Other congenital malformations of kidney (Q63)

The ICD-10 code section Q63 covers a variety of rare congenital kidney malformations that differ from the common anomalies usually coded elsewhere. These codes identify specific structural kidney abnormalities present from birth that can affect kidney function or anatomy.

This section includes subcodes such as Q63.0 for accessory or duplex kidneys, also known as double kidney or duplicated collecting system; Q63.1 for fused or lobulated kidneys, including horseshoe kidney (a common fusion anomaly); and Q63.2 for ectopic kidneys, which may be abnormally positioned like pelvic or thoracic kidneys. Other codes cover hyperplastic or enlarged kidneys (Q63.3), various other specified congenital malformations (Q63.8), and unspecified congenital kidney malformations (Q63.9). Using these codes helps medical professionals precisely classify rare kidney conditions such as congenital hydronephrosis, megacalycosis, or complex syndromes involving multiple organ systems, facilitating accurate diagnosis, treatment planning, and health record documentation. This set of codes is essential for clinicians coding congenital kidney anomalies beyond common diagnoses, offering clarity when terms like duplex kidney, horseshoe kidney, or ectopic kidney are encountered in medical documentation.