2027 ICD-10-CM Diagnosis Code Q27.8Other specified congenital malformations of peripheral vascular system

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.8
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q27.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of peripheral vascular system. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of peripheral vascular system
Short Description
Oth congenital malformations of peripheral vascular system
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.8Other specified congenital malformations of peripheral vascular system

Present on Admission (POA)Billing

Q27.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aberrant origin of left subclavian artery
  • Aberrant retroesophageal brachiocephalic artery
  • Aberrant retro-esophageal subclavian artery causing dysphagia
  • Abnormal connection of hepatic vein to atrium
  • Absent venous duct
  • Agenesis of artery
  • Agenesis of internal carotid artery
  • Aneurysm osteoarthritis syndrome
  • Anomalous origin of left common carotid artery from brachiocephalic artery
  • Anomalous origin of right subclavian artery
  • Anomaly of umbilical vein group I
  • Anomaly of umbilical vein group II
  • Anomaly of umbilical vein group III
  • Anomaly of umbilical vein group IV
  • Aplasia of radial artery
  • Arterial embryological remnant
  • Atresia of systemic vein
  • Bilateral congenital anomaly of renal veins
  • Capillary malformation-arteriovenous malformation syndrome
  • CLAPO syndrome
  • Compression of esophagus
  • Compression of trachea
  • Congenital abnormality of hepatic vein
  • Congenital absence of artery
  • Congenital absence of azygos vein
  • Congenital absence of carotid artery
  • Congenital absence of innominate vein
  • Congenital absence of subclavian artery
  • Congenital absence of vein
  • Congenital aneurysm of systemic artery
  • Congenital anomaly of azygos vein
  • Congenital anomaly of blood vessel of lower limb
  • Congenital anomaly of blood vessel of spine
  • Congenital anomaly of blood vessel of upper limb
  • Congenital anomaly of left renal artery
  • Congenital anomaly of left renal vein
  • Congenital anomaly of renal blood vessel
  • Congenital anomaly of renal vein
  • Congenital anomaly of right renal artery
  • Congenital anomaly of right renal vein
  • Congenital arterial aneurysm
  • Congenital atresia of artery
  • Congenital atresia of vein
  • Congenital dilatation of carotid artery
  • Congenital dilatation of innominate artery
  • Congenital dilatation of subclavian artery
  • Congenital disruption of omphalomesenteric artery
  • Congenital elongation of innominate artery
  • Congenital intramuscular fast-flow vascular abnormality
  • Congenital malformation of left renal vein
  • Congenital malformation of renal vein
  • Congenital malformation of right renal vein
  • Congenital malposition of carotid artery
  • Congenital malposition of innominate artery
  • Congenital malposition of subclavian artery
  • Congenital occlusion of femoral vein
  • Congenital occlusion of iliac vein
  • Congenital peripheral aneurysm
  • Congenital phlebectasia
  • Congenital stenosis of carotid artery
  • Congenital stenosis of innominate artery
  • Congenital stenosis of subclavian artery
  • Congenital stricture of artery
  • Congenital stricture of retinal artery
  • Congenital transposition of azygos vein
  • Congenital varix
  • Congenital vascular anomaly of eye
  • Congenital vascular malformation due to inherited syndrome
  • Congenital vascular malformation of lip
  • Congenital vascular malformation of orbital region
  • Congenital venous malformation of spleen
  • Deep vein aplasia
  • Deep vein hypoplasia
  • Distal origin of brachiocephalic artery with tracheal compression
  • Distal origin of brachiocephalic trunk
  • Distended umbilical veins
  • Double artery
  • Ductus venosus abnormality
  • Dysphagia lusoria
  • Ectopic artery
  • EPHB4-related capillary malformation, arteriovenous malformation
  • Glomuvenous malformation
  • Hepatic vein to left atrium
  • Hepatic vein to left atrium and right atrium
  • Hepatic vein to right atrium
  • Hepatoportal microvascular dysplasia
  • Hypoplasia of artery
  • Isolation of brachiocephalic trunk
  • Isolation of branch of aortic arch
  • Isolation of common carotid artery
  • Isolation of left subclavian artery
  • Isolation of right common carotid artery
  • Isolation of right subclavian artery
  • Isolation of subclavian artery
  • Lethal arteriopathy syndrome due to fibulin-4 deficiency
  • Levoatrial cardinal vein
  • Mixed vascular malformation
  • Multiple dysplasia syndrome
  • Multiple venous malformation of skin and mucous membrane
  • NEVADA syndrome
  • Obstruction of femoral vein
  • Obstruction of iliac vein
  • Obstruction of peripheral vein
  • Occlusion of femoral vein
  • Occlusion of iliac vein
  • Peripheral congenital arteriovenous aneurysm
  • Peripheral venous malformation
  • Persistence of primitive artery
  • Persistent descending vein
  • Persistent embryonic proatlantal intersegmental artery
  • Persistent omphalomesenteric artery
  • Persistent vertical vein
  • RASA1-related capillary malformation, arteriovenous malformation
  • Retroaortic brachiocephalic vein
  • Retroesophageal subclavian artery
  • Separate hepatic venous and inferior caval venous connections to heart
  • Specific mixed vascular syndrome
  • Splenoportal vascular anomaly
  • Stenosis of brachiocephalic artery
  • Stenosis of retinal artery
  • Stricture of artery
  • Subclavian artery stenosis
  • Supernumerary azygos vein
  • Systemic to pulmonary collateral artery connecting with artery
  • Systemic to pulmonary collateral artery connecting with central pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with isolated intraparenchymal pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with tracheobronchial arteries
  • Systemic to pulmonary collateral artery contributing to dual lung supply
  • Systemic to pulmonary collateral artery from left brachiocephalic artery
  • Systemic to pulmonary collateral artery from left carotid artery
  • Systemic to pulmonary collateral artery from left renal artery
  • Systemic to pulmonary collateral artery from right brachiocephalic artery
  • Systemic to pulmonary collateral artery from right carotid artery
  • Systemic to pulmonary collateral artery from right renal artery
  • Systemic venovenous collateral vein
  • True congenital varicose veins
  • Umbilical vein varix
  • Vascular compression of esophagus by aberrant artery
  • Vascular compression of esophagus by aberrant right subclavian artery arising from descending aorta
  • Vascular ring with right aortic arch and left arterial duct from anomalous retroesophageal brachiocephalic artery
  • Vein absent
  • Venous anomaly of umbilical cord
  • Venous remnant
  • Verrucous epidermal nevus
  • Weber's true diffuse phlebarteriectasis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q27.8: its own notes plus those printed at Q27 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Absence of peripheral vascular system
  • Atresia of peripheral vascular system
  • Congenital aneurysm (peripheral)
  • Congenital stricture, artery
  • Congenital varix

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • arteriovenous malformation (Q27.3-)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Q27 Other congenital malformations of peripheral vascular system applies to 12 codes
  • anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
  • anomalies of coronary vessels (Q24.5)
  • anomalies of pulmonary artery (Q25.5-Q25.7)
  • congenital retinal aneurysm (Q14.1)
  • hemangioma and lymphangioma (D18.-)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q27.8, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q27.8: they are not reported together with it, unless the two conditions are unrelated.

  • Q28 Other congenital malformations of circulatory system
    congenital aneurysm NOS (Q27.8)

Excludes2 1

These codes carry an Excludes2 note naming Q27.8: its condition is not part of those codes, and both may be reported when the patient has both.

  • Q28 Other congenital malformations of circulatory system
    congenital peripheral aneurysm (Q27.8)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.69 Oth spcf prph vscl anoml
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q27.8Overview

What is the ICD-10 code for other specified congenital malformations of peripheral vascular system?

The ICD-10-CM code for other specified congenital malformations of peripheral vascular system is Q27.8 (sometimes written as Q278). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q27.8 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of peripheral vascular system on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q27.8 group to?

When other specified congenital malformations of peripheral vascular system is the principal diagnosis on an inpatient stay, it groups to MS-DRG 301, 300, 299, with relative weights from 0.7132 to 1.5840 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of peripheral vascular system on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.

Can Q27.8 be reported with a code from Q27.3?

Not as a rule. The Excludes1 note on Q27.8 lists "arteriovenous malformation (Q27.3-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).