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  2. ICD-10-CM Codes List
  3. E00–E89
  4. E20-E35
  5. Hypoparathyroidism (E20)

Hypoparathyroidism (E20)

Hypoparathyroidism is coded under E20 in ICD-10 and covers conditions where the parathyroid glands produce insufficient hormone, leading to low calcium levels. These codes specifically identify the type and cause of hypoparathyroidism for accurate clinical documentation and treatment planning.

The main ICD-10 codes include E20.0 for idiopathic hypoparathyroidism, which might present as cataracts due to this unexplained cause. E20.1 refers to pseudohypoparathyroidism and its subtypes, often linked with resistance to parathyroid hormone, with synonyms like pseudopseudohypoparathyroidism clarifying differential diagnoses. Other codes, such as E20.81 and its subcategories, specify hypoparathyroidism due to impaired parathyroid hormone secretion, including inherited forms like autosomal dominant hypocalcemia (E20.810) and autoimmune causes (E20.812). Codes like E20.89 and E20.9 account for other specified or unspecified hypoparathyroidism, covering conditions such as neonatal or transient types and related systemic complications like tetany or cataracts. Using the precise ICD-10 code for hypoparathyroidism ensures clear communication between healthcare providers and accurate patient record-keeping for these varied endocrine disorders.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • Di George's syndrome D82.1
  • postprocedural hypoparathyroidism E89.2
  • tetany NOS R29.0
  • transitory neonatal hypoparathyroidism P71.4

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Hypoparathyroidism

A condition caused by a deficiency of PARATHYROID HORMONE (or PTH). It is characterized by HYPOCALCEMIA and hyperphosphatemia. Hypocalcemia leads to TETANY. The acquired form is due to removal or injuries to the PARATHYROID GLANDS. The congenital form is due to mutations of genes, such as TBX1; (see DIGEORGE SYNDROME); CASR encoding CALCIUM-SENSING RECEPTOR; or PTH encoding parathyroid hormone.

Pseudohypoparathyroidism

A hereditary syndrome clinically similar to HYPOPARATHYROIDISM. It is characterized by HYPOCALCEMIA; HYPERPHOSPHATEMIA; and associated skeletal development impairment and caused by failure of response to PARATHYROID HORMONE rather than deficiencies. A severe form with resistance to multiple hormones is referred to as Type 1a and is associated with maternal mutant allele of the ALPHA CHAIN OF STIMULATORY G PROTEIN.

Pseudopseudohypoparathyroidism

A form of PSEUDOHYPOPARATHYROIDISM characterized by the same features except for the abnormal response to hormones such as PARATHYROID HORMONE. It is associated with paternally inherited mutant alleles of the ALPHA CHAIN OF STIMULATORY G PROTEIN.

Tetany

A disorder characterized by muscle twitches, cramps, and carpopedal spasm, and when severe, laryngospasm and seizures. This condition is associated with unstable depolarization of axonal membranes, primarily in the peripheral nervous system. Tetany usually results from HYPOCALCEMIA or reduced serum levels of MAGNESIUM that may be associated with HYPERVENTILATION; HYPOPARATHYROIDISM; RICKETS; UREMIA; or other conditions. (From Adams et al., Principles of Neurology, 6th ed, p1490)