2026 ICD-10-CM Diagnosis Code E71.310Long chain/very long chain acyl CoA dehydrogenase deficiency
ICD-10-CM Codes›E00–E89›E70-E88›E71
- Billable — Valid for Submission
- Chronic Condition
E71.310 is a billable ICD-10-CM diagnosis code for long chain/very long chain acyl CoA dehydrogenase deficiency. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as Acyl-CoA dehydrogenase deficiency. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acyl-CoA dehydrogenase deficiency
- Combined deficiency of long chain 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase
- Long chain acyl-CoA dehydrogenase deficiency
- Very long chain acyl-CoA dehydrogenase deficiency
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- LCAD deficiency
- VLCAD deficiency
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- long chain/very long chain acyl CoA - E71.310
- LCAD (long chain acyl CoA dehydrogenase deficiency) - E71.310
- VLCAD (very long chain acyl CoA dehydrogenase deficiency) - E71.310
- Disorder (of) - See Also: Disease;
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Deficiency, deficient
- dehydrogenase
- long chain/very long chain acyl CoA
- Deficiency, deficient
- LCAD (long chain acyl CoA dehydrogenase deficiency)
- Deficiency, deficient
- VLCAD (very long chain acyl CoA dehydrogenase deficiency)
- Disorder(of)
- fatty acid
- oxidation
- LCAD
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Lipid Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert E71.310 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About E71.310Overview
Is E71.310 (Disorders of fatty-acid oxidation) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report long chain/very long chain acyl CoA dehydrogenase deficiency on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What is the ICD-9 equivalent of E71.310?
Under the General Equivalence Mappings, long chain/very long chain acyl CoA dehydrogenase deficiency converts to ICD-9-CM 277.85 (disorders acid oxidation). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
