2026 ICD-10-CM Diagnosis Code Q26.2Total anomalous pulmonary venous connection

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q26

ICD-10-CM Q26.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q26.2 is a billable ICD-10-CM diagnosis code for total anomalous pulmonary venous connection. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q26.2
Billable Status
Yes — Valid for Submission
Code Describes
Total anomalous pulmonary venous connection
Short Description
Total anomalous pulmonary venous connection
Same as the full description in the CMS dataset.
Parent Code
Q26
Congenital malformations of great veins

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ26Congenital malformations of great veins
This CodeQ26.2Total anomalous pulmonary venous connection

Present on Admission (POA)Billing

Q26.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Anomalous pulmonary venous connection of mixed type
  • Divided left atrium with all pulmonary veins to proximal chamber and then to left atrium
  • Divided left atrium with all pulmonary veins to proximal chamber and then to left atrium with additional pulmonary venous chamber communication to right atrium
  • Infracardiac location of anomalous pulmonary venous connection
  • Infracardiac location of anomalous pulmonary venous connection to hepatic vein
  • Intracardiac location of anomalous pulmonary venous connection
  • Intracardiac location of anomalous pulmonary venous connection to coronary sinus
  • Intracardiac location of anomalous pulmonary venous connection to right atrium
  • Subdiaphragmatic total anomalous pulmonary venous return
  • Supracardiac location of anomalous pulmonary venous connection
  • Supradiaphragmatic total anomalous pulmonary venous return
  • Total anomalous pulmonary venous connection of infracardiac type
  • Total anomalous pulmonary venous connection of intracardiac type
  • Total anomalous pulmonary venous connection of supracardiac type
  • Total anomalous pulmonary venous connection to coronary sinus
  • Total anomalous pulmonary venous connection to hepatic vein
  • Total anomalous pulmonary venous connection to right atrium
  • Total anomalous pulmonary venous connection to superior vena cava
  • Total anomalous pulmonary venous connections of mixed type
  • Total anomalous pulmonary venous return

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Total anomalous pulmonary venous return TAPVR, subdiaphragmatic
  • Total anomalous pulmonary venous return TAPVR, supradiaphragmatic

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • connection
        • pulmonary venous
          • total
    • Anomaly, anomalous(congenital) (unspecified type)
      • pulmonary
        • venous connection
          • total
    • Atresia, atretic
      • vein NEC
        • pulmonary
          • total
    • Malformation(congenital)
      • great
        • vein
          • anomalous
            • pulmonary venous connection
              • total

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q26.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.41 Tot anom pulm ven connec
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q26.2Overview

Is Q26.2 (Congenital malformations of great veins) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report total anomalous pulmonary venous connection on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q26.2 group to?

When total anomalous pulmonary venous connection is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q26.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for total anomalous pulmonary venous connection on inpatient claims.

What is the ICD-9 equivalent of Q26.2?

Under the General Equivalence Mappings, total anomalous pulmonary venous connection converts to ICD-9-CM 747.41 (tot anom pulm ven connec). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.