2026 ICD-10-CM Diagnosis Code G11.19Other early-onset cerebellar ataxia

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11.19
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G11.19 is a billable ICD-10-CM diagnosis code for other early-onset cerebellar ataxia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G11.19
Billable Status
Yes — Valid for Submission
Code Describes
Other early-onset cerebellar ataxia
Short Description
Other early-onset cerebellar ataxia
Same as the full description in the CMS dataset.
Parent Code
G11.1
Early-onset cerebellar ataxia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11.19Other early-onset cerebellar ataxia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal recessive posterior column ataxia and retinitis pigmentosa
  • Childhood-onset autosomal recessive slowly progressive spinocerebellar ataxia
  • Dyssynergia cerebellaris myoclonica
  • Early onset cerebellar ataxia with essential tremor
  • Early onset cerebellar ataxia with hypogonadism
  • Early onset cerebellar ataxia with myoclonus
  • Early onset cerebellar ataxia with retained tendon reflexes
  • Early onset cerebellar ataxia with retinitis pigmentosa and optic atrophy
  • Infantile onset spinocerebellar ataxia
  • Infantile-onset autosomal recessive non progressive cerebellar ataxia
  • Non-progressive cerebellar ataxia
  • Primary cerebellar degeneration
  • Progressive cerebellar tremor
  • Progressive spinocerebellar ataxia with retained tendon reflexes
  • Spectrin-associated autosomal recessive cerebellar ataxia
  • Vestibulocerebellar ataxia
  • X chromosome-linked sideroblastic anemia
  • X-linked intellectual disability with ataxia and apraxia syndrome
  • X-linked sideroblastic anemia with spinocerebellar ataxia
  • X-linked spinocerebellar ataxia type 3
  • X-linked spinocerebellar ataxia type 4

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Early-onset cerebellar ataxia with essential tremor
  • Early-onset cerebellar ataxia with myoclonus Hunt's ataxia
  • Early-onset cerebellar ataxia with retained tendon reflexes
  • X-linked recessive spinocerebellar ataxia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Ataxia, ataxy, ataxic
      • cerebellar (hereditary)
        • with
          • essential tremor
    • Ataxia, ataxy, ataxic
      • cerebellar (hereditary)
        • with
          • myoclonus [Hunt's ataxia]
    • Ataxia, ataxy, ataxic
      • cerebellar (hereditary)
        • with
          • retained tendon reflexes
    • Ataxia, ataxy, ataxic
      • Hunt's
    • Ataxia, ataxy, ataxic
      • spinocerebellar, X-linked recessive
    • Disease, diseased
      • Hunt's (herpetic geniculate ganglionitis) (neuralgia)
        • dyssynergia cerebellaris myoclonica
    • Dyssynergia
      • cerebellaris myoclonica (Hunt's ataxia)
    • Hunt's
      • disease or syndrome (herpetic geniculate ganglionitis)
        • dyssynergia cerebellaris myoclonica
    • Ramsay-Hunt disease or syndrome
      • meaning dyssynergia cerebellaris myoclonica
    • Syndrome
      • Hunt's (herpetic geniculate ganglionitis) (neuralgia)
        • dyssynergia cerebellaris myoclonica

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cerebellar Disorders

When you play the piano or hit a tennis ball you are activating the cerebellum. The cerebellum is the area of the brain that controls coordination and balance. Problems with the cerebellum include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G11.19 replaces the following previously assigned code(s):

  • G11.1 - Early-onset cerebellar ataxia
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G11.19Overview

Is G11.19 (Early-onset cerebellar ataxia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other early-onset cerebellar ataxia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.