2027 ICD-10-CM Diagnosis Code Q44.70Other congenital malformation of liver, unspecified

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q44

ICD-10-CM Q44.70
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q44.70 is a billable ICD-10-CM diagnosis code for other congenital malformation of liver, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 441 through 443. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 10 closely related codes. The code is exempt from POA reporting. Coders also document this condition as cone dystrophy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q44.70
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformation of liver, unspecified
Short Description
Other congenital malformation of liver, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q44.7
Other congenital malformations of liver

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ44Congenital malformations of gallbladder, bile ducts and liver
This CodeQ44.70Other congenital malformation of liver, unspecified

Present on Admission (POA)Billing

Q44.70 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations of the digestive system (Q38-Q45).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cone dystrophy
  • Congenital abnormality of liver and/or biliary tract
  • Congenital anomaly of liver
  • Mitochondrial DNA depletion syndrome hepatocerebrorenal form
  • Mitochondrial DNA depletion syndrome, hepatocerebral form due to DGUOK deficiency
  • Navajo neurohepatopathy
  • Retinohepatoendocrinologic syndrome
  • Trichohepatoenteric syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q44.70: its own notes plus those printed at Q44.7 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital malformation of liver, NOS

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

From Q44.7 Other congenital malformations of liver applies to 3 codes
  • if applicable, associated malformations affecting other systems

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Liver Diseases

Your liver is the largest organ inside your body. It helps your body digest food, store energy, and remove poisons.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement Q44.70 replaces the following previously assigned code(s):

  • Q44.7 - Other congenital malformations of liver
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q44.70Overview

What is the ICD-10 code for other congenital malformation of liver, unspecified?

The ICD-10-CM code for other congenital malformation of liver, unspecified is Q44.70 (sometimes written as Q4470). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q44.70 (Other congenital malformations of liver) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformation of liver, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q44.70 group to?

When other congenital malformation of liver, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 442, 441, 443, with relative weights from 0.6890 to 1.8226 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q44.70 a CC or MCC?

CMS lists Q44.70 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 10 closely related codes in its exclusion list.

Is Q44.70 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformation of liver, unspecified on inpatient claims. The code appears in the Other congenital malformations of the digestive system (Q38-Q45) range of the CMS exempt list.