Valid for Submission
E71.39 is a billable diagnosis code used to specify a medical diagnosis of other disorders of fatty-acid metabolism. The code E71.39 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions.
The ICD-10-CM code E71.39 might also be used to specify conditions or terms like 3-hydroxy-3-methylglutaryl-coenzyme a synthase deficiency, acetyl-coa: carboxylase deficiency, carnitine acylcarnitine translocase deficiency, deficiency of 2,4-dienoyl-coa reductase, deficiency of 2-hydroxyglutarate dehydrogenase , deficiency of 3-hydroxybutyryl-coa epimerase, etc.
Index to Diseases and Injuries
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code E71.39 are found in the index:
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- 3-hydroxy-3-methylglutaryl-coenzyme A synthase deficiency
- Acetyl-CoA: carboxylase deficiency
- Carnitine acylcarnitine translocase deficiency
- Deficiency of 2,4-dienoyl-CoA reductase
- Deficiency of 2-hydroxyglutarate dehydrogenase
- Deficiency of 3-hydroxybutyryl-CoA epimerase
- Deficiency of 3-hydroxyisobutyryl CoA hydrolase
- Deficiency of acetate-CoA ligase
- Deficiency of acetoacetyl-CoA reductase
- Deficiency of acetyl-CoA acylase
- Deficiency of acetyl-CoA deacylase
- Deficiency of acetyl-CoA hydrolase
- Deficiency of carnitine acetyltransferase
- Deficiency of coenzyme-A transferase
- Deficiency of glutarate-CoA ligase
- Deficiency of long-chain fatty-acyl-CoA hydrolase
- Deficiency of long-chain-fatty-acid-CoA ligase
- Deficiency of malonyl-CoA decarboxylase
- Deficiency of palmitoyl-CoA hydrolase
- Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency
- Long-chain fatty acid transport deficiency
- Malonic aciduria
Convert E71.39 to ICD-9 Code
The General Equivalency Mapping (GEM) crosswalk indicates an approximate mapping between the ICD-10 code E71.39 its ICD-9 equivalent. The approximate mapping means there is not an exact match between the ICD-10 code and the ICD-9 code and the mapped code is not a precise representation of the original code.
Information for Patients
Lipid Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.
Lipid metabolism disorders, such as Gaucher disease and Tay-Sachs disease, involve lipids. Lipids are fats or fat-like substances. They include oils, fatty acids, waxes, and cholesterol. If you have one of these disorders, you may not have enough enzymes to break down lipids. Or the enzymes may not work properly and your body can't convert the fats into energy. They cause a harmful amount of lipids to build up in your body. Over time, that can damage your cells and tissues, especially in the brain, peripheral nervous system, liver, spleen, and bone marrow. Many of these disorders can be very serious, or sometimes even fatal.
These disorders are inherited. Newborn babies get screened for some of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.
Enzyme replacement therapies can help with a few of these disorders. For others, there is no treatment. Medicines, blood transfusions, and other procedures may help with complications.
[Learn More in MedlinePlus]