2027 ICD-10-CM Diagnosis Code E20.1Pseudohypoparathyroidism
ICD-10-CM Codes›E00–E89›E20-E35›E20
- Billable — Valid for Submission
- Chronic Condition
E20.1 is a billable ICD-10-CM diagnosis code for pseudohypoparathyroidism. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 640 through 641. Coders also document this condition as cataract due to pseudohypoparathyroidism. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified endocrine disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Cataract due to pseudohypoparathyroidism
- Genetic syndromic childhood obesity
- Pseudohypoparathyroidism
- Pseudohypoparathyroidism and pseudopseudohypoparathyroidism
- Pseudohypoparathyroidism type 1C
- Pseudohypoparathyroidism type I A
- Pseudohypoparathyroidism type I B
- Pseudohypoparathyroidism type II
- Pseudopseudohypoparathyroidism
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to E20.1: its own notes plus those printed at E20, block E20-E35, and Chapter 4. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Notes
General instructions on how these codes are used.
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name E20.1, its category, or a range that includes it.
Excludes1 3
These codes carry an Excludes1 note naming E20.1: they are not reported together with it, unless the two conditions are unrelated.
Excludes2 1
These codes carry an Excludes2 note naming E20.1: its condition is not part of those codes, and both may be reported when the patient has both.
- E34.8 Other specified endocrine disorderspseudohypoparathyroidism (E20.1)
Code First 3
These codes say to code first a condition named in the note, and E20.1 is one of the conditions named.
Notes 1
These notes mention E20.1.
- Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseasesAll neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere. names E16-E31, which includes this code
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Pseudohypoparathyroidism E20.1
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Pseudohypoparathyroidism
a hereditary syndrome clinically similar to hypoparathyroidism. it is characterized by hypocalcemia; hyperphosphatemia; and associated skeletal development impairment and caused by failure of response to parathyroid hormone rather than deficiencies. a severe form with resistance to multiple hormones is referred to as type 1a and is associated with maternal mutant allele of the alpha chain of stimulatory g protein.
Patient EducationClinical
Metabolic Disorders
Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert E20.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About E20.1Overview
What is the ICD-10 code for pseudohypoparathyroidism?
The ICD-10-CM code for pseudohypoparathyroidism is E20.1 (sometimes written as E201). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is E20.1 (Hypoparathyroidism) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report pseudohypoparathyroidism on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does E20.1 group to?
When pseudohypoparathyroidism is the principal diagnosis on an inpatient stay, it groups to MS-DRG 641, 640, with relative weights from 0.7864 to 1.3392 depending on complications. Higher weights mean higher Medicare reimbursement.
Can E20.1 be reported with D82.1?
Not as a rule. The Excludes1 note at E20, which applies to E20.1, lists "Di George's syndrome (D82.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of E20.1?
Under the General Equivalence Mappings, pseudohypoparathyroidism converts to ICD-9-CM 275.49 (dis calcium metablsm NEC). The mapping is approximate, so confirm the match fits the documentation.
