2027 ICD-10-CM Diagnosis Code Q80Congenital ichthyosis

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q80

ICD-10-CM Q80
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q80 is a non-billable ICD-10-CM category code for congenital ichthyosis, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q80.0, Q80.1, Q80.2, and Q80.3.

Code Identity

ICD-10-CM Code
Q80
Billable Status
No — Non-Billable Category
Code Describes
Congenital ichthyosis
Short Description
Congenital ichthyosis
Same as the full description in the CMS dataset.
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ80Congenital ichthyosis
This CodeQ80Congenital ichthyosis

Specific Coding for Congenital ichthyosisOverview

Non-specific codes like Q80 require more characters. Use one of these billable codes instead:

  • Use Q80.0 for Ichthyosis vulgaris

  • Use Q80.1 for X-linked ichthyosis

  • Use Q80.2 for Lamellar ichthyosis

  • Use Q80.3 for Congenital bullous ichthyosiform erythroderma

  • Use Q80.4 for Harlequin fetus

  • Use Q80.8 for Other congenital ichthyosis

  • Use Q80.9 for Congenital ichthyosis, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q80: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q80, its category, or a range that includes it.

Excludes1 2

These codes carry an Excludes1 note naming Q80: they are not reported together with it, unless the two conditions are unrelated.

  • L85.0 Acquired ichthyosis
    congenital ichthyosis (Q80.-)
  • P83 Other conditions of integument specific to newborn
    congenital malformations of skin and integument (Q80-Q84)

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Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q80Overview

What is the ICD-10 code for congenital ichthyosis?

Q80 is the ICD-10-CM category for congenital ichthyosis, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q80 (Congenital ichthyosis) a billable code?

No. This is a category header that groups the codes for congenital ichthyosis, and headers cannot be submitted on claims. Claims for congenital ichthyosis need a more specific code from this category, such as Q80.0, Q80.1, and Q80.2.

Can Q80 be reported with G60.1?

Not as a rule. The Excludes1 note on Q80 lists "Refsum's disease (G60.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).