2026 ICD-10-CM Diagnosis Code E84.19Cystic fibrosis with other intestinal manifestations

ICD-10-CM CodesE00–E89E70-E88E84

ICD-10-CM E84.19
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E84.19 is a billable ICD-10-CM diagnosis code for cystic fibrosis with other intestinal manifestations. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 393 through 395. Coders also document this condition as digestive system manifestation co-occurrent and due to cystic fibrosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cystic fibrosis.

Code Identity

ICD-10-CM Code
E84.19
Billable Status
Yes — Valid for Submission
Code Describes
Cystic fibrosis with other intestinal manifestations
Short Description
Cystic fibrosis with other intestinal manifestations
Same as the full description in the CMS dataset.
Parent Code
Cystic fibrosis with intestinal manifestations

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE84Cystic fibrosis
This CodeE84.19Cystic fibrosis with other intestinal manifestations

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Digestive system manifestation co-occurrent and due to cystic fibrosis
  • Distal intestinal obstruction syndrome
  • Distal intestinal obstruction syndrome due to cystic fibrosis
  • Fibrosing colonopathy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Distal intestinal obstruction syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Fibrosis, fibrotic
      • cystic (of pancreas)
        • with
          • distal intestinal obstruction syndrome
    • Fibrosis, fibrotic
      • cystic (of pancreas)
        • with
          • fecal impaction
    • Fibrosis, fibrotic
      • cystic (of pancreas)
        • with
          • intestinal manifestations NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END012
Cystic fibrosis
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disease of the mucus and sweat glands. It affects mostly your lungs, pancreas, liver, intestines, sinuses, and sex organs. CF causes your mucus to be thick and sticky. The mucus clogs the lungs, causing breathing problems and making it easy for bacteria to grow.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E84.19 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
277.03 Cystic fibrosis w GI man
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E84.19Overview

Is E84.19 (Cystic fibrosis with intestinal manifestations) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report cystic fibrosis with other intestinal manifestations on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does E84.19 group to?

When cystic fibrosis with other intestinal manifestations is the principal diagnosis on an inpatient stay, it groups to MS-DRG 393, 394, 395, with relative weights from 0.6490 to 1.5993 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of E84.19?

Under the General Equivalence Mappings, cystic fibrosis with other intestinal manifestations converts to ICD-9-CM 277.03 (cystic fibrosis w GI man). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.