Version 2024

2024 ICD-10-CM Diagnosis Code E71.1

Other disorders of branched-chain amino-acid metabolism

ICD-10-CM Code:
E71.1
ICD-10 Code for:
Other disorders of branched-chain amino-acid metabolism
Is Billable?
Not Valid for Submission
Code Navigator:

Code Classification

  • Endocrine, nutritional and metabolic diseases
    (E00–E89)
    • Metabolic disorders
      (E70-E88)
      • Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
        (E71)

E71.1 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of other disorders of branched-chain amino-acid metabolism. The code is not specific and is NOT valid for the year 2024 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Other disorders of branched-chain amino-acid metabolism

Non-specific codes like E71.1 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for other disorders of branched-chain amino-acid metabolism:

  • E71.11 for Branched-chain organic acidurias - NON-BILLABLE CODE

  • Use E71.110 for Isovaleric acidemia - BILLABLE CODE

  • Use E71.111 for 3-methylglutaconic aciduria - BILLABLE CODE

  • Use E71.118 for Other branched-chain organic acidurias - BILLABLE CODE

  • E71.12 for Disorders of propionate metabolism - NON-BILLABLE CODE

  • Use E71.120 for Methylmalonic acidemia - BILLABLE CODE

  • Use E71.121 for Propionic acidemia - BILLABLE CODE

  • Use E71.128 for Other disorders of propionate metabolism - BILLABLE CODE

  • Use E71.19 for Other disorders of branched-chain amino-acid metabolism - BILLABLE CODE

Patient Education


Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.

A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.

You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.