2026 ICD-10-CM Diagnosis Code Q89.2Congenital malformations of other endocrine glands

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.2 is a billable ICD-10-CM diagnosis code for congenital malformations of other endocrine glands. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 643 through 645. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.2
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformations of other endocrine glands
Short Description
Congenital malformations of other endocrine glands
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.2Congenital malformations of other endocrine glands

Present on Admission (POA)Billing

Q89.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aberrant parathyroid gland
  • Aberrant thyroid gland
  • Accessory parathyroid gland
  • Accessory pituitary gland
  • Accessory thymic tissue
  • Accessory thyroid gland
  • Agenesis of thymus
  • Anterior pituitary hormone deficiency
  • Aplasia of parathyroid gland
  • Aplasia of thymus
  • Athyrotic hypothyroidism sequence
  • Autosomal dominant variant form of albumin
  • Cervical thymic remnant
  • Cervical thyroid remnant
  • Cone dystrophy
  • Congenital abnormal shape of thymus
  • Congenital absence of parathyroid gland
  • Congenital absence of pituitary gland
  • Congenital absence of thymus
  • Congenital anomaly of endocrine gland
  • Congenital anomaly of endocrine gonad
  • Congenital anomaly of parathyroid glands
  • Congenital anomaly of pituitary gland
  • Congenital anomaly of the thymus
  • Congenital anomaly of the thyroid gland
  • Congenital cleft of thymus
  • Congenital hypoplasia of anterior pituitary
  • Congenital hypoplasia of posterior pituitary
  • Congenital hypoplasia of thymus
  • Congenital hypothyroidism due to congenital anomaly of thyroid gland
  • Congenital hypothyroidism with ectopic thyroid
  • Congenital hypothyroidism without goiter
  • Congenital iodine deficiency syndrome
  • Congenital malformation of anterior pituitary
  • Congenital malformation of posterior pituitary
  • Congenital malposition of the thyroid gland
  • Congenital malposition of thymus
  • Duplication of pituitary gland
  • Ectopic pituitary tissue
  • Ectopic thymic tissue
  • Endocrine-cerebro-osteodysplasia syndrome
  • Familial isolated hypoparathyroidism
  • Familial thyroglossal duct cyst
  • Hereditary isolated hypoparathyroidism due to agenesis of parathyroid gland
  • Inherited disorder of thyroid metabolism
  • Lingual goiter
  • Lingual thyroid
  • Persistent thyroglossal duct
  • Pharyngeal pituitary tissue
  • Pituitary stalk interruption syndrome
  • Postaxial polydactyly, anterior pituitary anomalies, facial dysmorphism syndrome
  • Retinohepatoendocrinologic syndrome
  • Retrosternal thyroid gland
  • Short stature, pituitary and cerebellar defect and small sella turcica syndrome
  • Thymic, renal, anal, lung dysplasia syndrome
  • Thyroglossal duct anomaly
  • Thyroglossal duct cyst
  • Thyroglossal duct sinus
  • Thyroxine transport defect

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital malformation of parathyroid or thyroid gland
  • Persistent thyroglossal duct
  • Thyroglossal cyst

Type 1 Excludes

  • congenital goiter E03.0
  • congenital hypothyroidism E03.1

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • endocrine gland NEC
    • Aberrant(congenital)
      • parathyroid gland
    • Aberrant(congenital)
      • pituitary gland
    • Aberrant(congenital)
      • thymus (gland)
    • Aberrant(congenital)
      • thyroid gland
    • Absence(of) (organ or part) (complete or partial)
      • endocrine gland (congenital) NEC
    • Absence(of) (organ or part) (complete or partial)
      • parathyroid gland (acquired)
        • congenital
    • Absence(of) (organ or part) (complete or partial)
      • pituitary gland (congenital)
    • Absence(of) (organ or part) (complete or partial)
      • thymus gland
    • Accessory(congenital)
      • endocrine gland NEC
    • Accessory(congenital)
      • parathyroid gland
    • Accessory(congenital)
      • pituitary gland
    • Accessory(congenital)
      • thymus gland
    • Accessory(congenital)
      • thyroid gland
    • Agenesis
      • endocrine (gland) NEC
    • Agenesis
      • parathyroid (gland)
    • Agenesis
      • pituitary (gland)
    • Agenesis
      • thymus (gland)
    • Anomaly, anomalous(congenital) (unspecified type)
      • endocrine gland NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • hypophyseal
    • Anomaly, anomalous(congenital) (unspecified type)
      • parathyroid gland
    • Anomaly, anomalous(congenital) (unspecified type)
      • pituitary (gland)
    • Anomaly, anomalous(congenital) (unspecified type)
      • thymus gland
    • Anomaly, anomalous(congenital) (unspecified type)
      • thyroid (gland)
    • Cyst(colloid) (mucous) (simple) (retention)
      • congenital NEC
        • thymus (gland)
    • Cyst(colloid) (mucous) (simple) (retention)
      • thyroglossal duct (infected) (persistent)
    • Cyst(colloid) (mucous) (simple) (retention)
      • thyrolingual duct (infected) (persistent)
    • Deformity
      • endocrine gland NEC
    • Deformity
      • hypophyseal (congenital)
    • Deformity
      • parathyroid (gland)
    • Deformity
      • pituitary (congenital)
    • Deformity
      • thymus (tissue) (congenital)
    • Deformity
      • thyroid (gland) (congenital)
    • Distortion(s) (congenital)
      • endocrine NEC
    • Distortion(s) (congenital)
      • parathyroid (gland)
    • Distortion(s) (congenital)
      • pituitary (gland)
    • Distortion(s) (congenital)
      • thymus (gland)
    • Distortion(s) (congenital)
      • thyroid (gland)
    • Ectopic, ectopia(congenital)
      • thyroid
    • Fistula(cutaneous)
      • thyroglossal duct
    • Goiter(plunging) (substernal)
      • lingual
    • Hypoplasia, hypoplastic
      • endocrine (gland) NEC
    • Hypoplasia, hypoplastic
      • parathyroid (gland)
    • Hypoplasia, hypoplastic
      • pituitary (gland) (congenital)
    • Hypoplasia, hypoplastic
      • thymus (gland)
    • Malformation(congenital)
      • parathyroid gland
    • Malformation(congenital)
      • thyroid gland
    • Malposition
      • congenital
        • endocrine (gland) NEC
    • Malposition
      • congenital
        • parathyroid (gland)
    • Malposition
      • congenital
        • pituitary (gland)
    • Malposition
      • congenital
        • thymus (gland)
    • Malposition
      • congenital
        • thyroid (gland) (tissue)
    • Nasopharyngeal
      • pituitary gland
    • Persistence, persistent(congenital)
      • thyroglossal duct
    • Persistence, persistent(congenital)
      • thyrolingual duct
    • Remnant
      • thyroglossal duct
    • Retrosternal thyroid(congenital)
    • Substernal thyroid
      • congenital
    • Thyroglossal
      • cyst
    • Thyroglossal
      • duct, persistent
    • Thyroid(gland) (body)
      • lingual
    • Thyrolingual duct, persistent

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Lingual Thyroid

    a condition characterized by the presence of rudimentary thyroid tissue at the base of the tongue. it is due to failed embryonic development and migration of thyroid tissue to its normal location. the lingual thyroid usually cannot maintain adequate hormone production thereby resulting in hypothyroidism.

  • Cone Dystrophy

    a general term which describes a group of rare eye disorders that affect the cone cells of the retina. cone dystrophy can cause a variety of symptoms including decreased visual clarity or acuity when looking straight ahead (central vision), a reduced ability to see colors, and an increased sensitivity to light (photophobia).

  • Lingual Goiter

    pathological enlargement of the lingual thyroid, ectopic thyroid tissue at the base of the tongue. it may cause upper airway obstruction; dysphagia; or hypothyroidism symptoms.

  • Congenital Hypothyroidism with Ectopic Thyroid

    thyroid hormone deficiency present at birth that is associated with ectopic thyroid tissue located in the neck region.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.2 Endocrine anomaly NEC
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.2Overview

Is Q89.2 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformations of other endocrine glands on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.2 group to?

When congenital malformations of other endocrine glands is the principal diagnosis on an inpatient stay, it groups to MS-DRG 643, 644, 645, with relative weights from 0.7683 to 1.6461 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformations of other endocrine glands on inpatient claims.

What is the ICD-9 equivalent of Q89.2?

Under the General Equivalence Mappings, congenital malformations of other endocrine glands converts to ICD-9-CM 759.2 (endocrine anomaly NEC). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.