Other congenital malformations of kidney (Q63) ICD-10-CM
The Q63 code range covers other congenital malformations of kidney with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- congenital nephrotic syndrome N04
Codes in the Q63 Range 7 codes · 6 billable
About the Q63 Code Range
The ICD-10 code section Q63 covers a variety of rare congenital kidney malformations that differ from the common anomalies usually coded elsewhere. These codes identify specific structural kidney abnormalities present from birth that can affect kidney function or anatomy.
This section includes subcodes such as Q63.0 for accessory or duplex kidneys, also known as double kidney or duplicated collecting system; Q63.1 for fused or lobulated kidneys, including horseshoe kidney (a common fusion anomaly); and Q63.2 for ectopic kidneys, which may be abnormally positioned like pelvic or thoracic kidneys. Other codes cover hyperplastic or enlarged kidneys (Q63.3), various other specified congenital malformations (Q63.8), and unspecified congenital kidney malformations (Q63.9). Using these codes helps medical professionals precisely classify rare kidney conditions such as congenital hydronephrosis, megacalycosis, or complex syndromes involving multiple organ systems, facilitating accurate diagnosis, treatment planning, and health record documentation. This set of codes is essential for clinicians coding congenital kidney anomalies beyond common diagnoses, offering clarity when terms like duplex kidney, horseshoe kidney, or ectopic kidney are encountered in medical documentation.
Questions About This Page
How many billable codes are in the Q63 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q63 range classify?
The range classifies other congenital malformations of kidney. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
