2026 ICD-10-CM Diagnosis Code Q79.63Vascular Ehlers-Danlos syndrome

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q79

ICD-10-CM Q79.63
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q79.63 is a billable ICD-10-CM diagnosis code for vascular Ehlers-Danlos syndrome. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. Coders also document this condition as periodontitis due to Ehlers-Danlos syndrome type 4. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q79.63
Billable Status
Yes — Valid for Submission
Code Describes
Vascular Ehlers-Danlos syndrome
Short Description
Vascular Ehlers-Danlos syndrome
Same as the full description in the CMS dataset.
Parent Code
Q79.6
Ehlers-Danlos syndromes

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ79Congenital malformations of musculoskeletal system, not elsewhere classified
This CodeQ79.63Vascular Ehlers-Danlos syndrome

Present on Admission (POA)Billing

Q79.63 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Periodontitis due to Ehlers-Danlos syndrome type 4
  • Vascular Ehlers-Danlos syndrome
  • Vascular Ehlers-Danlos, polymicrogyria syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Vascular EDS (vEDS)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • Ehlers-Danlos
        • vascular (vascular EDS) (vEDS)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Ehlers-Danlos Syndrome

Ehlers-Danlos syndrome (EDS) is a group of inherited disorders that weaken connective tissues. Connective tissues are proteins that support skin, bones, blood vessels, and other organs.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement Q79.63 replaces the following previously assigned code(s):

  • Q79.6 - Ehlers-Danlos syndrome
  • Q79.6 - Ehlers-Danlos syndromes
FY 2020AddedAdded to the ICD-10-CM code setEffective October 1, 2019.
FY 2021–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q79.63Overview

Is Q79.63 (Ehlers-Danlos syndromes) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report vascular Ehlers-Danlos syndrome on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q79.63 group to?

When vascular Ehlers-Danlos syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q79.63 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for vascular Ehlers-Danlos syndrome on inpatient claims.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.