2026 ICD-10-CM Diagnosis Code Q27.8Other specified congenital malformations of peripheral vascular system

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.8
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q27.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of peripheral vascular system. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of peripheral vascular system
Short Description
Oth congenital malformations of peripheral vascular system
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.8Other specified congenital malformations of peripheral vascular system

Present on Admission (POA)Billing

Q27.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aberrant origin of left subclavian artery
  • Aberrant retroesophageal brachiocephalic artery
  • Aberrant retro-esophageal subclavian artery causing dysphagia
  • Abnormal connection of hepatic vein to atrium
  • Absent venous duct
  • Agenesis of artery
  • Agenesis of internal carotid artery
  • Aneurysm osteoarthritis syndrome
  • Anomalous origin of left common carotid artery from brachiocephalic artery
  • Anomalous origin of right subclavian artery
  • Anomaly of umbilical vein group I
  • Anomaly of umbilical vein group II
  • Anomaly of umbilical vein group III
  • Anomaly of umbilical vein group IV
  • Aplasia of radial artery
  • Arterial embryological remnant
  • Atresia of systemic vein
  • Bilateral congenital anomaly of renal veins
  • CLAPO syndrome
  • Compression of esophagus
  • Compression of trachea
  • Congenital abnormality of hepatic vein
  • Congenital absence of artery
  • Congenital absence of azygos vein
  • Congenital absence of carotid artery
  • Congenital absence of innominate vein
  • Congenital absence of subclavian artery
  • Congenital absence of vein
  • Congenital aneurysm of systemic artery
  • Congenital anomaly of azygos vein
  • Congenital anomaly of blood vessel of lower limb
  • Congenital anomaly of blood vessel of spine
  • Congenital anomaly of blood vessel of upper limb
  • Congenital anomaly of left renal artery
  • Congenital anomaly of left renal vein
  • Congenital anomaly of renal blood vessel
  • Congenital anomaly of renal vein
  • Congenital anomaly of right renal artery
  • Congenital anomaly of right renal vein
  • Congenital arterial aneurysm
  • Congenital atresia of artery
  • Congenital atresia of vein
  • Congenital dilatation of carotid artery
  • Congenital dilatation of innominate artery
  • Congenital dilatation of subclavian artery
  • Congenital disruption of omphalomesenteric artery
  • Congenital elongation of innominate artery
  • Congenital malformation of left renal vein
  • Congenital malformation of renal vein
  • Congenital malformation of right renal vein
  • Congenital malposition of carotid artery
  • Congenital malposition of innominate artery
  • Congenital malposition of subclavian artery
  • Congenital occlusion of femoral vein
  • Congenital occlusion of iliac vein
  • Congenital peripheral aneurysm
  • Congenital phlebectasia
  • Congenital stenosis of carotid artery
  • Congenital stenosis of innominate artery
  • Congenital stenosis of subclavian artery
  • Congenital stricture of artery
  • Congenital stricture of retinal artery
  • Congenital transposition of azygos vein
  • Congenital varix
  • Congenital vascular anomaly of eye
  • Congenital vascular malformation due to inherited syndrome
  • Congenital vascular malformation of lip
  • Congenital vascular malformation of orbital region
  • Deep vein aplasia
  • Deep vein hypoplasia
  • Distal origin of brachiocephalic artery with tracheal compression
  • Distal origin of brachiocephalic trunk
  • Distended umbilical veins
  • Double artery
  • Ductus venosus abnormality
  • Dysphagia lusoria
  • Ectopic artery
  • Glomuvenous malformation
  • Hepatic vein to left atrium
  • Hepatic vein to left atrium and right atrium
  • Hepatic vein to right atrium
  • Hepatoportal microvascular dysplasia
  • Hypoplasia of artery
  • Isolation of brachiocephalic trunk
  • Isolation of branch of aortic arch
  • Isolation of common carotid artery
  • Isolation of left subclavian artery
  • Isolation of right common carotid artery
  • Isolation of right subclavian artery
  • Isolation of subclavian artery
  • Lethal arteriopathy syndrome due to fibulin-4 deficiency
  • Levoatrial cardinal vein
  • Mixed vascular malformation
  • Multiple dysplasia syndrome
  • Multiple venous malformation of skin and mucous membrane
  • NEVADA syndrome
  • Obstruction of femoral vein
  • Obstruction of iliac vein
  • Obstruction of peripheral vein
  • Occlusion of femoral vein
  • Occlusion of iliac vein
  • Peripheral congenital arteriovenous aneurysm
  • Peripheral venous malformation
  • Persistence of primitive artery
  • Persistent descending vein
  • Persistent embryonic proatlantal intersegmental artery
  • Persistent omphalomesenteric artery
  • Persistent vertical vein
  • Retroaortic brachiocephalic vein
  • Retroesophageal subclavian artery
  • Separate hepatic venous and inferior caval venous connections to heart
  • Specific mixed vascular syndrome
  • Splenoportal vascular anomaly
  • Stenosis of brachiocephalic artery
  • Stenosis of retinal artery
  • Stricture of artery
  • Subclavian artery stenosis
  • Supernumerary azygos vein
  • Systemic to pulmonary collateral artery connecting with artery
  • Systemic to pulmonary collateral artery connecting with central pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with isolated intraparenchymal pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with tracheobronchial arteries
  • Systemic to pulmonary collateral artery contributing to dual lung supply
  • Systemic to pulmonary collateral artery from left brachiocephalic artery
  • Systemic to pulmonary collateral artery from left carotid artery
  • Systemic to pulmonary collateral artery from left renal artery
  • Systemic to pulmonary collateral artery from right brachiocephalic artery
  • Systemic to pulmonary collateral artery from right carotid artery
  • Systemic to pulmonary collateral artery from right renal artery
  • Systemic venovenous collateral vein
  • True congenital varicose veins
  • Umbilical vein varix
  • Vascular compression of esophagus by aberrant artery
  • Vascular compression of esophagus by aberrant right subclavian artery arising from descending aorta
  • Vascular ring with right aortic arch and left arterial duct from anomalous retroesophageal brachiocephalic artery
  • Vein absent
  • Venous anomaly of umbilical cord
  • Venous remnant
  • Verrucous epidermal nevus
  • Weber's true diffuse phlebarteriectasis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Absence of peripheral vascular system
  • Atresia of peripheral vascular system
  • Congenital aneurysm (peripheral)
  • Congenital stricture, artery
  • Congenital varix

Type 1 Excludes

  • arteriovenous malformation Q27.3

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • artery (peripheral)
    • Aberrant(congenital)
      • artery (peripheral)
        • digestive system
    • Aberrant(congenital)
      • artery (peripheral)
        • lower limb
    • Aberrant(congenital)
      • artery (peripheral)
        • specified site NEC
    • Aberrant(congenital)
      • artery (peripheral)
        • subclavian
    • Aberrant(congenital)
      • artery (peripheral)
        • upper limb
    • Aberrant(congenital)
      • subclavian artery
    • Aberrant(congenital)
      • vein (peripheral) NEC
    • Aberrant(congenital)
      • vein (peripheral) NEC
        • digestive system
    • Aberrant(congenital)
      • vein (peripheral) NEC
        • lower limb
    • Aberrant(congenital)
      • vein (peripheral) NEC
        • specified site NEC
    • Aberrant(congenital)
      • vein (peripheral) NEC
        • upper limb
    • Absence(of) (organ or part) (complete or partial)
      • artery (congenital) (peripheral)
    • Absence(of) (organ or part) (complete or partial)
      • artery (congenital) (peripheral)
        • specified NEC
    • Absence(of) (organ or part) (complete or partial)
      • vein (peripheral) congenital NEC
    • Absence(of) (organ or part) (complete or partial)
      • vein (peripheral) congenital NEC
        • digestive system
    • Absence(of) (organ or part) (complete or partial)
      • vein (peripheral) congenital NEC
        • lower limb
    • Absence(of) (organ or part) (complete or partial)
      • vein (peripheral) congenital NEC
        • specified site NEC
    • Absence(of) (organ or part) (complete or partial)
      • vein (peripheral) congenital NEC
        • upper limb
    • Agenesis
      • artery (peripheral)
        • specified NEC
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
        • digestive system
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
        • lower limb
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
        • specified site NEC
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
        • upper limb
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • peripheral NEC
        • congenital
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • peripheral NEC
        • congenital
          • digestive system
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • peripheral NEC
        • congenital
          • lower limb
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • peripheral NEC
        • congenital
          • specified site NEC
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • peripheral NEC
        • congenital
          • upper limb
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • venous
        • congenital
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • venous
        • congenital
          • digestive system
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • venous
        • congenital
          • lower limb
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • venous
        • congenital
          • specified site NEC
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • venous
        • congenital
          • upper limb
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • digestive system
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • lower limb
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • peripheral
          • specified NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • specified site NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • subclavian
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • upper limb
    • Atresia, atretic
      • artery NEC
    • Atresia, atretic
      • artery NEC
        • digestive system
    • Atresia, atretic
      • artery NEC
        • lower limb
    • Atresia, atretic
      • artery NEC
        • specified site NEC
    • Atresia, atretic
      • artery NEC
        • upper limb
    • Atresia, atretic
      • vascular NEC
    • Atresia, atretic
      • vascular NEC
        • digestive system
    • Atresia, atretic
      • vascular NEC
        • lower limb
    • Atresia, atretic
      • vascular NEC
        • specified site NEC
    • Atresia, atretic
      • vascular NEC
        • upper limb
    • Atresia, atretic
      • vein NEC
    • Atresia, atretic
      • vein NEC
        • digestive system
    • Atresia, atretic
      • vein NEC
        • lower limb
    • Atresia, atretic
      • vein NEC
        • specified site NEC
    • Atresia, atretic
      • vein NEC
        • upper limb
    • Hypertrophy, hypertrophic
      • artery
        • congenital NEC
    • Hypertrophy, hypertrophic
      • artery
        • congenital NEC
          • digestive system
    • Hypertrophy, hypertrophic
      • artery
        • congenital NEC
          • lower limb
    • Hypertrophy, hypertrophic
      • artery
        • congenital NEC
          • specified site NEC
    • Hypertrophy, hypertrophic
      • artery
        • congenital NEC
          • upper limb
    • Hypoplasia, hypoplastic
      • artery (peripheral)
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • digestive system
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • lower limb
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • specified site NEC
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • upper limb
    • Hypoplasia, hypoplastic
      • peripheral vascular system
    • Hypoplasia, hypoplastic
      • peripheral vascular system
        • digestive system
    • Hypoplasia, hypoplastic
      • peripheral vascular system
        • lower limb
    • Hypoplasia, hypoplastic
      • peripheral vascular system
        • specified site NEC
    • Hypoplasia, hypoplastic
      • peripheral vascular system
        • upper limb
    • Hypoplasia, hypoplastic
      • vascular NEC peripheral
    • Hypoplasia, hypoplastic
      • vascular NEC peripheral
        • digestive system
    • Hypoplasia, hypoplastic
      • vascular NEC peripheral
        • lower limb
    • Hypoplasia, hypoplastic
      • vascular NEC peripheral
        • specified site NEC
    • Hypoplasia, hypoplastic
      • vascular NEC peripheral
        • upper limb
    • Hypoplasia, hypoplastic
      • vein (s) (peripheral)
    • Hypoplasia, hypoplastic
      • vein (s) (peripheral)
        • digestive system
    • Hypoplasia, hypoplastic
      • vein (s) (peripheral)
        • lower limb
    • Hypoplasia, hypoplastic
      • vein (s) (peripheral)
        • specified site NEC
    • Hypoplasia, hypoplastic
      • vein (s) (peripheral)
        • upper limb
    • Malformation(congenital)
      • peripheral vascular system
        • specified type NEC
    • Malposition
      • congenital
        • artery (peripheral)
    • Malposition
      • congenital
        • artery (peripheral)
          • digestive system
    • Malposition
      • congenital
        • artery (peripheral)
          • lower limb
    • Malposition
      • congenital
        • artery (peripheral)
          • specified site NEC
    • Malposition
      • congenital
        • artery (peripheral)
          • upper limb
    • Malposition
      • congenital
        • peripheral vascular system
    • Malposition
      • congenital
        • vein (s) (peripheral)
    • Stricture
      • artery
        • congenital (peripheral)
    • Stricture
      • artery
        • congenital (peripheral)
          • digestive system
    • Stricture
      • artery
        • congenital (peripheral)
          • lower limb
    • Stricture
      • artery
        • congenital (peripheral)
          • specified site NEC
    • Stricture
      • artery
        • congenital (peripheral)
          • upper limb
    • Varix(lower limb)
      • congenital (any site)
    • Varix(lower limb)
      • esophagus (idiopathic) (primary) (ulcerated)
        • congenital
    • Varix(lower limb)
      • orbit
        • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.69 Oth spcf prph vscl anoml
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q27.8Overview

Is Q27.8 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of peripheral vascular system on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q27.8 group to?

When other specified congenital malformations of peripheral vascular system is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of peripheral vascular system on inpatient claims.

What is the ICD-9 equivalent of Q27.8?

Under the General Equivalence Mappings, other specified congenital malformations of peripheral vascular system converts to ICD-9-CM 747.69 (oth spcf prph vscl anoml). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.