2026 ICD-10-CM Diagnosis Code Q25.40Congenital malformation of aorta unspecified

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.40
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.40 is a billable ICD-10-CM diagnosis code for congenital malformation of aorta unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. Coders also document this condition as aortic arch anomaly, facial dysmorphism, intellectual disability syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.40
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of aorta unspecified
Short Description
Congenital malformation of aorta unspecified
Same as the full description in the CMS dataset.
Parent Code
Q25.4
Other congenital malformations of aorta

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.40Congenital malformation of aorta unspecified

Present on Admission (POA)Billing

Q25.40 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aortic arch anomaly, facial dysmorphism, intellectual disability syndrome
  • Compression of esophagus
  • Compression of trachea
  • Compression of trachea and esophagus co-occurrent and due to congenital anomaly of aortic arch
  • Congenital anomaly of abdominal aorta
  • Congenital anomaly of aortic arch AND/OR descending aorta
  • Congenital anomaly of descending thoracic aorta
  • Dextrotransposition of aorta
  • Disorder of ascending aorta due to conotruncal malformation
  • Right aortic arch

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • aorta (arch) NEC
    • Deformity
      • aorta (arch) (congenital)
    • Malformation(congenital)
      • aorta

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Right Aortic Arch

    an anatomic abnormality that occurs during embryonic development, in which the aortic arch is right-sided.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.40 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.20 Cong anom of aorta NOS
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement Q25.40 replaces the following previously assigned code(s):

  • Q25.4 - Other congenital malformations of aorta
FY 2018AddedAdded to the ICD-10-CM code setEffective October 1, 2017.
FY 2019–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.40Overview

Is Q25.40 (Other congenital malformations of aorta) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of aorta unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.40 group to?

When congenital malformation of aorta unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.40 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of aorta unspecified on inpatient claims.

What is the ICD-9 equivalent of Q25.40?

Under the General Equivalence Mappings, congenital malformation of aorta unspecified converts to ICD-9-CM 747.20 (cong anom of aorta NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.