2026 ICD-10-CM Diagnosis Code Q89.7Multiple congenital malformations, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.7
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.7 is a billable ICD-10-CM diagnosis code for multiple congenital malformations, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.7
Billable Status
Yes — Valid for Submission
Code Describes
Multiple congenital malformations, not elsewhere classified
Short Description
Multiple congenital malformations, not elsewhere classified
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.7Multiple congenital malformations, not elsewhere classified

Present on Admission (POA)Billing

Q89.7 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acephalobrachius
  • ADNP-related multiple congenital anomalies, intellectual disability, autism spectrum disorder
  • Akinesia
  • Autositic twin of asymmetrical conjoined twins
  • Cantu's syndrome
  • CK syndrome
  • Cloverleaf skull syndrome
  • Cloverleaf skull with multiple congenital anomalies syndrome
  • Complex craniosynostosis
  • Congenital complete absence of upper limb
  • Congenital generalized hypercontractile muscle stiffness syndrome
  • Duhamel's syndrome
  • Ectrodactyly-ectodermal dysplasia-clefting syndrome
  • Ethmocephalus
  • Fetal hereditary disease
  • Hydrolethalus syndrome
  • Lethal multiple pterygium syndrome
  • Male emopamil-binding protein disorder with neurological defect
  • Monocephalus
  • Monocephalus tripus dibrachius
  • Moore-Federman syndrome
  • Multiple congenital anomalies, hypotonia, seizures syndrome
  • Multiple congenital anomalies, hypotonia, seizures syndrome type 2
  • Multiple malformation syndrome with unusual brain and/or neuromuscular findings
  • Multiple pterygium syndrome
  • Native American myopathy
  • Ochoa syndrome
  • Omocephalus
  • Parieto-occipital craniosynostosis
  • Pentalogy of Cantrell
  • Sagittal craniosynostosis
  • SETD2-related microcephaly, severe intellectual disability, multiple congenital anomalies syndrome
  • Synotus
  • Timothy syndrome
  • Timothy syndrome type 2

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Multiple congenital anomalies NOS
  • Multiple congenital deformities NOS

Type 1 Excludes

  • congenital malformation syndromes affecting multiple systems Q87

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • multiple NEC
    • Deformity
      • multiple, congenital NEC
    • Malformation(congenital)
      • multiple types NEC
    • Monster, monstrosity(single)
    • Paracephalus
    • Teratism

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Pentalogy of Cantrell

    rare congenital deformity syndrome characterized by a combination of five anomalies as a result of neural tube defect. the five anomalies are a midline supraumbilical abdominal wall defect (e.g., omphalocele), a lower sternum defect, a congenital intracardiac defect, an anterior diaphragm defect, and a diaphragmatic pericardium defect (e.g., pericardial effusion). variants with incomplete and variable combinations of the defects are known. ectopia cordis; cleft lip; and cleft palate are often associated with the syndrome.

  • Pentalogy of Cantrell

    a rare syndrome characterized by the presence of omphalocele, anterior diaphragmatic hernia, sternal cleft, ectopia cordis, and ventricular septal defect or left ventricle diverticulum.

  • Akinesia

    lack of movement.

  • Fetal Akinesia Deformation Sequence|FADS|Pena-Shokeir syndrome, Type 1

    a condition characterized by fetal akinesia and intrauterine growth restriction, that may be associated with mutation(s) in the rapsn or dok7 genes, encoding 43 kda receptor-associated protein of the synapse and protein dok-7, respectively.

  • Lethal Multiple Pterygium Syndrome

    a rare variant of multiple pterygium syndrome, characterized by severe athrogryposis, pterygium, akinesia and often hydrops fetalis and cystic hygroma. this variant is fatal, usually during the second or third trimester of pregnancy.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.7 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.7 Mult congen anomal NEC
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.7Overview

Is Q89.7 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report multiple congenital malformations, not elsewhere classified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.7 group to?

When multiple congenital malformations, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.7 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for multiple congenital malformations, not elsewhere classified on inpatient claims.

What is the ICD-9 equivalent of Q89.7?

Under the General Equivalence Mappings, multiple congenital malformations, not elsewhere classified converts to ICD-9-CM 759.7 (mult congen anomal NEC). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.