ICD-10-CM Code Q26.8

Other congenital malformations of great veins

Version 2020 Billable Code POA Exempt

Valid for Submission

Q26.8 is a billable code used to specify a medical diagnosis of other congenital malformations of great veins. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q26.8 might also be used to specify conditions or terms like abnormal inferior vena caval connection, abnormality of right inferior caval vein, abnormality of right inferior caval vein, abnormality of right inferior caval vein, abnormality of right superior vena cava, abnormality of right superior vena cava, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

ICD-10:Q26.8
Short Description:Other congenital malformations of great veins
Long Description:Other congenital malformations of great veins

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q26.8:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q26.8 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abnormal inferior vena caval connection
  • Abnormality of right inferior caval vein
  • Abnormality of right inferior caval vein
  • Abnormality of right inferior caval vein
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Absence of inferior vena cava
  • Absence of superior vena cava
  • Absent bridging vein
  • Absent right superior vena cava
  • Anomalous insertion of right superior vena cava to left atrium
  • Atresia of left superior caval vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atretic right superior vena cava
  • Azygos continuation of inferior caval vein to right superior caval vein
  • Bilateral superior vena cava
  • Congenital abnormality of great veins and coronary sinus
  • Congenital abnormality of great veins and coronary sinus
  • Congenital abnormality of hepatic vein
  • Congenital absence of inferior vena cava
  • Congenital absence of superior vena cava
  • Congenital absence of vena cava
  • Congenital atresia of inferior vena cava
  • Congenital atresia of superior vena cava
  • Congenital dilatation of inferior vena cava
  • Congenital dilatation of superior vena cava
  • Congenital hypoplasia of cardiac vein
  • Congenital hypoplasia of pulmonary artery
  • Congenital malposition of inferior vena cava
  • Congenital malposition of superior vena cava
  • Congenital pulmonary venous atrium
  • Congenital stenosis of pulmonary veins
  • Congenital systemic venous atrium
  • Hypoplasia of cardiac vein
  • Inferior cava to left of spine with right descending aorta
  • Inferior caval vein anterior and same side as descending aorta
  • Inferior caval vein connecting to right atrium and left atrium
  • Inferior vena cava connecting to coronary sinus
  • Inferior vena cava connecting to morphological left atrium
  • Inferior vena cava interruption with bilateral azygos continuation
  • Inferior vena cava interruption with left sided hemiazygos continuation
  • Inferior vena cava interruption with right sided azygos continuation
  • Inferior vena cava to left of spine
  • Interrupted left inferior caval vein
  • Interrupted right inferior caval vein
  • Left inferior caval vein connecting to left atrium and right atrium
  • Left sided azygos continuation of inferior caval vein to left superior caval vein
  • Obstructive Eustachian valve
  • Persistent common pulmonary vein
  • Persistent left posterior cardinal vein
  • Prolapse of Eustachian valve
  • Prominent valve of inferior vena cava
  • Prominent valve of inferior vena cava
  • Pulmonary vein stenosis
  • Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
  • Pulmonary venous hypoplasia
  • Right inferior caval vein connecting to left atrium and right atrium
  • Right inferior caval vein connecting to left sided atrium
  • Right superior caval vein connecting to coronary sinus
  • Right superior caval vein connecting to coronary sinus and then to left sided atrium
  • Right superior caval vein connecting to left atrium and right atrium
  • Right superior caval vein persisting to coronary sinus and then to right sided atrium
  • Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
  • Scimitar syndrome
  • Scimitar syndrome with additional anomalous pulmonary venous connection
  • Separate hepatic venous and inferior caval venous connections to heart
  • Sinus venosus atrial septal defect
  • Sinus venosus atrial septal defect
  • Sinus venosus defect with overriding inferior vena cava
  • Sinus venosus defect with overriding superior vena cava
  • Transposition of inferior vena cava
  • Venous valvular anomaly
  • Venous valvular anomaly

Diagnostic Related Groups

The ICD-10 code Q26.8 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.

  • 306 - CARDIAC CONGENITAL AND VALVULAR DISORDERS WITH MCC
  • 307 - CARDIAC CONGENITAL AND VALVULAR DISORDERS WITHOUT MCC

Present on Admission (POA)

Q26.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q26.8 to ICD-9

  • 747.49 - Great vein anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great veins (Q26)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

  • Rapid breathing
  • Cyanosis - a bluish tint to the skin, lips, and fingernails
  • Fatigue
  • Poor blood circulation

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute


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