2026 ICD-10-CM Diagnosis Code E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

ICD-10-CM Codes›E00–E89›E70-E88›E71

ICD-10-CM E71
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E71 is a non-billable ICD-10-CM category code for disorders of branched-chain amino-acid metabolism and fatty-acid metabolism, so it cannot be submitted on claims. Use a more specific code from this category instead, such as E71.0, E71.110, E71.111, and E71.118.

Code Identity

ICD-10-CM Code
E71
Billable Status
No — Non-Billable Category
Code Describes
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Chapter
E70-E88
Metabolic disorders

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
This CodeE71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Specific Coding for Disord of branched-chain amino-acid metab & fatty-acid metabOverview

Non-specific codes like E71 require more characters. Use one of these billable codes instead:

  • Use E71.0 for Maple-syrup-urine disease

  • E71.1 for Other disorders of branched-chain amino-acid metabolism

  • E71.11 for Branched-chain organic acidurias

  • E71.12 for Disorders of propionate metabolism

  • Use E71.19 for Other disorders of branched-chain amino-acid metabolism

  • Use E71.2 for Disorder of branched-chain amino-acid metabolism, unspecified

  • E71.3 for Disorders of fatty-acid metabolism

  • Use E71.30 for Disorder of fatty-acid metabolism, unspecified

  • E71.31 for Disorders of fatty-acid oxidation

  • Use E71.32 for Disorders of ketone metabolism

  • Use E71.39 for Other disorders of fatty-acid metabolism

  • E71.4 for Disorders of carnitine metabolism

  • Use E71.40 for Disorder of carnitine metabolism, unspecified

  • Use E71.41 for Primary carnitine deficiency

  • Use E71.42 for Carnitine deficiency due to inborn errors of metabolism

  • Use E71.43 for Iatrogenic carnitine deficiency

  • E71.44 for Other secondary carnitine deficiency

  • E71.5 for Peroxisomal disorders

  • Use E71.50 for Peroxisomal disorder, unspecified

  • E71.51 for Disorders of peroxisome biogenesis

  • E71.52 for X-linked adrenoleukodystrophy

  • Use E71.53 for Other group 2 peroxisomal disorders

  • E71.54 for Other peroxisomal disorders

Patient EducationClinical

Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E71Overview

Is E71 a billable code?

No. This is a category header that groups the codes for disorders of branched-chain amino-acid metabolism and fatty-acid metabolism, and headers cannot be submitted on claims. Claims for disorders of branched-chain amino-acid metabolism and fatty-acid metabolism need a more specific code from this category, such as E71.0, E71.110, and E71.111.