2026 ICD-10-CM Diagnosis Code Q25.72Congenital pulmonary arteriovenous malformation

ICD-10-CM CodesQ00-Q99Q20-Q28Q25

ICD-10-CM Q25.72
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.72 is a billable ICD-10-CM diagnosis code for congenital pulmonary arteriovenous malformation. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. Coders also document this condition as associated pulmonary arterial hypertension. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.72
Billable Status
Yes — Valid for Submission
Code Describes
Congenital pulmonary arteriovenous malformation
Short Description
Congenital pulmonary arteriovenous malformation
Same as the full description in the CMS dataset.
Parent Code
Other congenital malformations of pulmonary artery

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.72Congenital pulmonary arteriovenous malformation

Present on Admission (POA)Billing

Q25.72 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Associated pulmonary arterial hypertension
  • Congenital dilatation of pulmonary artery
  • Congenital pulmonary arteriovenous aneurysm
  • Congenital pulmonary artery aneurysm
  • Dilatation of pulmonary artery
  • Pulmonary arterial hypertension associated with congenital heart disease
  • Pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt
  • Pulmonary artery aneurysm

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital pulmonary arteriovenous aneurysm

Index to Diseases and InjuriesGuidance

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • pulmonary
        • arteriovenous
    • Communication
      • between
        • pulmonary artery and pulmonary vein, congenital
    • Fistula(cutaneous)
      • arteriovenous (acquired) (nonruptured)
        • congenital (peripheral)
          • pulmonary
    • Fistula(cutaneous)
      • arteriovenous (acquired) (nonruptured)
        • pulmonary
          • congenital
    • Fistula(cutaneous)
      • pulmonary
        • arteriovenous
          • congenital
    • Malformation(congenital)
      • pulmonary
        • arteriovenous
    • Shunt
      • arteriovenous, pulmonary (acquired)
        • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Arteriovenous Malformations

Arteriovenous malformations (AVMs) are defects in your vascular system. Your vascular system is your body's network of blood vessels. It includes your:

The full article covers:

  • What are arteriovenous malformations (AVMs)?
  • What causes arteriovenous malformations (AVMs)?
  • What are the symptoms of arteriovenous malformations (AVMs)?
  • How are arteriovenous malformations (AVMs) diagnosed?
  • What are the treatments for arteriovenous malformations (AVMs)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.72 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.32 Pulmonary AV malformatn
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.72Overview

Is Q25.72 (Other congenital malformations of pulmonary artery) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital pulmonary arteriovenous malformation on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.72 group to?

When congenital pulmonary arteriovenous malformation is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.72 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital pulmonary arteriovenous malformation on inpatient claims.

What is the ICD-9 equivalent of Q25.72?

Under the General Equivalence Mappings, congenital pulmonary arteriovenous malformation converts to ICD-9-CM 747.32 (pulmonary AV malformatn). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.