular atrophy syndrome
  • Early-onset spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Fryns macrocephaly
  • Hereditary sensory and autonomic neuropathy with spastic paraplegia
  • Hereditary spastic paraplegia
  • IFIH1-related hereditary spastic paraplegia
  • Infantile ascending hereditary spastic paralysis
  • Kyphoscoliosis, lateral tongue atrophy, hereditary spastic paraplegia syndrome
  • Macular corneal dystrophy
  • Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial disease
  • Motor neuron disease due to hereditary spastic paraplegia
  • MT-ATP6-related mitochondrial spastic paraplegia
  • Palmoplantar keratoderma, spastic paralysis syndrome
  • Parkinsonism due to hereditary spastic paraplegia
  • Parkinsonism due to heredodegenerative disorder
  • Paroxysmal choreoathetosis
  • Paroxysmal dystonia
  • Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
  • Progressive macrocephaly
  • Progressive muscular atrophy
  • Punctate palmoplantar keratoderma
  • Pure hereditary spastic paraplegia
  • Second cranial nerve finding
  • Severe intellectual disability and progressive spastic paraplegia
  • Spastic ataxia with congenital miosis
  • Spastic ataxia, dysarthria due to glutaminase deficiency
  • Spastic paraparesis
  • Spastic paraparesis and deafness
  • Spastic paraparesis, cataracts, speech delay syndrome
  • Spastic paraplegia type 7
  • Spastic paraplegia with Paget disease of bone syndrome
  • Spastic paraplegia with precocious puberty syndrome
  • Spastic paraplegia, facial cutaneous lesion syndrome
  • Spastic paraplegia, glaucoma, intellectual disability syndrome
  • Spastic paraplegia, intellectual disability, nystagmus, obesity syndrome
  • Spastic paraplegia, nephritis, deafness syndrome
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Spastic paraplegia, optic atrophy, neuropathy syndrome
  • Spastic paraplegia, severe developmental delay, epilepsy syndrome
  • SPOAN and SPOAN-related disorder
  • X-linked complex hereditary spastic paraplegia
  • X-linked hereditary spastic paraplegia
  • X-linked pure hereditary spastic paraplegia
  • X-linked spastic paraplegia type 16
  • X-linked spastic paraplegia type 2
  • X-linked spastic paraplegia type 34

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G11.4: its own notes plus those printed at G11 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From G11 Hereditary ataxia applies to 11 codes
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)
From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name G11.4, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming G11.4: they are not reported together with it, unless the two conditions are unrelated.

  • G80 Cerebral palsy
    hereditary spastic paraplegia (G11.4)
  • R26 Abnormalities of gait and mobility
    hereditary ataxia (G11.-) names G11.-, which includes this code
  • R27 Other lack of coordination
    hereditary ataxia (G11.-) names G11.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Spastic Paraplegia, Hereditary

    a group of inherited diseases that share similar phenotypes but are genetically diverse. different genetic loci for autosomal recessive, autosomal dominant, and x-linked forms of hereditary spastic paraplegia have been identified. clinically, patients present with slowly progressive distal limb weakness and lower extremity spasticity. peripheral sensory neurons may be affected in the later stages of the disease. (j neurol neurosurg psychiatry 1998 jan;64(1):61-6; curr opin neurol 1997 aug;10(4):313-8)

Patient EducationClinical

Neuromuscular Disorders

Neuromuscular disorders affect your neuromuscular system. They can cause problems with:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G11.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
334.1 Hered spastic paraplegia
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G11.4Overview

What is the ICD-10 code for hereditary spastic paraplegia?

The ICD-10-CM code for hereditary spastic paraplegia is G11.4 (sometimes written as G114). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is G11.4 (Hereditary ataxia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary spastic paraplegia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does G11.4 group to?

When hereditary spastic paraplegia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 60, 58, 59, with relative weights from 0.9248 to 1.8430 depending on complications. Higher weights mean higher Medicare reimbursement.

Is G11.4 a CC or MCC?

CMS lists G11.4 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 176 closely related codes in its exclusion list.

What is the ICD-9 equivalent of G11.4?

Under the General Equivalence Mappings, hereditary spastic paraplegia converts to ICD-9-CM 334.1 (hered spastic paraplegia). The mapping is approximate, so confirm the match fits the documentation.

What HCC is G11.4?

G11.4 (hereditary spastic paraplegia) maps to CMS-HCC Category 200 (Friedreich and Other Hereditary Ataxias; Huntington Disease), commonly written as HCC 200, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 72 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.

Does G11.4 risk-adjust for Medicare Advantage payment?

Yes. When documented and reported on a Medicare Advantage encounter, G11.4 adds a risk adjustment factor of about 0.279 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.000 to 0.428 depending on the payment segment). HCC 200 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 200 category page.