2026 ICD-10-CM Diagnosis Code D68.04Acquired von Willebrand disease

ICD-10-CM Codes›D50–D89›D65-D69›D68

ICD-10-CM D68.04
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D68.04 is a billable ICD-10-CM diagnosis code for acquired von Willebrand disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as acquired coagulation factor inhibitor disorder. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Coagulation and hemorrhagic disorders.

Code Identity

ICD-10-CM Code
D68.04
Billable Status
Yes — Valid for Submission
Code Describes
Acquired von Willebrand disease
Short Description
Acquired von Willebrand disease
Same as the full description in the CMS dataset.
Parent Code
D68.0
Von Willebrand disease

Code Classification

ChapterD50–D89Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
SectionD65-D69Coagulation defects, purpura and other hemorrhagic conditions
CategoryD68Other coagulation defects
This CodeD68.04Acquired von Willebrand disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired coagulation factor inhibitor disorder
  • Acquired von Willebrand disease
  • Drug-induced coagulation inhibitor disorder
  • von Willebrand factor inhibitor disorder

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Acquired von Willebrand syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • von Willebrand (-Jürgens) (angiohemophilia)
        • acquired
    • Syndrome
      • von Willebrand (-Jürgen)
        • acquired

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR BLD006
Coagulation and hemorrhagic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Platelet Disorders

Platelets, also known as thrombocytes, are blood cells. They form in your bone marrow, a sponge-like tissue in your bones. Platelets play a major role in blood clotting. Normally, when one of your blood vessels is injured, you start to bleed.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement D68.04 replaces the following previously assigned code(s):

  • D68.0 - Von Willebrand disease
  • D68.0 - Von Willebrand's disease
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D68.04Overview

Is D68.04 (Von Willebrand disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report acquired von Willebrand disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.