2027 ICD-10-CM Diagnosis Code Q25.72Congenital pulmonary arteriovenous malformation

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.72
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25.72 is a billable ICD-10-CM diagnosis code for congenital pulmonary arteriovenous malformation. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 11 closely related codes. The code is exempt from POA reporting. Coders also document this condition as associated pulmonary arterial hypertension. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.72
Billable Status
Yes — Valid for Submission
Code Describes
Congenital pulmonary arteriovenous malformation
Short Description
Congenital pulmonary arteriovenous malformation
Same as the full description in the CMS dataset.
Parent Code
Q25.7
Other congenital malformations of pulmonary artery

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.72Congenital pulmonary arteriovenous malformation

Present on Admission (POA)Billing

Q25.72 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Associated pulmonary arterial hypertension
  • Congenital dilatation of pulmonary artery
  • Congenital pulmonary arteriovenous aneurysm
  • Congenital pulmonary artery aneurysm
  • Dilatation of pulmonary artery
  • Pulmonary arterial hypertension associated with congenital heart disease
  • Pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt
  • Pulmonary artery aneurysm

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25.72: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital pulmonary arteriovenous aneurysm

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q25.72, its category, or a range that includes it.

Excludes1 2

These codes carry an Excludes1 note naming Q25.72: they are not reported together with it, unless the two conditions are unrelated.

  • I28.0 Arteriovenous fistula of pulmonary vessels
    congenital arteriovenous fistula (Q25.72)
  • I28.1 Aneurysm of pulmonary artery
    congenital arteriovenous aneurysm (Q25.72)

Excludes2 1

These codes carry an Excludes2 note naming Q25.72: its condition is not part of those codes, and both may be reported when the patient has both.

  • Q27 Other congenital malformations of peripheral vascular system
    anomalies of pulmonary artery (Q25.5-Q25.7) names Q25.5-Q25.7, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Arteriovenous Malformations

Arteriovenous malformations (AVMs) are defects in your vascular system. Your vascular system is your body's network of blood vessels. It includes your:

The full article covers:

  • What are arteriovenous malformations (AVMs)?
  • What causes arteriovenous malformations (AVMs)?
  • What are the symptoms of arteriovenous malformations (AVMs)?
  • How are arteriovenous malformations (AVMs) diagnosed?
  • What are the treatments for arteriovenous malformations (AVMs)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.72 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.32 Pulmonary AV malformatn
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25.72Overview

What is the ICD-10 code for congenital pulmonary arteriovenous malformation?

The ICD-10-CM code for congenital pulmonary arteriovenous malformation is Q25.72 (sometimes written as Q2572). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q25.72 (Other congenital malformations of pulmonary artery) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital pulmonary arteriovenous malformation on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q25.72 group to?

When congenital pulmonary arteriovenous malformation is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.72 a CC or MCC?

CMS lists Q25.72 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 11 closely related codes in its exclusion list.

Is Q25.72 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital pulmonary arteriovenous malformation on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.