2027 ICD-10-CM Diagnosis Code Q89.7Multiple congenital malformations, not elsewhere classified
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q89.7 is a billable ICD-10-CM diagnosis code for multiple congenital malformations, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 3 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q89.7 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acephalobrachius
- ADNP-related multiple congenital anomalies, intellectual disability, autism spectrum disorder
- Akinesia
- Asymmetrical conjoined twins
- Autositic twin of asymmetrical conjoined twins
- Cantu's syndrome
- CK syndrome
- Cloverleaf skull syndrome
- Cloverleaf skull with multiple congenital anomalies syndrome
- Complex craniosynostosis
- Congenital complete absence of upper limb
- Congenital generalized hypercontractile muscle stiffness syndrome
- Duhamel's syndrome
- Ectrodactyly-ectodermal dysplasia-clefting syndrome
- Ethmocephalus
- Fetal hereditary disease
- Hydrolethalus syndrome
- Lethal multiple pterygium syndrome
- Male emopamil-binding protein disorder with neurological defect
- Monocephalus
- Monocephalus tripus dibrachius
- Moore-Federman syndrome
- Multiple congenital anomalies, hypotonia, seizures syndrome
- Multiple congenital anomalies, hypotonia, seizures syndrome type 2
- Multiple malformation syndrome with unusual brain and/or neuromuscular findings
- Multiple pterygium syndrome
- Native American myopathy
- Ochoa syndrome
- Omocephalus
- Parieto-occipital craniosynostosis
- Pentalogy of Cantrell
- Sagittal craniosynostosis
- SETD2-related microcephaly, severe intellectual disability, multiple congenital anomalies syndrome
- Synotus
- Timothy syndrome
- Timothy syndrome type 2
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q89.7: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Multiple congenital anomalies NOS
- Multiple congenital deformities NOS
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- congenital malformation syndromes affecting multiple systems (Q87.-)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Malformation (congenital) See Also: Anomaly;
multiple types NEC Q89.7
Paracephalus Q89.7
Teratism Q89.7
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q89.7 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q89.7Overview
What is the ICD-10 code for multiple congenital malformations, not elsewhere classified?
The ICD-10-CM code for multiple congenital malformations, not elsewhere classified is Q89.7 (sometimes written as Q897). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q89.7 (Other congenital malformations, not elsewhere classified) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report multiple congenital malformations, not elsewhere classified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q89.7 group to?
When multiple congenital malformations, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q89.7 a CC or MCC?
CMS lists Q89.7 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 3 closely related codes in its exclusion list.
Is Q89.7 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for multiple congenital malformations, not elsewhere classified on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.
