Cystic kidney disease (Q61) ICD-10-CM
The Q61 code range covers cystic kidney disease with 14 ICD-10-CM diagnosis codes. 11 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q61 Range 14 codes · 11 billable
- Q61 Cystic kidney diseaseNon-billable
- Q61.0 Congenital renal cystNon-billable
- Q61.00 Congenital renal cyst, unspecified
- Q61.01 Congenital single renal cyst
- Q61.02 Congenital multiple renal cysts
- Q61.1 Polycystic kidney, infantile typeNon-billable
- Q61.11 Cystic dilatation of collecting ducts
- Q61.19 Other polycystic kidney, infantile type
- Q61.2 Polycystic kidney, adult type
- Q61.3 Polycystic kidney, unspecified
- Q61.4 Renal dysplasia
- Q61.5 Medullary cystic kidney
- Q61.8 Other cystic kidney diseases
- Q61.9 Cystic kidney disease, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q61 range.
Hydranencephaly
A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
Medullary Sponge Kidney
A non-hereditary KIDNEY disorder characterized by the abnormally dilated (ECTASIA) medullary and inner papillary portions of the collecting ducts. These collecting ducts usually contain CYSTS or DIVERTICULA filled with jelly-like material or small calculi (KIDNEY STONES) leading to infections or obstruction. It should be distinguished from congenital or hereditary POLYCYSTIC KIDNEY DISEASES.
About the Q61 Code Range
ICD-10 code Q61 and its subcodes are specifically used to identify various forms of cystic kidney diseases, including congenital kidney cysts and polycystic kidney disease types affecting infants and adults. These codes facilitate precise differentiation among kidney cyst conditions for accurate diagnosis and treatment documentation.
The ICD-10 code Q61.0 series covers congenital renal cysts, with specific distinctions such as Q61.01 for a congenital single renal cyst and Q61.02 for multiple cysts. Synonyms like "solitary multilocular renal cyst" help clarify these codes when encountering alternate terminology. Codes such as Q61.1 and its subcategories address infantile polycystic kidney disease, including "cystic dilatation of collecting ducts." The adult form is coded under Q61.2, also known as "autosomal dominant polycystic kidney disease," a common genetic disorder. Additional codes like Q61.4 represent renal dysplasia, often linked with syndromes and conditions involving multiple cysts. Other categories, including Q61.5, capture medullary cystic kidney disease, which has various synonyms like "nephronophthisis" and "medullary sponge kidney." These distinctions enable precise classification of cystic kidney conditions for both clinical and billing purposes using the ICD-10 system.
Questions About This Page
How many billable codes are in the Q61 range?
Of the 14 codes in this range, 11 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q61 range classify?
The range classifies cystic kidney disease. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
