2027 ICD-10-CM Diagnosis Code Q74.0Other congenital malformations of upper limb(s), including shoulder girdle

ICD-10-CM Codes›Q00-Q99›Q65-Q79›s

ICD-10-CM Q74.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q74.0 is a billable ICD-10-CM diagnosis code for other congenital malformations of upper limb(s), including shoulder girdle. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q74.0
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of upper limb(s), including shoulder girdle
Short Description
Oth congen malform of upper limb(s), inc shoulder girdle
Parent Code
Q74
Other congenital malformations of limb(s)

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategorysOther congenital malformations of limb (Q74)
This CodeQ74.0Other congenital malformations of upper limb(s), including shoulder girdle

Present on Admission (POA)Billing

Q74.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aberrant forearm extensor muscle
  • Aberrant intrinsic muscles of hand
  • Aberrant muscle of the upper limb
  • Abnormal tapering of humerus
  • Absence of clavicle
  • Absence of scapula
  • Accessory carpal bones
  • Acrodysplasia scoliosis
  • Acrosyndactyly of the fingers
  • Adducted thumbs and arthrogryposis syndrome Christian type
  • Agenesis of clavicle
  • Agenesis of scapula
  • Amegakaryocytic thrombocytopenia
  • Amegakaryocytic thrombocytopenia with congenital malformation
  • Antecubital pterygium syndrome
  • Aplasia of bone of radius and/or ulna
  • Aplasia of bone of thorax
  • Aplasia of clavicle
  • Aplasia of humerus
  • Aplasia of radius
  • Aplasia of scapula
  • Asymmetric dysplasia of radius
  • Atrioventricular septal defect, blepharophimosis, radial and anal defect syndrome
  • Bifid digit
  • Bifid thumb
  • Bilateral accessory carpal bone of wrists
  • Bilateral congenital abnormal fusion of carpal bones
  • Bilateral congenital anomaly of upper limbs
  • Bilateral congenital cubitus varus
  • Bilateral congenital deformity of upper limbs
  • Bilateral congenital dislocation of hip
  • Bilateral congenital dysplasia of upper limbs
  • Bilateral congenital elevation of scapulae
  • Bilateral congenital upper limb hypertrophy
  • Bilateral humeroradial synostosis
  • Bilateral humero-ulnar synostosis
  • Bilateral Madelung deformity
  • Bilateral polydactyly of thumb
  • Bilateral radioulnar synostosis
  • Bilateral triphalangeal thumb
  • Bowing of upper limb
  • Brachymesophalangia
  • Capitate-hamate synostosis
  • Char syndrome
  • Cleft mandible
  • Cleidocranial dysostosis
  • Congenital abnormal fusion of bones of upper limb
  • Congenital abnormal fusion of carpal and metacarpal bone
  • Congenital abnormal fusion of carpal bone
  • Congenital abnormal fusion of humerus
  • Congenital abnormal fusion of left carpal bones
  • Congenital abnormal fusion of metacarpal bone
  • Congenital abnormal fusion of radius
  • Congenital abnormal fusion of right carpal bones
  • Congenital abnormal fusion of scapula with humerus bone
  • Congenital abnormal fusion of second metacarpal bone
  • Congenital abnormal fusion of ulna
  • Congenital abnormal shape of carpal bone
  • Congenital abnormal shape of clavicle
  • Congenital abnormal shape of humerus
  • Congenital abnormal shape of metacarpal bone
  • Congenital abnormal shape of radius
  • Congenital abnormal shape of scapula
  • Congenital abnormal shape of ulna
  • Congenital abnormal slender shape of diaphysis of long bone
  • Congenital abnormal slender shape of forearm bone
  • Congenital abnormal slender shape of humerus
  • Congenital abnormal slender shape of long bone
  • Congenital abnormal slender shape of radius
  • Congenital abnormal slender shape of shaft of humerus
  • Congenital abnormal slender shape of ulna
  • Congenital absence of carpal bone
  • Congenital absence of humerus
  • Congenital absence of part of upper arm
  • Congenital absence of radius
  • Congenital absence of scapula
  • Congenital amputation of upper limb
  • Congenital anomalies of elbow and upper arm
  • Congenital anomaly of bone of shoulder girdle
  • Congenital anomaly of carpal bone
  • Congenital anomaly of humerus
  • Congenital anomaly of left upper limb
  • Congenital anomaly of metacarpal bone
  • Congenital anomaly of radius
  • Congenital anomaly of right upper limb
  • Congenital anomaly of scapula
  • Congenital anomaly of ulna
  • Congenital anomaly of upper limb
  • Congenital bent humerus
  • Congenital bent radius
  • Congenital bent scapula
  • Congenital bilateral cubitus valgus
  • Congenital bilateral radioulnar synostosis
  • Congenital bowing of ulna
  • Congenital cubitus valgus
  • Congenital cubitus varus
  • Congenital cubitus varus of left elbow
  • Congenital cubitus varus of right elbow
  • Congenital deformity of bilateral clavicles
  • Congenital deformity of bilateral forearms
  • Congenital deformity of bone of forearm
  • Congenital deformity of clavicle
  • Congenital deformity of left clavicle
  • Congenital deformity of left forearm
  • Congenital deformity of left upper limb
  • Congenital deformity of right clavicle
  • Congenital deformity of right forearm
  • Congenital deformity of right upper limb
  • Congenital deformity of scapula
  • Congenital deformity of shoulder
  • Congenital deformity of upper arm
  • Congenital deformity of upper limb
  • Congenital dislocation of elbow
  • Congenital dislocation of glenohumeral joint
  • Congenital dislocation of joint of shoulder region
  • Congenital dislocation of left glenohumeral joint
  • Congenital dislocation of left hip
  • Congenital dislocation of patella
  • Congenital dislocation of radial head
  • Congenital dislocation of right glenohumeral joint
  • Congenital dislocation of right hip
  • Congenital dolichostenomelia
  • Congenital dysplasia of joint of left shoulder region
  • Congenital dysplasia of joint of right shoulder region
  • Congenital dysplasia of joint of shoulder region
  • Congenital dysplasia of left upper limb
  • Congenital dysplasia of radius
  • Congenital dysplasia of right upper limb
  • Congenital elevation of left scapula
  • Congenital elevation of right scapula
  • Congenital elevation of scapula
  • Congenital facial asymmetry
  • Congenital glenoid dysplasia
  • Congenital glenoid dysplasia of bilateral scapulae
  • Congenital glenoid dysplasia of left scapula
  • Congenital glenoid dysplasia of right scapula
  • Congenital humeral varus
  • Congenital hypoplasia of bone of radius and/or ulna
  • Congenital hypoplasia of bone of thorax
  • Congenital hypoplasia of cerebral hemisphere
  • Congenital hypoplasia of cerebral white matter
  • Congenital hypoplasia of clavicle
  • Congenital hypoplasia of glenoid cavity
  • Congenital hypoplasia of radius
  • Congenital hypoplasia of scapula
  • Congenital left cubitus valgus
  • Congenital left radioulnar synostosis
  • Congenital macrodactyly
  • Congenital malformation of thumb
  • Congenital malposition of carpal bone
  • Congenital malposition of humerus
  • Congenital malposition of metacarpal bone
  • Congenital malposition of radius
  • Congenital malposition of ulna
  • Congenital negative ulnar variant of wrist
  • Congenital omphalocele
  • Congenital omphalocele, diaphragmatic hernia, cardiovascular anomalies, radial ray defect syndrome
  • Congenital positive ulnar variant of bilateral wrists
  • Congenital positive ulnar variant of wrist
  • Congenital pseudoarthrosis of clavicle
  • Congenital pseudoarthrosis of limb
  • Congenital radioulnar synostosis
  • Congenital right cubitus valgus
  • Congenital right radioulnar synostosis
  • Congenital scoliosis deformity of spine
  • Congenital subluxation of carpus
  • Congenital synostosis of bilateral humerus, radius, and ulna
  • Congenital synostosis of second metacarpal bone with trapezoid bone
  • Congenital thickening of humerus
  • Congenital thickening of radius
  • Congenital thickening of scapula
  • Congenital thickening of ulna
  • Congenital trigger finger
  • Congenital trigger finger of bilateral hands
  • Congenital trigger finger of left hand
  • Congenital trigger finger of right hand
  • Congenital ulnar positive variant of left wrist
  • Congenital ulnar positive variant of right wrist
  • Congenital umbilical hernia
  • Constricting band of extremity
  • Constriction ring of upper limb with acrosyndactyly and amputation
  • Constriction ring of upper limb with lymphedema
  • Constriction ring syndrome
  • Constriction ring syndrome of upper limb
  • Craniofacial microsomia
  • Craniolacunia
  • Deformity of humerus
  • Deformity of radius
  • Deformity of scapula
  • Deformity of ulna
  • Dislocation of joint of left shoulder region due to congenital dysplasia of joint of left shoulder region
  • Dislocation of joint of right shoulder region due to congenital dysplasia of joint of right shoulder region
  • Dislocation of joint of shoulder region due to congenital dysplasia of joint of shoulder region
  • Distal radioulnar synostosis
  • Duane-radial ray syndrome
  • Duane's syndrome
  • Duplication of humerus
  • Duplication of radius
  • Duplication of upper limb
  • Duplication of whole hand
  • Duplication of whole limb
  • Duplication of whole upper limb
  • Failure of differentiation of bones of forearm
  • Femur fibula ulna complex
  • Frontonasal dysplasia sequence
  • Frontonasal dysplasia, bifid nose, upper limb anomalies syndrome
  • Generalized spacing of maxillary teeth
  • Hemifacial microsomia
  • Hemifacial microsomia with radial defect syndrome
  • Hip pathological dislocation
  • Hitch-hiker thumb
  • Humeroradial synostosis
  • Humeroradioulnar synostosis
  • Humeroulnar synostosis
  • Humerus trochlea aplasia
  • Hydrocephalus, costovertebral dysplasia, Sprengel anomaly syndrome
  • Hyperphalangy
  • Hypertrophy of humerus
  • Hypertrophy of radius
  • Hypertrophy of scapula
  • Hypertrophy of ulna
  • Hypertrophy of upper limb
  • Hypoplasia of corpus callosum
  • Hypoplasia of radius
  • Incomplete ossification of carpal bone
  • Incomplete ossification of humerus
  • Incomplete ossification of metacarpal bone
  • Incomplete ossification of radius
  • Incomplete ossification of scapula
  • Incomplete ossification of ulna
  • L1 syndrome
  • Lack of ossification of carpal bone
  • Lack of ossification of humerus
  • Lack of ossification of metacarpal bone
  • Lack of ossification of radius
  • Lack of ossification of scapula
  • Lack of ossification of ulna
  • Left accessory carpal bone of wrist
  • Left radioulnar synostosis
  • Liebenberg syndrome
  • Localized congenital skull defect
  • Lunate-triquetrum synostosis
  • Lymphedema of upper limb
  • Macrodactylia of fingers
  • Macrodactyly of hand
  • Macrodactyly of left finger
  • Macrodactyly of thumb
  • Macromelia
  • Madelung's deformity
  • Manus plana
  • Mesomelic dysplasia of upper limb
  • Morava Mehes syndrome
  • Oto-onycho-peroneal syndrome
  • Overgrowth of partial upper limb
  • Overgrowth of upper limb
  • Overgrowth of whole upper limb
  • Parietal foramina with clavicular hypoplasia
  • Partial radial absence
  • Pathological dislocation of bilateral hips
  • Pathological dislocation of left hip
  • Pathological dislocation of right hip
  • Pelvis shoulder dysplasia
  • PHAVER syndrome
  • Polydactyly of left thumb
  • Polydactyly of right thumb
  • Proximal radioulnar synostosis
  • Pseudoarthrosis
  • Pseudoarthrosis of clavicle
  • Radioulnar dysostosis
  • Radioulnar synostosis
  • Radioulnar synostosis and dislocation of radial head
  • Radioulnar synostosis with amegakaryocytic thrombocytopenia syndrome
  • Radioulnar synostosis with developmental delay and hypotonia syndrome
  • Radioulnar synostosis with microcephaly and scoliosis syndrome
  • Right accessory carpal bone of wrist
  • Right radioulnar synostosis
  • Robin sequence
  • Scaphoid-lunate synostosis
  • Schmitt Gillenwater Kelly syndrome
  • Short stature, Pierre Robin sequence, cleft mandible, hand anomalies, clubfoot syndrome
  • Spondylometaphyseal dysplasia, bowed forearms, facial dysmorphism syndrome
  • Steel syndrome
  • Supernumerary metacarpal bone
  • Thin clavicle
  • Tibial hemimelia, polysyndactyly, triphalangeal thumb syndrome
  • Triphalangeal thumb
  • Triphalangeal thumb and dislocation of patella syndrome
  • Triphalangeal thumb and polysyndactyly syndrome
  • Triphalangeal thumb with brachyectrodactyly syndrome
  • True congenital shoulder dislocation
  • Ulnar dimelia
  • Ulnar mammary syndrome
  • Undergrowth of whole hand
  • Upper limb defect with eye and ear abnormalities syndrome
  • Windblown hand

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q74.0: its own notes plus those printed at Q74 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Accessory carpal bones
  • Cleidocranial dysostosis
  • Congenital pseudarthrosis of clavicle
  • Macrodactylia (fingers)
  • Madelung's deformity
  • Radioulnar synostosis
  • Sprengel's deformity
  • Triphalangeal thumb

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q74 Other congenital malformations of limb(s) applies to 6 codes

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q74.0, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q74.0: they are not reported together with it, unless the two conditions are unrelated.

  • M20 Acquired deformities of fingers and toes
    congenital deformities and malformations of fingers and toes (Q66.-, Q68-Q70, Q74.-) names Q74.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cleidocranial Dysplasia

    autosomal dominant syndrome in which there is delayed closing of the cranial fontanelles; complete or partial absence of the collarbones (clavicles); wide pubic symphysis; short middle phalanges of the fifth fingers; and dental and vertebral anomalies.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q74.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
755.53 Radioulnar synostosis
Approximate The match is approximate rather than exact.
ICD-9-CM
755.54 Madelung's deformity
Approximate The match is approximate rather than exact.
ICD-9-CM
755.56 Accessory carpal bones
Approximate The match is approximate rather than exact.
ICD-9-CM
755.57 Macrodactylia (fingers)
Approximate The match is approximate rather than exact.
ICD-9-CM
755.59 Upper limb anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q74.0Overview

Is Q74.0 (Other congenital malformations of limb(s)) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of upper limb(s), including shoulder girdle on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q74.0 group to?

When other congenital malformations of upper limb(s), including shoulder girdle is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q74.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of upper limb(s), including shoulder girdle on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.

Can Q74.0 be reported with a code from Q69?

Not as a rule. The Excludes1 note at Q74, which applies to Q74.0, lists "polydactyly (Q69.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of Q74.0?

Under the General Equivalence Mappings, other congenital malformations of upper limb(s), including shoulder girdle converts to ICD-9-CM 755.53 (radioulnar synostosis), 755.54 (Madelung's deformity), and 755.56 (accessory carpal bones). The mapping is approximate, so confirm the match fits the documentation.