2024 ICD-10-CM Diagnosis Code E20.9

Hypoparathyroidism, unspecified

ICD-10-CM Code:
E20.9
ICD-10 Code for:
Hypoparathyroidism, unspecified
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Endocrine, nutritional and metabolic diseases
    (E00–E89)
    • Disorders of other endocrine glands
      (E20-E35)
      • Hypoparathyroidism
        (E20)

E20.9 is a billable diagnosis code used to specify a medical diagnosis of hypoparathyroidism, unspecified. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Unspecified diagnosis codes like E20.9 are acceptable when clinical information is unknown or not available about a particular condition. Although a more specific code is preferable, unspecified codes should be used when such codes most accurately reflect what is known about a patient's condition. Specific diagnosis codes should not be used if not supported by the patient's medical record.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 10p partial monosomy syndrome
  • Cataract in hypoparathyroidism
  • Cataract in systemic disorders
  • Chorea due to endocrine disorder
  • Chorea due to hypoparathyroidism
  • Deletion of part of chromosome 10
  • Endocrine myopathy
  • Hypocalcemic tetany
  • Hypoparathyroidism
  • Hypoparathyroidism due to granulomatous disease
  • Hypoparathyroidism due to hemochromatosis
  • Hypoparathyroidism due to impaired PTH secretion
  • Hypoparathyroidism, deafness, renal disease syndrome
  • Myopathy in hypoparathyroidism
  • Parathyroid hypocalcemic tetany
  • Tetany

Clinical Classification

Clinical Information

  • Hypoparathyroidism

    a condition caused by a deficiency of parathyroid hormone (or pth). it is characterized by hypocalcemia and hyperphosphatemia. hypocalcemia leads to tetany. the acquired form is due to removal or injuries to the parathyroid glands. the congenital form is due to mutations of genes, such as tbx1; (see digeorge syndrome); casr encoding calcium-sensing receptor; or pth encoding parathyroid hormone.
  • Tetany

    a disorder characterized by muscle twitches, cramps, and carpopedal spasm, and when severe, laryngospasm and seizures. this condition is associated with unstable depolarization of axonal membranes, primarily in the peripheral nervous system. tetany usually results from hypocalcemia or reduced serum levels of magnesium that may be associated with hyperventilation; hypoparathyroidism; rickets; uremia; or other conditions. (from adams et al., principles of neurology, 6th ed, p1490)
  • Acquired Hypoparathyroidism

    hypoparathyroidism, the cause of which is not present at birth.
  • Albright Hereditary Osteodystrophy with Multiple Hormone Resistance|PHP1a|Pseudohypoparathyroidism Type 1a

    parathyroid hormone (pth) resistance caused by heterozygous inactivating mutation(s) of the maternal allele of the gnas gene encoding gs-alpha, resulting in expression of pth from only the paternal allele. clinical manifestations include albright hereditary osteodystrophy, early-onset obesity, and, in some cases, resistance to thyroid-stimulating hormone, gonadotropins, and growth hormone-releasing hormone, reflecting additional manifestations of gs-alpha deficiency.
  • Albright Hereditary Osteodystrophy without Multiple Hormone Resistance|Albright Hereditary Osteodystrophy with Multiple Hormone Resistance|PPHP|Pseudopseudohypoparathyroidism

    a condition caused by inactivating mutation(s) in the paternal allele of the gnas gene, encoding gs-alpha, resulting in expression of the gs-alpha protein from only the maternal allele. affected individuals have the clinical phenotype of albright hereditary osteodystrophy without hormone resistance.
  • Albright's Hereditary Osteodystrophy|Albright Hereditary Osteodystrophy|Albright's Hereditary Osteodystrophy with Multiple Hormone Resistance|PHP1A|Pseudohypoparathyroidism, Type IA

    a rare, autosomal dominant syndrome caused by mutations in the gnas gene. it is characterized by the presence of short stature, obesity, round face, brachydactyly, subcutaneous ossifications, and pseudohypoparathtyroidism.
  • Autosomal Dominant Hypoparathyroidism

    hypoparathyroidism associated with heterozygous mutation(s) in the pth gene, which encodes parathyroid hormone, or in the gcm2 gene, which encodes chorion-specific transcription factor gcmb.
  • Autosomal Recessive Hypoparathyroidism

    hypoparathyroidism associated with homozygous mutation(s) in the pth gene, which encodes parathyroid hormone, or in the gcm2 gene, which encodes chorion-specific transcription factor gcmb.
  • Barakat Syndrome|Hypoparathyroidism, Deafness, and Renal Anomalies Syndrome

    a condition characterized by hypoparathyroidism, sensorineural deafness, and renal failure. it is related to autosomal dominant inactivating mutation(s) in gata3, encoding a transcription factor important for the embryonic development of the parathyroid gland, the auditory stem, and the kidneys.
  • Grade 1 Hypoparathyroidism, CTCAE|Grade 1 Hypoparathyroidism

    asymptomatic; clinical or diagnostic observations only; intervention not indicated
  • Grade 2 Hypoparathyroidism, CTCAE|Grade 2 Hypoparathyroidism

    moderate symptoms; medical intervention indicated
  • Grade 3 Hypoparathyroidism, CTCAE|Grade 3 Hypoparathyroidism

    severe symptoms; medical intervention or hospitalization indicated
  • Grade 4 Hypoparathyroidism, CTCAE|Grade 4 Hypoparathyroidism

    life-threatening consequences; urgent intervention indicated
  • Grade 5 Hypoparathyroidism, CTCAE|Grade 5 Hypoparathyroidism

    death
  • Hypoparathyroidism

    an endocrine disorder characterized by decreased production of parathyroid hormone by the parathyroid glands. it is usually caused by damage of the parathyroid glands during head and neck surgery. signs and symptoms include muscle cramps, abdominal pain, dry skin, brittle nails, cataracts, tetany, and convulsions.
  • Hypoparathyroidism, CTCAE|Hypoparathyroidism|Hypoparathyroidism

    a disorder characterized by a decrease in production of parathyroid hormone by the parathyroid glands.
  • Hypoparathyroidism-Retardation-Dysmorphism Syndrome|HRDS|Hypoparathyroidism with Short Stature, Mental Retardation, and Seizures|Hypoparathyroidism, Congenital, Associated with Dysmorphism, Growth Retardation, and Developmental Delay|Sanjad-Sakati Syndrome

    an autosomal recessive condition caused by mutation(s) in the tbce gene, encoding tubulin-specific chaperone e. it is characterized by congenital hypoparathyroidism, mental retardation, seizures and developmental delay.
  • Iatrogenic Hypoparathyroidism

    hypoparathyroidism resulting from medical treatment or intervention.
  • Parathyroid Hormone Resistance|Pseudohypoparathyroidism|Pseudoparathyroidism

    a finding indicating decreased tissue sensitivity to parathyroid hormone.
  • Primary Hypoparathyroidism

    abnormally low levels of parathyroid hormone due to a disorder originating within the parathyroid glands.
  • Pseudohypoparathyroidism

    a condition characterized by the insensitivity of the tissues to respond to the activity of the parathyroid hormone. it results in increased levels of parathyroid hormone in the serum, hypocalcemia, and hyperphosphatemia.
  • Renal Parathyroid Hormone Resistance|Pseudohypoparathyroidism Type 1b

    parathyroid hormone resistance caused by defects in methylation in the gnas gene that cause loss of expression of gs-alpha from the maternal allele in renal tissue, resulting in decreased phosphate excretion and increased calcium excretion. individuals with this condition may also have brachydactyly and partial resistance to thyroid-stimulating hormone.
  • Secondary Parathyroid Hormone Resistance|Acquired Parathyroid Hormone Resistance|Acquired Parathyroid Hormone Resistance|Pseudohypoparathyroidism, Type 2|Pseudohypoparathyroidism, Type 2

    parathyroid hormone (pth) resistance caused by vitamin d deficiency and characterized by clinically increased pth concentrations with relative hyperphosphatemia. the diagnosis can be confirmed by finding of a normal cyclic adenosine monophosphate (camp) response to pth infusion, but deficient phosphaturic response, indicating a defect distal to camp generation in renal cells.
  • TBCE wt Allele|HRD|Hypoparathyroidism, Growth and Mental Retardation, and Dysmorphism Gene|KCS|KCS1|Kenny-Caffey Syndrome Gene|PEAMO|Tubulin Folding Cofactor E wt Allele|pac2

    human tbce wild-type allele is located in the vicinity of 1q42.3 and is approximately 85 kb in length. this allele, which encodes tubulin-specific chaperone e protein, is involved in both tubulin folding and tubulin dimer dissociation. mutations in the gene are associated with progressive encephalopathy with amyotrophy and optic atrophy, hypoparathyroidism-retardation-dysmorphism syndrome and kenny-caffey syndrome 1.
  • Transient Neonatal Hypoparathyroidism

    a disorder of decreased production of parathyroid hormone by the parathyroid gland in a newborn. it is due to maternal hyperparathyroidism. it may be characterized by hypocalcemic seizures in the first weeks of life.
  • X-Linked Hypoparathyroidism|X-linked Hypoparathyroidism

    hypoparathyroidism in which the inheritance is recessive and linked to the q26-q27 region of the x chromosome. the parathyroid glands are usually incompletely developed (parathyroid dysgenesis) or absent (parathyroid agenesis).
  • Tetany

    sudden and involuntary contraction of a muscle of group of muscles due to hypocalcemia.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Parathyroid tetany

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert E20.9 to ICD-9-CM

  • ICD-9-CM Code: 252.1 - Hypoparathyroidism
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Parathyroid Disorders

Most people have four pea-sized glands, called parathyroid glands, on the thyroid gland in the neck. Though their names are similar, the thyroid and parathyroid glands are completely different. The parathyroid glands make parathyroid hormone (PTH), which helps your body keep the right balance of calcium and phosphorous.

If your parathyroid glands make too much or too little hormone, it disrupts this balance. If they secrete extra PTH, you have hyperparathyroidism, and your blood calcium rises. In many cases, a benign tumor on a parathyroid gland makes it overactive. Or, the extra hormones can come from enlarged parathyroid glands. Very rarely, the cause is cancer.

If you do not have enough PTH, you have hypoparathyroidism. Your blood will have too little calcium and too much phosphorous. Causes include injury to the glands, endocrine disorders, or genetic conditions. Treatment is aimed at restoring the balance of calcium and phosphorous.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.