ICD-10-CM Code I42.9

Cardiomyopathy, unspecified

Version 2020 Billable Code

Valid for Submission

I42.9 is a billable code used to specify a medical diagnosis of cardiomyopathy, unspecified. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code I42.9 might also be used to specify conditions or terms like benign scapuloperoneal muscular dystrophy with cardiomyopathy, cardiomyopathy, cardiomyopathy co-occurrent with human immunodeficiency virus infection, cardiomyopathy due to neuromuscular disorder, cirrhotic cardiomyopathy, congestive heart failure due to cardiomyopathy, etc

Short Description:Cardiomyopathy, unspecified
Long Description:Cardiomyopathy, unspecified

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code I42.9:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Cardiomyopathy (primary) (secondary) NOS

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code I42.9 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Benign scapuloperoneal muscular dystrophy with cardiomyopathy
  • Cardiomyopathy
  • Cardiomyopathy co-occurrent with human immunodeficiency virus infection
  • Cardiomyopathy due to neuromuscular disorder
  • Cirrhotic cardiomyopathy
  • Congestive heart failure due to cardiomyopathy
  • Familial cardiomyopathy
  • Heart disease co-occurrent with human immunodeficiency virus infection
  • Heart failure with reduced ejection fraction
  • Heart failure with reduced ejection fraction due to cardiomyopathy
  • Maternally inherited cardiomyopathy and hearing loss syndrome
  • Mitral valve regurgitation due to cardiomyopathy
  • Pacing-induced cardiomyopathy
  • Primary cardiomyopathy
  • Scapuloperoneal muscular dystrophy
  • Severe scapuloperoneal muscular dystrophy with cardiomyopathy
  • Tachycardia-induced cardiomyopathy
  • Tubular renal disease with cardiomyopathy syndrome
  • X-linked muscular dystrophy not predominantly limb girdle

Clinical Information

  • CARDIOMYOPATHY ALCOHOLIC-. disease of cardiac muscle resulting from chronic excessive alcohol consumption. myocardial damage can be caused by: 1 a toxic effect of alcohol; 2 malnutrition in alcoholics such as thiamine deficiency; or 3 toxic effect of additives in alcoholic beverages such as cobalt. this disease is usually manifested by dyspnea and palpitations with cardiomegaly and congestive heart failure heart failure.
  • CARDIOMYOPATHY DILATED-. a form of cardiac muscle disease that is characterized by ventricular dilation ventricular dysfunction and heart failure. risk factors include smoking; alcohol drinking; hypertension; infection; pregnancy; and mutations in the lmna gene encoding lamin type a a nuclear lamina protein.
  • CARDIOMYOPATHY HYPERTROPHIC-. a form of cardiac muscle disease characterized by left and/or right ventricular hypertrophy hypertrophy left ventricular; hypertrophy right ventricular frequent asymmetrical involvement of the heart septum and normal or reduced left ventricular volume. risk factors include hypertension; aortic stenosis; and gene mutation; familial hypertrophic cardiomyopathy.
  • CARDIOMYOPATHY RESTRICTIVE-. a form of cardiac muscle disease in which the ventricular walls are excessively rigid impeding ventricular filling. it is marked by reduced diastolic volume of either or both ventricles but normal or nearly normal systolic function. it may be idiopathic or associated with other diseases endomyocardial fibrosis or amyloidosis causing interstitial fibrosis.
  • CHAGAS CARDIOMYOPATHY-. a disease of the cardiac muscle developed subsequent to the initial protozoan infection by trypanosoma cruzi. after infection less than 10% develop acute illness such as myocarditis mostly in children. the disease then enters a latent phase without clinical symptoms until about 20 years later. myocardial symptoms of advanced chagas disease include conduction defects heart block and cardiomegaly.
  • CARDIOMYOPATHIES-. a group of diseases in which the dominant feature is the involvement of the cardiac muscle itself. cardiomyopathies are classified according to their predominant pathophysiological features dilated cardiomyopathy; hypertrophic cardiomyopathy; restrictive cardiomyopathy or their etiological/pathological factors cardiomyopathy alcoholic; endocardial fibroelastosis.
  • MUSCULAR DYSTROPHY DUCHENNE-. an x linked recessive muscle disease caused by an inability to synthesize dystrophin which is involved with maintaining the integrity of the sarcolemma. muscle fibers undergo a process that features degeneration and regeneration. clinical manifestations include proximal weakness in the first few years of life pseudohypertrophy cardiomyopathy see myocardial diseases and an increased incidence of impaired mentation. becker muscular dystrophy is a closely related condition featuring a later onset of disease usually adolescence and a slowly progressive course. adams et al. principles of neurology 6th ed p1415
  • CARDIOMYOPATHY HYPERTROPHIC FAMILIAL-. an autosomal dominant inherited form of hypertrophic cardiomyopathy. it results from any of more than 50 mutations involving genes encoding contractile proteins such as ventricular myosins; cardiac troponin t; alpha tropomyosin.
  • GLYCOGEN STORAGE DISEASE TYPE IIB-. an x linked dominant multisystem disorder resulting in cardiomyopathy myopathy and intellectual disability. it is caused by mutation in the gene encoding lysosomal associated membrane protein 2.
  • TAKOTSUBO CARDIOMYOPATHY-. a transient left ventricular apical dysfunction or ballooning accompanied by electrocardiographic ecg t wave inversions. this abnormality is associated with high levels of catecholamines either administered or endogenously secreted from a tumor or during extreme stress.
  • DIABETIC CARDIOMYOPATHIES-. diabetes complications in which ventricular remodeling in the absence of coronary atherosclerosis and hypertension results in cardiac dysfunctions typically left ventricular dysfunction. the changes also result in myocardial hypertrophy myocardial necrosis and fibrosis and collagen deposition due to impaired glucose tolerance.

Diagnostic Related Groups

The ICD-10 code I42.9 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Convert I42.9 to ICD-9

  • 425.4 - Prim cardiomyopathy NEC (Approximate Flag)
  • 425.9 - Second cardiomyopath NOS (Approximate Flag)

Code Classification

  • Diseases of the circulatory system (I00–I99)
    • Other forms of heart disease (I30-I52)
      • Cardiomyopathy (I42)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute

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