2027 ICD-10-CM Diagnosis Code G11.11Friedreich ataxia
ICD-10-CM Codes›G00–G99›G10-G14›G11
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- Risk Adjusts — HCC 200
- Chronic Condition
G11.11 is a billable ICD-10-CM diagnosis code for friedreich ataxia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 58 through 60. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 31 closely related codes. Coders also document this condition as cardiomyopathy in Friedreich's ataxia. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).
For Medicare Advantage risk adjustment, G11.11 maps to CMS-HCC Category 200 (Friedreich and Other Hereditary Ataxias; Huntington Disease) under the V28 model, adding a risk factor of about 0.279 for a community, non-dual, aged beneficiary in payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
G11.11 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Cardiomyopathy in Friedreich's ataxia
- Cerebellar ataxia associated with another disorder
- Dilated cardiomyopathy due to Friedreich's ataxia
- Friedreich ataxia
- Hypertrophic cardiomyopathy due to Friedreich ataxia
- Posterior cord syndrome due to Friedreich ataxia
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to G11.11: its own notes plus those printed at G11 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Autosomal recessive Friedreich ataxia
- Friedreich ataxia with retained reflexes
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name G11.11, its category, or a range that includes it.
Excludes1 2
These codes carry an Excludes1 note naming G11.11: they are not reported together with it, unless the two conditions are unrelated.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Disease, diseased See Also: Syndrome;
ataxia G11.11
combined systemic disease G11.11
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Friedreich Ataxia
an autosomal recessive disease, usually of childhood onset, characterized pathologically by degeneration of the spinocerebellar tracts, posterior columns, and to a lesser extent the corticospinal tracts. clinical manifestations include gait ataxia, pes cavus, speech impairment, lateral curvature of spine, rhythmic head tremor, kyphoscoliosis, congestive heart failure (secondary to a cardiomyopathy), and lower extremity weakness. most forms of this condition are associated with a mutation in a gene on chromosome 9, at band q13, which codes for the mitochondrial protein frataxin. (from adams et al., principles of neurology, 6th ed, p1081; n engl j med 1996 oct 17;335(16):1169-75) the severity of friedreich ataxia associated with expansion of gaa repeats in the first intron of the frataxin gene correlates with the number of trinucleotide repeats. (from durr et al, n engl j med 1996 oct 17;335(16):1169-75)
Patient EducationClinical
Friedreich Ataxia
Friedreich ataxia is an inherited disease that damages your nervous system. The damage affects your spinal cord and the nerves that control muscle movement in your arms and legs. Symptoms usually begin between the ages of 5 and 15. The main symptom is ataxia, which means trouble coordinating movements. Specific symptoms include:
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Code History & ChangesHistory
Replacement G11.11 replaces the following previously assigned code(s):
- G11.1 - Early-onset cerebellar ataxia
Questions About G11.11Overview
What is the ICD-10 code for friedreich ataxia?
The ICD-10-CM code for friedreich ataxia is G11.11 (sometimes written as G1111). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is G11.11 (Early-onset cerebellar ataxia) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report friedreich ataxia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does G11.11 group to?
When friedreich ataxia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 60, 58, 59, with relative weights from 0.9248 to 1.8430 depending on complications. Higher weights mean higher Medicare reimbursement.
Is G11.11 a CC or MCC?
CMS lists G11.11 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 31 closely related codes in its exclusion list.
What HCC is G11.11?
G11.11 (friedreich ataxia) maps to CMS-HCC Category 200 (Friedreich and Other Hereditary Ataxias; Huntington Disease), commonly written as HCC 200, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 72 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.
Does G11.11 risk-adjust for Medicare Advantage payment?
Yes. When documented and reported on a Medicare Advantage encounter, G11.11 adds a risk adjustment factor of about 0.279 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.000 to 0.428 depending on the payment segment). HCC 200 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 200 category page.
