2026 ICD-10-CM Diagnosis Code Q44.70Other congenital malformation of liver, unspecified

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q44

ICD-10-CM Q44.70
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q44.70 is a billable ICD-10-CM diagnosis code for other congenital malformation of liver, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 441 through 443. The code is exempt from POA reporting. Coders also document this condition as cone dystrophy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q44.70
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformation of liver, unspecified
Short Description
Other congenital malformation of liver, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q44.7
Other congenital malformations of liver

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ44Congenital malformations of gallbladder, bile ducts and liver
This CodeQ44.70Other congenital malformation of liver, unspecified

Present on Admission (POA)Billing

Q44.70 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cone dystrophy
  • Congenital abnormality of liver and/or biliary tract
  • Congenital anomaly of liver
  • Mitochondrial DNA depletion syndrome hepatocerebrorenal form
  • Mitochondrial DNA depletion syndrome, hepatocerebral form due to DGUOK deficiency
  • Navajo neurohepatopathy
  • Retinohepatoendocrinologic syndrome
  • Trichohepatoenteric syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital malformation of liver, NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • liver
    • Deformity
      • liver (congenital)
    • Malformation(congenital)
      • liver

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cone Dystrophy

    a general term which describes a group of rare eye disorders that affect the cone cells of the retina. cone dystrophy can cause a variety of symptoms including decreased visual clarity or acuity when looking straight ahead (central vision), a reduced ability to see colors, and an increased sensitivity to light (photophobia).

Code History & ChangesHistory

Replacement Q44.70 replaces the following previously assigned code(s):

  • Q44.7 - Other congenital malformations of liver
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q44.70Overview

Is Q44.70 (Other congenital malformations of liver) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformation of liver, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q44.70 group to?

When other congenital malformation of liver, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 441, 442, 443, with relative weights from 0.6997 to 1.7947 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q44.70 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformation of liver, unspecified on inpatient claims.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.