Other congenital malformations of urinary system (Q64)
ICD-10 code Q64 covers a range of congenital malformations affecting the urinary system, including the bladder, urethra, and related structures. These codes specifically identify various birth defects such as epispadias, bladder exstrophy, urethral strictures, and other rare structural malformations.
This section helps medical coders and healthcare professionals precisely document conditions like epispadias (Q64.0), also known as exstrophy epispadias complex in males and females, or exstrophy of the urinary bladder (Q64.1), including its subtypes such as cloacal exstrophy (Q64.12). It also includes congenital narrowings or blockages such as posterior urethral valves (Q64.2) and congenital bladder neck obstruction (Q64.31). Codes like Q64.4 cover malformations of the urachus, while Q64.5 tracks rare cases of congenital absence of bladder and urethra. More complex conditions, such as double urethra (Q64.74) or congenital urethrorectal fistula (Q64.73), are captured here as well. This detailed classification permits accurate identification and coding of diverse urinary tract congenital anomalies for appropriate clinical documentation and billing. Understanding synonyms like exstrophy of urinary bladder sequence or urethroperineal fistula facilitates correct code selection when encountering various terminologies in clinical records.
Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Congenital malformations of the urinary system (Q60-Q64)
Q64 Other congenital malformations of urinary system
- Q64.0 Epispadias
Q64.1 Exstrophy of urinary bladder
- Q64.10 Exstrophy of urinary bladder, unspecified
- Q64.11 Supravesical fissure of urinary bladder
- Q64.12 Cloacal exstrophy of urinary bladder
- Q64.19 Other exstrophy of urinary bladder
- Q64.2 Congenital posterior urethral valves
Q64.3 Other atresia and stenosis of urethra and bladder neck
- Q64.31 Congenital bladder neck obstruction
- Q64.32 Congenital stricture of urethra
- Q64.33 Congenital stricture of urinary meatus
- Q64.39 Other atresia and stenosis of urethra and bladder neck
- Q64.4 Malformation of urachus
- Q64.5 Congenital absence of bladder and urethra
- Q64.6 Congenital diverticulum of bladder
Q64.7 Other and unspecified congenital malformations of bladder and urethra
- Q64.70 Unspecified congenital malformation of bladder and urethra
- Q64.71 Congenital prolapse of urethra
- Q64.72 Congenital prolapse of urinary meatus
- Q64.73 Congenital urethrorectal fistula
- Q64.74 Double urethra
- Q64.75 Double urinary meatus
- Q64.79 Other congenital malformations of bladder and urethra
- Q64.8 Other specified congenital malformations of urinary system
- Q64.9 Congenital malformation of urinary system, unspecified
Other congenital malformations of urinary system (Q64)
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Epispadias
A birth defect due to malformation of the URETHRA in which the urethral opening is above its normal location. In the male, the malformed urethra generally opens on the top or the side of the PENIS, but the urethra can also be open the entire length of the penis. In the female, the malformed urethral opening is often between the CLITORIS and the labia, or in the ABDOMEN.
