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  2. ICD-10-CM Codes List
  3. Q00-Q99
  4. Q60-Q64
  5. Cystic kidney disease (Q61)

Cystic kidney disease (Q61)

ICD-10 code Q61 and its subcodes are specifically used to identify various forms of cystic kidney diseases, including congenital kidney cysts and polycystic kidney disease types affecting infants and adults. These codes facilitate precise differentiation among kidney cyst conditions for accurate diagnosis and treatment documentation.

The ICD-10 code Q61.0 series covers congenital renal cysts, with specific distinctions such as Q61.01 for a congenital single renal cyst and Q61.02 for multiple cysts. Synonyms like "solitary multilocular renal cyst" help clarify these codes when encountering alternate terminology. Codes such as Q61.1 and its subcategories address infantile polycystic kidney disease, including "cystic dilatation of collecting ducts." The adult form is coded under Q61.2, also known as "autosomal dominant polycystic kidney disease," a common genetic disorder. Additional codes like Q61.4 represent renal dysplasia, often linked with syndromes and conditions involving multiple cysts. Other categories, including Q61.5, capture medullary cystic kidney disease, which has various synonyms like "nephronophthisis" and "medullary sponge kidney." These distinctions enable precise classification of cystic kidney conditions for both clinical and billing purposes using the ICD-10 system.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • acquired cyst of kidney N28.1
  • Potter's syndrome Q60.6

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Hydranencephaly

A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)

Medullary Sponge Kidney

A non-hereditary KIDNEY disorder characterized by the abnormally dilated (ECTASIA) medullary and inner papillary portions of the collecting ducts. These collecting ducts usually contain CYSTS or DIVERTICULA filled with jelly-like material or small calculi (KIDNEY STONES) leading to infections or obstruction. It should be distinguished from congenital or hereditary POLYCYSTIC KIDNEY DISEASES.