ICD-10-CM Code G11.8

Other hereditary ataxias

Version 2021 Billable Code

Valid for Submission

G11.8 is a billable code used to specify a medical diagnosis of other hereditary ataxias. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code G11.8 might also be used to specify conditions or terms like abnormal saccadic eye movement, arts syndrome, ataxia pancytopenia syndrome, ataxia, photosensitivity, short stature syndrome, autosomal recessive cerebellar ataxia beauce type, autosomal recessive cerebellar ataxia with saccadic intrusion syndrome, etc

Short Description:Other hereditary ataxias
Long Description:Other hereditary ataxias

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code G11.8 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abnormal saccadic eye movement
  • Arts syndrome
  • Ataxia pancytopenia syndrome
  • Ataxia, photosensitivity, short stature syndrome
  • Autosomal recessive cerebellar ataxia Beauce type
  • Autosomal recessive cerebellar ataxia with saccadic intrusion syndrome
  • Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX deficiency
  • Autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome
  • Autosomal recessive cerebelloparenchymal disorder type 3
  • Bailey-Cushing syndrome
  • CAMOS syndrome
  • Cerebellar ataxia Cayman type
  • Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome
  • CLCN2-related leukoencephalopathy
  • Congenital non-progressive ataxia
  • Episodic ataxia
  • Episodic ataxia type 1
  • Episodic ataxia type 2
  • Episodic ataxia type 3
  • Episodic ataxia type 4
  • Episodic ataxia type 5
  • Episodic ataxia type 6
  • Episodic ataxia with slurred speech
  • Finding of intelligibility of articulation
  • Generalized convulsive epilepsy
  • Intellectual disability, hyperkinetic movement, truncal ataxia syndrome
  • Jervis' syndrome
  • Leukoencephalopathy, ataxia, hypodontia, hypomyelination syndrome
  • Oculomotor apraxia
  • Progressive sensory ataxia of Charolais
  • Recessive mitochondrial ataxia syndrome
  • Richards-Rundle syndrome
  • Sanger-Brown cerebellar ataxia
  • Slurred speech
  • Spinocerebellar ataxia dysmorphism syndrome
  • Spinocerebellar ataxia type 11
  • Spinocerebellar ataxia type 14
  • Spinocerebellar ataxia type 34
  • Spinocerebellar ataxia type 35
  • Spinocerebellar ataxia type 38
  • Spinocerebellar ataxia type 40
  • Spinocerebellar ataxia with axonal neuropathy type 1
  • Third cranial nerve finding
  • Truncal ataxia
  • Unintelligible articulation

Clinical Information

  • FRIEDREICH ATAXIA-. an autosomal recessive disease usually of childhood onset characterized pathologically by degeneration of the spinocerebellar tracts posterior columns and to a lesser extent the corticospinal tracts. clinical manifestations include gait ataxia pes cavus speech impairment lateral curvature of spine rhythmic head tremor kyphoscoliosis congestive heart failure secondary to a cardiomyopathy and lower extremity weakness. most forms of this condition are associated with a mutation in a gene on chromosome 9 at band q13 which codes for the mitochondrial protein frataxin. from adams et al. principles of neurology 6th ed p1081; n engl j med 1996 oct 17;33516:1169 75 the severity of friedreich ataxia associated with expansion of gaa repeats in the first intron of the frataxin gene correlates with the number of trinucleotide repeats. from durr et al n engl j med 1996 oct 17;33516:1169 75
  • SPINOCEREBELLAR DEGENERATIONS-. a heterogenous group of degenerative syndromes marked by progressive cerebellar dysfunction either in isolation or combined with other neurologic manifestations. sporadic and inherited subtypes occur. inheritance patterns include autosomal dominant autosomal recessive and x linked.

Convert G11.8 to ICD-9

  • 334.8 - Spinocerebellar dis NEC (Approximate Flag)

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Systemic atrophies primarily affecting the central nervous system (G10-G14)
      • Hereditary ataxia (G11)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients

Cerebellar Disorders

When you play the piano or hit a tennis ball you are activating the cerebellum. The cerebellum is the area of the brain that controls coordination and balance. Problems with the cerebellum include

  • Cancer
  • Genetic disorders
  • Ataxias - failure of muscle control in the arms and legs that result in movement disorders
  • Degeneration - disorders caused by brain cells decreasing in size or wasting away

Treatment of cerebellar disorders depends on the cause. In some cases, there is no cure but treatment may help with symptoms.

NIH: National Institute of Neurological Disorders and Stroke

  • Acute cerebellar ataxia (Medical Encyclopedia)
  • Olivopontocerebellar atrophy (Medical Encyclopedia)

[Learn More]

Movement Disorders

Movement disorders are neurologic conditions that cause problems with movement, such as

  • Increased movement that can be voluntary (intentional) or involuntary (unintended)
  • Decreased or slow voluntary movement

There are many different movement disorders. Some of the more common types include

  • Ataxia, the loss of muscle coordination
  • Dystonia, in which involuntary contractions of your muscles cause twisting and repetitive movements. The movements can be painful.
  • Huntington's disease, an inherited disease that causes nerve cells in certain parts of the brain to waste away. This includes the nerve cells that help to control voluntary movement.
  • Parkinson's disease, which is disorder that slowly gets worse over time. It causes tremors, slowness of movement, and trouble walking.
  • Tourette syndrome, a condition which causes people to make sudden twitches, movements, or sounds (tics)
  • Tremor and essential tremor, which cause involuntary trembling or shaking movements. The movements may be in one or more parts of your body.

Causes of movement disorders include

  • Genetics
  • Infections
  • Medicines
  • Damage to the brain, spinal cord, or peripheral nerves
  • Metabolic disorders
  • Stroke and vascular diseases
  • Toxins

Treatment varies by disorder. Medicines can cure some disorders. Others get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms and relieve pain.

  • Angelman syndrome (Medical Encyclopedia)
  • Chronic motor tic disorder (Medical Encyclopedia)
  • Facial tics (Medical Encyclopedia)
  • Movement - uncontrollable (Medical Encyclopedia)
  • Movement - uncontrolled or slow (Medical Encyclopedia)
  • Movement - uncoordinated (Medical Encyclopedia)
  • Movement - unpredictable or jerky (Medical Encyclopedia)
  • Neurodegeneration with brain iron accumulation (NBIA) (Medical Encyclopedia)
  • Tardive dyskinesia (Medical Encyclopedia)

[Learn More]