2026 ICD-10-CM Diagnosis Code G11.6Leukodystrophy with vanishing white matter disease

ICD-10-CM Codes›G00–G99›G10-G14›G11

ICD-10-CM G11.6
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G11.6 is a billable ICD-10-CM diagnosis code for leukodystrophy with vanishing white matter disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as vanishing white matter disease. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neurocognitive disorders and Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G11.6
Billable Status
Yes — Valid for Submission
Code Describes
Leukodystrophy with vanishing white matter disease
Short Description
Leukodystrophy with vanishing white matter disease
Same as the full description in the CMS dataset.
Parent Code
G11
Hereditary ataxia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG11Hereditary ataxia
This CodeG11.6Leukodystrophy with vanishing white matter disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Vanishing white matter disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Leukodystrophy
      • with vanishing white matter disease

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS011
Neurocognitive disorders
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient No · outpatient No

Code History & ChangesHistory

Replacement G11.6 replaces the following previously assigned code(s):

  • G11.8 - Other hereditary ataxias
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G11.6Overview

Is G11.6 (Hereditary ataxia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report leukodystrophy with vanishing white matter disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.