2027 ICD-10-CM Diagnosis Code Q63.8Other specified congenital malformations of kidney

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q63

ICD-10-CM Q63.8
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q63.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of kidney. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q63.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of kidney
Short Description
Other specified congenital malformations of kidney
Same as the full description in the CMS dataset.
Parent Code
Other congenital malformations of kidney

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ63Other congenital malformations of kidney
This CodeQ63.8Other specified congenital malformations of kidney

Present on Admission (POA)Billing

Q63.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the urinary system (Q60-Q64).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Accessory kidney
  • Acrorenal field defect, ectodermal dysplasia, and lipoatrophic diabetes
  • Bilateral congenital primary hydronephrosis
  • Bilateral hydronephrosis
  • Congenital abnormal shape of kidney
  • Congenital asymmetry of kidneys
  • Congenital calculus of kidney
  • Congenital calyceal diverticulum
  • Congenital dilatation of renal pelvis
  • Congenital hydrocalicosis
  • Congenital hydronephrosis
  • Congenital megacalycosis
  • Congenital megacalycosis of bilateral kidneys
  • Congenital membranous nephropathy due to maternal anti-neutral endopeptidase alloimmunization
  • Diffuse hyperplastic perilobular nephroblastomatosis
  • Dilatation of calyx
  • Dilatation of renal pelvis
  • Diverticulum of renal calyx
  • Inequality in size of kidneys
  • Infundibulopelvic stenosis multicystic kidney syndrome
  • Megacalycosis
  • Nodular renal blastema
  • PELVIS syndrome
  • Prominent renal pelvis
  • Renal caliceal diverticuli and deafness syndrome
  • Trifid kidney
  • Trifid pelvis of kidney
  • Triple kidney with triple pelvis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q63.8: its own notes plus those printed at Q63 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital renal calculi

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q63 Other congenital malformations of kidney applies to 6 codes
  • congenital nephrotic syndrome (N04.-)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q63.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.3 Kidney anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q63.8Overview

What is the ICD-10 code for other specified congenital malformations of kidney?

The ICD-10-CM code for other specified congenital malformations of kidney is Q63.8 (sometimes written as Q638). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q63.8 (Other congenital malformations of kidney) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of kidney on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q63.8 group to?

When other specified congenital malformations of kidney is the principal diagnosis on an inpatient stay, it groups to MS-DRG 699, 698, 700, with relative weights from 0.6740 to 1.6400 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q63.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of kidney on inpatient claims. The code appears in the Congenital malformations of the urinary system (Q60-Q64) range of the CMS exempt list.

Can Q63.8 be reported with a code from N04?

Not as a rule. The Excludes1 note at Q63, which applies to Q63.8, lists "congenital nephrotic syndrome (N04.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).