2026 ICD-10-CM Diagnosis Code Q22.3Other congenital malformations of pulmonary valve

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q22

ICD-10-CM Q22.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q22.3 is a billable ICD-10-CM diagnosis code for other congenital malformations of pulmonary valve. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q22.3
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of pulmonary valve
Short Description
Other congenital malformations of pulmonary valve
Same as the full description in the CMS dataset.
Parent Code
Q22
Congenital malformations of pulmonary and tricuspid valves

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ22Congenital malformations of pulmonary and tricuspid valves
This CodeQ22.3Other congenital malformations of pulmonary valve

Present on Admission (POA)Billing

Q22.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal number of pulmonary valve cusps
  • Abnormality of pulmonary valve cusp
  • Accessory tissue on pulmonary valve cusp
  • Acommissural unicuspid pulmonary valve
  • Anterior-posterior orientation of bicuspid pulmonary valve
  • Bicuspid pulmonary valve
  • Commissural fusion of pulmonary valve
  • Congenital abnormal shape of pulmonary valve
  • Congenital abnormality of arterial valves
  • Congenital abnormality of pulmonary valve cusp
  • Congenital dysplasia of cardiac valve
  • Congenital fusion of pulmonary valve segment
  • Congenital fusion of pulmonic cusps
  • Congenital hypertrophy of pulmonary valve
  • Congenital hypoplasia of pulmonary valve
  • Congenital pulmonary valve abnormality
  • Continuity between mitral valve and pulmonary valve
  • Discontinuity between mitral valve and pulmonary valve
  • Eccentric opening of tricuspid pulmonary valve
  • Fallot's trilogy
  • Fenestration of pulmonary valve cusp
  • Hypoplasia of pulmonary valve
  • Pulmonary valve cusp hypoplasia
  • Pulmonary valve dysplasia
  • Pulmonary valve overriding ventricular septum
  • Pulmonary valve ring hypoplasia
  • Quadricuspid pulmonary valve
  • Right-left orientation of bicuspid pulmonary valve
  • Supernumerary pulmonary valve cusps
  • Unicommissural unicuspid pulmonary valve
  • Unicuspid pulmonary valve
  • Ventricular septal defect with anterior malaligned outlet septum with overriding pulmonary valve
  • Ventricular septal defect with posterior malaligned outlet septum with overriding pulmonary valve

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital malformation of pulmonary valve NOS
  • Supernumerary cusps of pulmonary valve

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Accessory(congenital)
      • cusp (s), heart valve NEC
        • pulmonary
    • Accessory(congenital)
      • heart
        • valve NEC
          • pulmonary
    • Accessory(congenital)
      • valve, heart NEC
        • pulmonary
    • Anomaly, anomalous(congenital) (unspecified type)
      • cardiac
        • valve NEC
          • pulmonary
    • Anomaly, anomalous(congenital) (unspecified type)
      • heart
        • valve NEC
          • pulmonary
    • Anomaly, anomalous(congenital) (unspecified type)
      • pulmonary
        • valve
    • Anomaly, anomalous(congenital) (unspecified type)
      • pulmonary
        • valve
          • specified type NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • valve (heart) NEC
        • pulmonary
    • Development
      • defective, congenital
        • valve
          • pulmonary
    • Dilatation
      • cardiac (acute) (chronic)
        • congenital
          • valve NEC
            • pulmonary
    • Dilatation
      • pulmonary
        • valve, congenital
    • Disease, diseased
      • heart (organic)
        • valve, valvular (obstructive) (regurgitant)
          • congenital NEC
            • pulmonary
    • Fallot's
      • triad or trilogy
    • Fenestration, fenestrated
      • cusps, heart valve NEC
        • pulmonary
    • Fenestration, fenestrated
      • pulmonic cusps
    • Imperfect
      • closure (congenital)
        • cusps, heart valve NEC
          • pulmonary
    • Incompetency, incompetent, incompetence
      • pulmonary valve (heart)
        • congenital
    • Malformation(congenital)
      • pulmonary
        • valve
    • Supernumerary(congenital)
      • cusps, heart valve NEC
        • pulmonary
    • Supernumerary(congenital)
      • pulmonary, pulmonic cusps

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q22.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
746.00 Pulmonary valve anom NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q22.3Overview

Is Q22.3 (Congenital malformations of pulmonary and tricuspid valves) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of pulmonary valve on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q22.3 group to?

When other congenital malformations of pulmonary valve is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q22.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of pulmonary valve on inpatient claims.

What is the ICD-9 equivalent of Q22.3?

Under the General Equivalence Mappings, other congenital malformations of pulmonary valve converts to ICD-9-CM 746.00 (pulmonary valve anom NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.