2027 ICD-10-CM Diagnosis Code E71.30Disorder of fatty-acid metabolism, unspecified
ICD-10-CM Codes›E00–E89›E70-E88›E71
- Billable — Valid for Submission
- Chronic Condition
E71.30 is a billable ICD-10-CM diagnosis code for disorder of fatty-acid metabolism, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 642. Coders also document this condition as Acyl-CoA dehydrogenase deficiency. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.
E71.30 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 47 for payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
E71.30 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model, but it maps to payment categories in the other CMS models shown below.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acyl-CoA dehydrogenase deficiency
- Disorder of fatty acid metabolism
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to E71.30: its own notes plus those printed at E71.3, block E70-E88, and Chapter 4. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- carnitine deficiency due to inborn error of metabolism (E71.42)
- Ehlers-Danlos syndromes (Q79.6-)
Notes
General instructions on how these codes are used.
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name E71.30, its category, or a range that includes it.
Excludes1 4
These codes carry an Excludes1 note naming E71.30: they are not reported together with it, unless the two conditions are unrelated.
- E72 Other disorders of amino-acid metabolismfatty-acid metabolism (E71.3) names E71.3, which includes this code
- R79 Other abnormal findings of blood chemistry
- R79.83 Abnormal findings of blood amino-acid level
- Block R80-R82 Abnormal findings on examination of urine, without diagnosis
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Disorder (of) See Also: Disease;
metabolism E71.30
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Lipid Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert E71.30 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About E71.30Overview
What is the ICD-10 code for disorder of fatty-acid metabolism, unspecified?
The ICD-10-CM code for disorder of fatty-acid metabolism, unspecified is E71.30 (sometimes written as E7130). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is E71.30 (Disorders of fatty-acid metabolism) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report disorder of fatty-acid metabolism, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does E71.30 group to?
When disorder of fatty-acid metabolism, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 642 (inborn and Other Disorders of Metabolism), which carries a relative weight of 1.3226. Higher weights mean higher Medicare reimbursement.
Can E71.30 be reported with E71.5?
Not as a rule. The Excludes1 note at E71.3, which applies to E71.30, lists "peroxisomal disorders (E71.5)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of E71.30?
Under the General Equivalence Mappings, disorder of fatty-acid metabolism, unspecified converts to ICD-9-CM 272.8 (lipoid metabol dis NEC). The mapping is approximate, so confirm the match fits the documentation.
Does E71.30 risk-adjust for Medicare Advantage payment?
Not for Medicare Advantage: E71.30 maps to no category in the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 47 (Disorders of Lipoid Metabolism).
