2024 ICD-10-CM Diagnosis Code Q74.3

Arthrogryposis multiplex congenita

ICD-10-CM Code:
Q74.3
ICD-10 Code for:
Arthrogryposis multiplex congenita
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations and deformations of the musculoskeletal system
      (Q65-Q79)
      • Other congenital malformations of limb (Q74)
        (s)

Q74.3 is a billable diagnosis code used to specify a medical diagnosis of arthrogryposis multiplex congenita. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adducted thumbs and arthrogryposis syndrome Christian type
  • Akinesia
  • Akinesia
  • Akinesia
  • Antenatal multi-minicore disease with arthrogryposis multiplex congenita
  • Anterior horn cell disease
  • Arthrogryposis
  • Arthrogryposis and ectodermal dysplasia syndrome
  • Arthrogryposis hyperkeratosis syndrome lethal form
  • Arthrogryposis with oculomotor limitation and electroretinal anomaly
  • Arthrogryposis with renal dysfunction and cholestasis syndrome
  • Autism spectrum disorder, epilepsy, arthrogryposis syndrome
  • Autosomal recessive myogenic arthrogryposis multiplex congenita
  • Congenital abnormality of nipple
  • Congenital arthrogryposis due to teratogen
  • Congenital hypoplasia of breast
  • Congenital muscular dystrophy with arthrogryposis multiplex congenita
  • Digitotalar dysmorphism
  • Distal arthrogryposis syndrome
  • Distal arthrogryposis type 10
  • Distal arthrogryposis type 3
  • Distal arthrogryposis type 4
  • Distal arthrogryposis type 5D
  • Distal arthrogryposis type 6
  • Familial arthrogryposis-cholestatic hepatorenal syndrome
  • Hepatorenal syndrome
  • Hyperpyrexia
  • Hypomyelination neuropathy arthrogryposis syndrome
  • Hypoplasia of nipple
  • Illum syndrome
  • Inherited arthrogryposis
  • Inherited disorder of bilirubin metabolism
  • Inherited disorder of bilirubin metabolism
  • Joint contracture, webbed neck, micrognathia, hypoplastic nipple syndrome
  • Kuskokwim syndrome
  • Lethal arthrogryposis with anterior horn cell disease
  • Lethal congenital contracture syndrome type 1
  • Lethal congenital contracture syndrome type 2
  • Lethal congenital contracture syndrome type 3
  • Lethal congenital contracture syndrome type 5
  • Malignant hyperthermia
  • Malignant hyperthermia with arthrogryposis and torticollis syndrome
  • Morse Rawnsley Sargent syndrome
  • Multi-core congenital myopathy
  • MYBPC1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome
  • Neck webbing
  • Neurogenic arthrogryposis multiplex congenita
  • Neurogenic arthrogryposis multiplex congenita
  • Pelvic dysplasia, arthrogryposis of lower limbs syndrome
  • Rozin Hertz Goodman syndrome
  • Sheldon-Hall syndrome
  • X-linked distal arthrogryposis multiplex congenita
  • X-linked distal hereditary motor neuropathy

Clinical Classification

Clinical Information

  • Arthrogryposis

    persistent flexure or contracture of a joint.
  • Malignant Hyperthermia

    rapid and excessive rise of temperature accompanied by muscular rigidity following general anesthesia.
  • Hepatorenal Syndrome

    functional kidney failure in patients with liver disease, usually liver cirrhosis or portal hypertension (hypertension, portal), and in the absence of intrinsic renal disease or kidney abnormality. it is characterized by intense renal vasculature constriction, reduced renal blood flow, oliguria, and sodium retention.
  • Arthrogryposis

    a rare, non-progressive congenital disorder characterized by multiple joint contractures which are present at birth.
  • Congenital Contractural Arachnodactyly|Arthrogryposis, Distal, Type 9|Beals Syndrome|CCA

    an autosomal dominant connective tissue disorder caused by mutation(s) in the fbn2 gene, encoding fibrillin-2. it is characterized by contractures, arachnodactyly, scoliosis, micrognathia, and crumpled ears.
  • Freeman-Sheldon Syndrome|Cranio-Carpo-Tarsal Syndrome|Craniocarpotarsal Dysplasia|DA2A|Distal Arthrogryposis Type 2A|Freeman Sheldon Syndrome|Whistling-Face Syndrome|Windmill-Vane-Hand Syndrome

    a rare syndrome that is inherited in an autosomal dominant or recessive pattern and caused by mutations in the myh3 gene. it is a severe form of arthrogryposis. it is characterized by the presence of distinctive facial features (small mouth, midface hypoplasia, short nose, drooping of the eyelids, deep folds in the area between the nose and the lips, and strabismus), joint deformities that lead to permanently bent fingers and toes, club foot, scoliosis, and walking difficulties.
  • TPM2 wt Allele|AMCD1|Arthrogryposis Multiplex Congenital, Distal, Type 1 Gene|DA1|DA2B|HEL-S-273|NEM4|Nemaline Myopathy Type 4 Gene|TMSB|Tropomyosin 2 (Beta) wt Allele|Tropomyosin, Skeletal Muscle Beta Gene

    human tpm2 wild-type allele is located in the vicinity of 9p13 and is approximately 9 kb in length. this allele, which encodes tropomyosin beta chain protein, is involved in muscle contraction. mutation of the gene is associated with nemaline myopathy type 4, cap myopathy type 2 and distal arthrogryposis types 1a and 2b.
  • Akinesia

    lack of movement.
  • Fetal Akinesia Deformation Sequence|FADS|Pena-Shokeir syndrome, Type 1

    a condition characterized by fetal akinesia and intrauterine growth restriction, that may be associated with mutation(s) in the rapsn or dok7 genes, encoding 43 kda receptor-associated protein of the synapse and protein dok-7, respectively.
  • Hyperpyrexia

    body temperature of 106 degrees fahrenheit (41.1 degrees celsius) or higher.
  • Malignant Hyperthermia Syndrome|Malignant Hyperpyrexia|Malignant Hyperthermia|Malignant Hyperthermia

    a rare disorder characterized by rapid rise of the body temperature, accompanied by rhabdomyolysis and, if untreated, by collapse and death. it occurs in susceptible individuals who receive certain drugs for general anesthesia, gas anesthetics, or succinylcholine. it may be inherited in an autosomal dominant pattern.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q74.3 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q74.3 to ICD-9-CM

  • ICD-9-CM Code: 754.89 - Nonteratogenic anom NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Sheldon-Hall syndrome

Sheldon-Hall syndrome, also known as distal arthrogryposis type 2B, is a disorder characterized by joint deformities (contractures) that restrict movement in the hands and feet. The term "arthrogryposis" comes from the Greek words for joint (arthro-) and crooked or hooked (gryposis). "Distal" refers to areas of the body away from the center. The characteristic features of this condition include permanently bent fingers and toes (camptodactyly), overlapping fingers, and a hand deformity called ulnar deviation in which all of the fingers are angled outward toward the fifth (pinky) finger. Inward- and upward-turning feet (a condition called clubfoot) is also commonly seen in Sheldon-Hall syndrome. The specific hand and foot abnormalities vary among affected individuals; the abnormalities are present at birth and generally do not get worse over time.

People with Sheldon-Hall syndrome also usually have distinctive facial features, which include a triangular face; outside corners of the eyes that point downward (down-slanting palpebral fissures); deep folds in the skin between the nose and lips (nasolabial folds); and a small mouth with a high, arched roof of the mouth (palate). Other features that may occur in Sheldon-Hall syndrome include extra folds of skin on the neck (webbed neck) and short stature.

Sheldon-Hall syndrome does not usually affect other parts of the body, and intelligence and life expectancy are normal in this disorder.


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Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.