2026 ICD-10-CM Diagnosis Code Q25.49Other congenital malformations of aorta

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.49
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.49 is a billable ICD-10-CM diagnosis code for other congenital malformations of aorta. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.49
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of aorta
Short Description
Other congenital malformations of aorta
Same as the full description in the CMS dataset.
Parent Code
Q25.4
Other congenital malformations of aorta

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.49Other congenital malformations of aorta

Present on Admission (POA)Billing

Q25.49 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal course of aortic arch
  • Abnormal course of aortic arch and descending aorta
  • Abnormality of aortic arch
  • Aneurysm of aortic sinus of Valsalva with protrusion into left atrium
  • Anomalies of the aorta excluding coarction
  • Anomalous common origin of brachiocephalic artery and left common carotid artery
  • Anomalous origin of arterial duct from aortic diverticulum
  • Anomalous origin of arterial ligament from aortic diverticulum
  • Anomalous origin of arterial ligament from retroesophageal aortic diverticulum
  • Anomalous origin of the aortic arch
  • Aorta to right ventricle tunnel
  • Aortic arch centrally descending
  • Aortic left ventricular tunnel
  • Aortic left ventricular tunnel with right coronary artery from tunnel
  • Aortic orifice to posterior right of pulmonary orifice
  • Aortic root congenital abnormality
  • Aortic sinus of Valsalva aneurysm from noncoronary sinus
  • Aortic tunnel
  • Aortico-left ventricular tunnel with intracardiac aneurysm of septal portion
  • Ascending aorta absent
  • Cervical aortic arch
  • Coarctation of aortic arch
  • Common arterial trunk with obstruction of aortic arch
  • Common arterial trunk with pulmonary dominance
  • Common arterial trunk with pulmonary dominance and interrupted aortic arch
  • Congenital abnormalities of thoracic aortic branches
  • Congenital abnormality of supraaortic branch of thoracic aorta
  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital absence of aorta
  • Congenital absence of left pulmonary artery
  • Congenital aneurysm of aorta
  • Congenital anomaly of abdominal aorta
  • Congenital anomaly of aorta
  • Congenital anomaly of aortic arch
  • Congenital anomaly of aortic arch AND/OR descending aorta
  • Congenital anomaly of descending thoracic aorta
  • Congenital atresia of pulmonary valve
  • Congenital dilatation of aorta
  • Congenital dilation of ascending aorta
  • Congenital duplication of aorta
  • Congenital malposition of aorta
  • Descending aorta anterior and same side as azygos vein with absent inferior vena cava
  • Descending aorta anterior and same side as azygos vein with azygos continuity of inferior caval vein
  • Developmental malformation of branchial arch
  • Dextrotransposition of aorta
  • Interrupted aortic arch
  • Interrupted aortic arch between left subclavian and left common carotid artery
  • Interruption of aortic arch between subclavian artery and common carotid artery
  • Isolation of branch of aortic arch
  • Isolation of left subclavian artery
  • Isolation of subclavian artery
  • Kommerell's diverticulum
  • Left aortic arch and right descending aorta
  • Major aortopulmonary collateral artery
  • Major systemic to pulmonary collateral artery
  • Malalignment of aortic sinus in relation to pulmonary sinus
  • Neuhauser anomaly
  • Obstruction of aortic arch
  • Overriding aorta
  • Persistent aortic arch convolutions
  • Persisting fifth aortic arch
  • Persisting fifth aortic arch with atresia of fourth arch
  • Preductal coarctation of aorta
  • Preductal interruption of aorta
  • Pseudocoarctation of aorta
  • Retroesophageal aortic arch
  • Sinus of Valsalva abnormality
  • Solitary aortic trunk with pulmonary atresia
  • Systemic to pulmonary collateral artery from abdominal aorta
  • Systemic to pulmonary collateral artery from descending thoracic aorta
  • Vascular ring of aorta
  • Vascular ring with left aortic arch
  • Vascular ring with left aortic arch and retroesophageal right descending aorta and right arterial duct arising from aortic diverticulum and aberrant right subclavian artery
  • Vascular ring with left aortic arch and retrotracheal right patent arterial duct
  • Vascular ring with left aortic arch and right arterial duct arising from aberrant retroesophageal right subclavian artery
  • Vascular ring with left aortic arch and right arterial duct arising from retroesophageal aortic diverticulum
  • Vascular ring with left aortic arch and right arterial duct arising from retroesophageal aortic diverticulum and aberrant right subclavian artery
  • Vascular ring with left aortic arch and right arterial duct ligament arising from retroesophageal aortic diverticulum with aberrant right subclavian artery
  • Vascular ring with left aortic arch and right arterial ligament
  • Vascular ring with left aortic arch and right patent arterial duct
  • Vascular ring with left aortic arch to right descending aorta and right arterial ligament
  • Vascular ring with left aortic arch to right descending aorta and right patent arterial duct
  • Vascular ring with mirror image branching of right aortic arch and left arterial ligament
  • Vascular ring with right aortic arch
  • Vascular ring with right aortic arch and left arterial duct from anomalous retroesophageal brachiocephalic artery
  • Vascular ring with right aortic arch and left arterial duct from anomalous retroesophageal left subclavian artery
  • Vascular ring with right aortic arch and left arterial duct from retroesophageal diverticulum of aorta
  • Vascular ring with right aortic arch and left arterial duct from retroesophageal diverticulum of aorta and anomalous left subclavian artery
  • Vascular ring with right aortic arch and left arterial ligament
  • Vascular ring with right aortic arch and left arterial ligament between left subclavian artery and left common carotid artery
  • Vascular ring with right aortic arch and left arterial ligament with anomalous retroesophageal left subclavian artery
  • Vascular ring with right aortic arch and left patent arterial duct
  • Vascular ring with right aortic arch and right arterial ligament with absent left pulmonary artery
  • Vascular ring with right aortic arch and right patent arterial duct with absent left pulmonary artery

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Aortic arch
  • Bovine arch

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • transverse aortic arch, congenital
    • Anomaly, anomalous(congenital) (unspecified type)
      • sinus of Valsalva
    • Arch
      • aortic
    • Arch
      • bovine
    • Congenital
      • aortic septum
    • Deformity
      • transverse aortic arch (congenital)
    • Malformation(congenital)
      • aorta
        • specified type NEC
    • Malposition
      • congenital
        • aorta
    • Overriding
      • aorta
    • Persistence, persistent(congenital)
      • left
        • root with right arch of aorta
    • Pseudotruncus arteriosus

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Interrupted Aortic Arch

    a rare congenital cardiovascular disorder characterized by the presence of a gap between the ascending and descending portions of the thoracic aorta. this disorder is often associated with ventricular septal defect, ductus arteriosus, or truncus arteriosus.

  • Overriding Aorta

    a congenital anatomic anomaly in which the aorta is positioned directly above a ventricular septal defect, thus receiving blood from both the right and left ventricles, resulting in an overall decrease in oxygenated haemoglobin and tissue cyanosis.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.49 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.29 Cong anom of aorta NEC
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement Q25.49 replaces the following previously assigned code(s):

  • Q25.4 - Other congenital malformations of aorta
FY 2018AddedAdded to the ICD-10-CM code setEffective October 1, 2017.
FY 2019–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.49Overview

Is Q25.49 (Other congenital malformations of aorta) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of aorta on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.49 group to?

When other congenital malformations of aorta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.49 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of aorta on inpatient claims.

What is the ICD-9 equivalent of Q25.49?

Under the General Equivalence Mappings, other congenital malformations of aorta converts to ICD-9-CM 747.29 (cong anom of aorta NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.