2027 ICD-10-CM Diagnosis Code Q43.9Congenital malformation of intestine, unspecified

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q43

ICD-10-CM Q43.9
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q43.9 is a billable ICD-10-CM diagnosis code for congenital malformation of intestine, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 393 through 395. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 21 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q43.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of intestine, unspecified
Short Description
Congenital malformation of intestine, unspecified
Same as the full description in the CMS dataset.
Parent Code
Other congenital malformations of intestine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ43Other congenital malformations of intestine
This CodeQ43.9Congenital malformation of intestine, unspecified

Present on Admission (POA)Billing

Q43.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations of the digestive system (Q38-Q45).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Absent radius, anogenital anomalies syndrome
  • Anal atresia
  • Anorectal anomaly
  • Anorectal fistula
  • Aplasia of bone of radius and/or ulna
  • Aplasia of radius
  • Atrioventricular septal defect, blepharophimosis, radial and anal defect syndrome
  • Congenital absence of radius
  • Congenital anomaly of anus
  • Congenital anomaly of duodenum
  • Congenital anomaly of intestinal tract
  • Congenital anomaly of large intestine
  • Congenital anomaly of rectum
  • Congenital anomaly of small intestine
  • Congenital anorectal fistula due to high anorectal malformation
  • Congenital anorectal fistula due to intermediate anorectal malformation
  • Congenital anorectal fistula due to low anorectal malformation
  • Congenital fistula of anus
  • Congenital fistula of rectum
  • Congenital fistula of rectum and anus
  • Congenital nephritis
  • Congenital non-syndromic anorectal malformation
  • Craniosynostosis, anal anomaly, porokeratosis syndrome
  • Lowe Kohn Cohen syndrome
  • Manitoba oculotrichoanal syndrome
  • Primary desmosis coli
  • Severe intellectual disability, epilepsy, anal anomaly, distal phalangeal hypoplasia syndrome
  • STAR syndrome
  • Telecanthus
  • Thymic, renal, anal, lung dysplasia syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q43.9: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q43.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.5 Intestinal anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q43.9Overview

What is the ICD-10 code for congenital malformation of intestine, unspecified?

The ICD-10-CM code for congenital malformation of intestine, unspecified is Q43.9 (sometimes written as Q439). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q43.9 (Other congenital malformations of intestine) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of intestine, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q43.9 group to?

When congenital malformation of intestine, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 394, 395, 393, with relative weights from 0.6379 to 1.5877 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q43.9 a CC or MCC?

CMS lists Q43.9 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 21 closely related codes in its exclusion list.

Is Q43.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of intestine, unspecified on inpatient claims. The code appears in the Other congenital malformations of the digestive system (Q38-Q45) range of the CMS exempt list.