2027 ICD-10-CM Diagnosis Code Q89.2Congenital malformations of other endocrine glands

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.2
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q89.2 is a billable ICD-10-CM diagnosis code for congenital malformations of other endocrine glands. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 643 through 645. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.2
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformations of other endocrine glands
Short Description
Congenital malformations of other endocrine glands
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.2Congenital malformations of other endocrine glands

Present on Admission (POA)Billing

Q89.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aberrant parathyroid gland
  • Aberrant thyroid gland
  • Accessory parathyroid gland
  • Accessory pituitary gland
  • Accessory thymic tissue
  • Accessory thyroid gland
  • Agenesis of thymus
  • Anterior pituitary hormone deficiency
  • Aplasia of parathyroid gland
  • Aplasia of thymus
  • Athyrotic hypothyroidism sequence
  • Autosomal dominant variant form of albumin
  • Cervical thymic remnant
  • Cervical thyroid remnant
  • Cone dystrophy
  • Congenital abnormal shape of thymus
  • Congenital absence of parathyroid gland
  • Congenital absence of pituitary gland
  • Congenital absence of thymus
  • Congenital anomaly of endocrine gland
  • Congenital anomaly of endocrine gonad
  • Congenital anomaly of parathyroid glands
  • Congenital anomaly of pituitary gland
  • Congenital anomaly of the thymus
  • Congenital anomaly of the thyroid gland
  • Congenital cleft of thymus
  • Congenital hypoplasia of anterior pituitary
  • Congenital hypoplasia of posterior pituitary
  • Congenital hypoplasia of thymus
  • Congenital hypothyroidism due to congenital anomaly of thyroid gland
  • Congenital hypothyroidism with ectopic thyroid
  • Congenital hypothyroidism without goiter
  • Congenital iodine deficiency syndrome
  • Congenital malformation of anterior pituitary
  • Congenital malformation of posterior pituitary
  • Congenital malposition of the thyroid gland
  • Congenital malposition of thymus
  • Duplication of pituitary gland
  • Ectopic pituitary tissue
  • Ectopic thymic tissue
  • Endocrine-cerebro-osteodysplasia syndrome
  • Familial isolated hypoparathyroidism
  • Familial thyroglossal duct cyst
  • Hereditary isolated hypoparathyroidism due to agenesis of parathyroid gland
  • Inherited disorder of thyroid metabolism
  • Lingual goiter
  • Lingual thyroid
  • Multiple malformation syndrome due to non-infectious environmental agents
  • Persistent thyroglossal duct
  • Pharyngeal pituitary tissue
  • Pituitary stalk interruption syndrome
  • Postaxial polydactyly, anterior pituitary anomalies, facial dysmorphism syndrome
  • Retinohepatoendocrinologic syndrome
  • Retrosternal thyroid gland
  • Short stature, pituitary and cerebellar defect and small sella turcica syndrome
  • Thymic, renal, anal, lung dysplasia syndrome
  • Thyroglossal duct anomaly
  • Thyroglossal duct cyst
  • Thyroglossal duct sinus
  • Thyroxine transport defect

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q89.2: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital malformation of parathyroid or thyroid gland
  • Persistent thyroglossal duct
  • Thyroglossal cyst

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • congenital goiter (E03.0)
  • congenital hypothyroidism (E03.1)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q89.2, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q89.2: they are not reported together with it, unless the two conditions are unrelated.

  • Q18 Other congenital malformations of face and neck
    persistent thyroglossal duct (Q89.2)

Excludes2 2

These codes carry an Excludes2 note naming Q89.2: its condition is not part of those codes, and both may be reported when the patient has both.

  • Block Q10-Q18 Congenital malformations of eye, ear, face and neck
    congenital malformation of parathyroid gland (Q89.2)
  • Block Q10-Q18 Congenital malformations of eye, ear, face and neck
    congenital malformation of thyroid gland (Q89.2)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.2 Endocrine anomaly NEC
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q89.2Overview

What is the ICD-10 code for congenital malformations of other endocrine glands?

The ICD-10-CM code for congenital malformations of other endocrine glands is Q89.2 (sometimes written as Q892). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q89.2 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformations of other endocrine glands on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q89.2 group to?

When congenital malformations of other endocrine glands is the principal diagnosis on an inpatient stay, it groups to MS-DRG 644, 645, 643, with relative weights from 0.7461 to 1.6138 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformations of other endocrine glands on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.

Can Q89.2 be reported with E03.0?

Not as a rule. The Excludes1 note on Q89.2 lists "congenital goiter (E03.0)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).