ICD-10-CM Code Q82.8

Other specified congenital malformations of skin

Version 2020 Billable Code POA Exempt

Valid for Submission

Q82.8 is a billable code used to specify a medical diagnosis of other specified congenital malformations of skin. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q82.8 might also be used to specify conditions or terms like abnormal dermatoglyphic pattern, abnormal palmar creases, abnormal plantar creases, absence of fingerprints with congenital milia syndrome, acquired perforating pseudoxanthoma elasticum, acquired pseudoxanthoma elasticum, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Other specified congenital malformations of skin
Long Description:Other specified congenital malformations of skin

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q82.8:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Abnormal palmar creases
  • Accessory skin tags
  • Benign familial pemphigus Hailey-Hailey
  • Congenital poikiloderma
  • Cutis laxa (hyperelastica)
  • Dermatoglyphic anomalies
  • Inherited keratosis palmaris et plantaris
  • Keratosis follicularis Darier-White

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Ehlers-Danlos syndrome Q79.6

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q82.8 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abnormal dermatoglyphic pattern
  • Abnormal palmar creases
  • Abnormal plantar creases
  • Absence of fingerprints with congenital milia syndrome
  • Acquired perforating pseudoxanthoma elasticum
  • Acquired pseudoxanthoma elasticum
  • Acral Darier's disease
  • Acral peeling skin syndrome
  • Acrocyanosis
  • Acroerythrokeratoderma
  • Acrokerato-elastoidosis
  • Acrokeratosis
  • Acrokeratosis verruciformis of Darier disease
  • Acrokeratosis verruciformis of Hopf
  • Acromegaloid phenotype with cutis verticis gyrata and corneal leukoma
  • Acroosteolysis
  • Alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy and respiratory tract infections
  • Alveolar bone loss
  • Ambiguous genitalia
  • Angiomatosis
  • Aplasia cutis congenita secondary to malformation syndrome
  • Arrhythmogenic right ventricular cardiomyopathy
  • Atrophoderma vermiculatum
  • Autosomal dominant diffuse palmoplantar keratoderma Norrbotten type
  • Autosomal dominant dyskeratosis congenita
  • Autosomal dominant mutilating keratoderma
  • Autosomal dominant palmoplantar keratoderma and congenital alopecia
  • Autosomal dominant pseudoxanthoma elasticum
  • Autosomal recessive cutis laxa type 2B
  • Autosomal recessive dyskeratosis congenita
  • Autosomal recessive hypohidrotic ectodermal dysplasia syndrome
  • Autosomal recessive palmoplantar keratoderma and congenital alopecia syndrome
  • Autosomal recessive pseudoxanthoma elasticum
  • Benign acanthosis nigricans
  • Bloom syndrome
  • Brugsch's syndrome
  • CAMOS syndrome
  • CEDNIK syndrome
  • Central cleft lip
  • Chronic hemolytic anemia
  • Circumscribed palmoplantar keratoderma
  • Cole disease
  • Congenital absence of skin on scalp
  • Congenital absence of skin on scalp with epidermal nevi
  • Congenital accessory skin tag
  • Congenital anomaly of oral mucosa
  • Congenital anomaly of oral mucosa
  • Congenital atrophy of optic nerve
  • Congenital clinodactyly
  • Congenital corneal opacity
  • Congenital cutaneous angiomatosis
  • Congenital deficiency of pigment of skin
  • Congenital dermal sinus
  • Congenital ectodermal defect
  • Congenital erosive and vesicular dermatosis
  • Congenital hypotrichia
  • Congenital hypotrichia
  • Congenital keratoderma
  • Congenital keratoderma
  • Congenital lethal erythroderma
  • Congenital leukonychia
  • Congenital livedo reticularis
  • Congenital melanosis
  • Congenital oculocutaneous hypopigmentation
  • Congenital palmoplantar and perioral keratoderma of Olmsted
  • Congenital pigmentary skin anomalies
  • Congenital pigmented melanocytic nevus of skin
  • Congenital pigmented melanocytic nevus of skin
  • Congenital retrognathism
  • Congenital scar
  • Congenital skin contracture
  • Congenital woolly hair
  • Congenital woolly hair
  • Congenital woolly hair
  • Congenital woolly hair
  • Congenital/genetic syndrome with poikiloderma
  • Congenital/hereditary hypermelanotic disorder
  • Connective tissue nevus of skin
  • Corneal intraepithelial dyskeratosis, palmoplantar hyperkeratosis, laryngeal dyskeratosis syndrome
  • Corneal leukoma
  • Craniofaciofrontodigital syndrome
  • Craniosynostosis, anal anomaly, porokeratosis syndrome
  • Curly hair, acral keratoderma, caries syndrome
  • Cutaneous lesion resulting from spina bifida
  • Cutis gyrata syndrome of Beare and Stevenson
  • Cutis laxa
  • Cutis laxa secondary to inherited disorder of connective tissue
  • Cutis laxa with osteodystrophy
  • Cutis laxa, autosomal dominant
  • Cutis laxa, autosomal recessive
  • Cutis laxa, autosomal recessive
  • Cutis laxa, recessive, type I
  • Cutis laxa, recessive, type II
  • Cutis verticis gyrata
  • Cutis verticis gyrata
  • Cyanosis of skin and/or skin-associated mucous membrane
  • Darier disease
  • Deaf blind hypopigmentation syndrome Yemenite type
  • Dermatoglyphs - skin lines
  • Dermatoleukodystrophy
  • Dermatopathia pigmentosa reticularis
  • Dermodental dysplasia
  • Diffuse dermatitis
  • Diffuse palmoplantar keratoderma and acrocyanosis syndrome
  • Diffuse palmoplantar keratoderma of Thost-Unna
  • Diffuse palmoplantar keratoderma with painful fissures
  • Disseminated superficial porokeratosis
  • Dwarfism, alopecia, pseudoanodontia, cutis laxa
  • Dyschromatosis universalis
  • Dyskeratosis congenita
  • Dysplasia of larynx
  • Ectodermal dysplasia with hair-nail defect
  • Ectodermal dysplasia with hair-nail defect
  • Ectodermal dysplasia with sweating defect
  • Ectodermal dysplasia with tooth-nail defects
  • Ectodermal dysplasia with tooth-sweating defect
  • Eosinophilic pustular folliculitis
  • Epidermolytic palmoplantar keratoderma of Vorner
  • Erythrokeratoderma
  • Erythrokeratoderma progressiva of Gottron
  • Erythrokeratodermia variabilis
  • Exostosis, anetoderma, brachydactyly type E syndrome
  • Extensive congenital erosions, vesicles and reticulate scarring
  • Facial dysmorphism, cleft palate, loose skin syndrome
  • Familial benign pemphigus
  • Familial focal facial dermal dysplasia
  • Familial generalized lentiginosis
  • Familial multiple fibrofolliculoma
  • Familial progressive hyper and hypopigmentation
  • Fibrofolliculoma
  • Finding of palmar crease
  • Flexural Darier's disease
  • Flynn-Aird syndrome
  • Focal dermal hypoplasia
  • Focal palmoplantar and gingival keratoderma
  • Focal palmoplantar keratoderma with joint keratoses
  • Follicular hyperkeratosis
  • Frontonasal dysplasia sequence
  • Genetic defect of hair shaft
  • Genetic syndrome with hypermelanosis
  • Genodermatosis
  • Giant porokeratosis
  • Goltz syndrome
  • Hairy malformation of palms and soles
  • Hemolytic anemia with emphysema AND cutis laxa
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acroosteolysis
  • Hereditary benign acanthosis nigricans
  • Hereditary benign acanthosis nigricans with insulin resistance
  • Hereditary benign intraepithelial dyskeratosis
  • Hereditary clubbing
  • Hereditary congenital hypomelanotic and hypermelanotic cutaneous macules, growth retardation, intellectual disability syndrome
  • Hereditary diffuse palmoplantar keratoderma
  • Hereditary erythrokeratolysis
  • Hereditary follicular keratoses
  • Hereditary hypermelanosis
  • Hereditary palmoplantar keratoderma
  • Hereditary palmoplantar keratoderma Gamborg Nielsen type
  • Hereditary sclerosing poikiloderma
  • Hereditary sclerosing poikiloderma of Weary
  • Hidrotic ectodermal dysplasia Christianson Fourie type
  • Hidrotic ectodermal dysplasia Halal type
  • Hidrotic ectodermal dysplasia syndrome
  • Howel-Evans' syndrome
  • Hoyeraal-Hreidarsson syndrome
  • Hyperplasia of gingiva
  • Hypertrophic Darier's disease
  • Hypohidrosis, enamel hypoplasia, palmoplantar keratoderma, intellectual disability syndrome
  • Hypoplasia of thumb
  • Hypotrichosis with keratosis pilaris and lentiginosis
  • Hypotrichosis, osteolysis, periodontitis, palmoplantar keratoderma syndrome
  • Inherited cutaneous hyperpigmentation
  • Inherited cutis laxa
  • Inherited disorder of keratinization
  • Inherited pseudoxanthoma elasticum
  • Insulin receptor defect
  • Isolated congenital adermatoglyphia
  • Juvenile elastoma
  • Keratoderma
  • Keratoderma areata
  • Keratoderma hereditarium mutilans with ichthyosis syndrome
  • Keratoderma plantare sulcata
  • Keratoderma with pachyonychia congenita
  • Keratoderma with scleroatrophy of the extremities
  • Keratolysis exfoliativa
  • Keratolytic winter erythema
  • Keratosis follicularis, dwarfism, cerebral atrophy syndrome
  • Keratosis linearis, ichthyosis congenita, sclerosing keratoderma syndrome
  • Keratosis pilaris
  • Keratosis pilaris atrophicans
  • Keratosis pilaris decalvans
  • Keratosis pilaris with ichthyosis and deafness
  • Keratosis rubra pilaris
  • Kindler's syndrome
  • Kohlschutter's syndrome
  • Leukonychia totalis
  • Leukonychia totalis, acanthosis-nigricans-like lesions, abnormal hair syndrome
  • Lichen spinulosus
  • Linear porokeratosis
  • Linear/nevoid/zosteriform Darier's disease
  • Lipomatous hamartoma
  • Livedo reticularis
  • Localized congenital cutis laxa
  • Lumpy scalp syndrome
  • Macrocephaly-capillary malformation
  • MACS syndrome
  • Malignant melanoma arising in congenital nevus
  • MEDNIK syndrome
  • Melanin pigmentation of oral mucosa
  • Melanosis of mucosa of body orifice
  • Michelin-tire baby
  • Microphthalmia with linear skin defect syndrome
  • Milia
  • Multiple benign annular creases of extremities
  • Multiple lentigines syndrome
  • Multiple malformation syndrome with senile-like appearance
  • Multiple malformation syndrome, small stature, without skeletal dysplasia
  • Mutilating keratoderma
  • Mutilating keratoderma
  • Naegeli-Franceschetti-Jadassohn syndrome
  • Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
  • Nail dystrophy associated with bullous dermatoses
  • Nail dystrophy due to benign familial pemphigus
  • Nail dystrophy due to Darier's disease
  • Naxos disease
  • Neonatal cutis laxa with marfanoid phenotype
  • Neonatal eosinophilic pustular folliculitis
  • Neonatal skin infection
  • Neurocutaneous melanosis sequence
  • Neuroectodermal melanolysosomal disease
  • Nevus elasticus
  • Oculo-cerebro-cutaneous syndrome
  • Osteoporosis and oculocutaneous hypopigmentation syndrome
  • Pai syndrome
  • Palmar pitting due to Darier's disease
  • Palmoplantar hyperkeratosis-hyperpigmentation syndrome of Cantu
  • Palmoplantar keratoderma
  • Palmoplantar keratoderma Nagashima type
  • Palmoplantar keratoderma transgrediens
  • Palmoplantar keratoderma with clinodactyly syndrome
  • Palmoplantar keratoderma with deafness syndrome
  • Palmoplantar keratoderma, 46,XX sex reversal, predisposition to squamous cell carcinoma syndrome
  • Papillon-Lefèvre syndrome
  • Papular epidermal nevi with skyline basal cell layers syndrome
  • Papuloverrucous palmoplantar keratoderma of Jakac-Wolf
  • Peripheral cyanosis
  • Poikiloderma, alopecia, retrognathism, cleft palate syndrome
  • Porokeratosis
  • Porokeratosis of Mibelli
  • Porokeratosis of Mibelli, linear unilateral type
  • Porokeratosis of Mibelli, plaque type
  • Porokeratosis of Mibelli, superficial disseminated type
  • Porokeratosis plantaris palmaris et disseminata
  • Preauricular dimple
  • Primary essential cutis verticis gyrata
  • Primary non-essential cutis verticis gyrata
  • Progressive palmoplantar keratoderma of Greither
  • Pseudoxanthoma elasticum
  • Punctate palmoplantar keratoderma
  • Punctate palmoplantar keratoderma
  • Punctate palmoplantar keratoderma type 1
  • Reticulate pigmented anomaly of flexures
  • Rothmund-Thomson syndrome
  • SCARF syndrome
  • Severe dermatitis, multiple allergies, metabolic wasting syndrome
  • Single transverse palmar crease
  • Skin fragility, wooly hair, palmoplantar keratoderma syndrome
  • Skin peeling disorder
  • Spastic paraplegia, intellectual disability, palmoplantar hyperkeratosis syndrome
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Striate palmoplantar keratoderma
  • Symmetrical dyschromatosis of extremities
  • Terminal osseous dysplasia and pigmentary defect syndrome
  • Thumb deformity, alopecia, pigmentation anomaly syndrome
  • Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
  • Trichodental syndrome
  • Trichothiodystrophy
  • Vascular neurocutaneous syndrome
  • Wooly hair
  • Wooly hair
  • Wooly hair
  • Wooly hair
  • Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome
  • Wooly hair with palmoplantar keratoderma syndrome
  • Wrinkly skin syndrome
  • X-linked dyskeratosis congenita
  • Zosteriform lentiginosis
  • Zosteriform reticulate hyperpigmentation

Diagnostic Related Groups

The ICD-10 code Q82.8 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q82.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q82.8 to ICD-9

  • 757.2 - Dermatoglyphic anomalies (Approximate Flag)
  • 757.39 - Skin anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations of skin (Q82)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Skin Conditions

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

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