2027 ICD-10-CM Diagnosis Code Q25.1Coarctation of aorta

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25.1 is a billable ICD-10-CM diagnosis code for coarctation of aorta. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 45 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.1
Billable Status
Yes — Valid for Submission
Code Describes
Coarctation of aorta
Short Description
Coarctation of aorta
Same as the full description in the CMS dataset.
Parent Code
Q25
Congenital malformations of great arteries

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.1Coarctation of aorta

Present on Admission (POA)Billing

Q25.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abdominal aortic coarctation
  • Abnormality within thorax due to coarctation of aorta
  • Abscess at site of aortic coarctation
  • Abscess of aorta
  • Coarctation of aorta
  • Coarctation of aorta between left common carotid artery and right common carotid artery
  • Coarctation of aorta between subclavian artery and common carotid artery
  • Coarctation of aortic arch
  • Coarctation of infrarenal abdominal aorta
  • Coarctation of suprarenal abdominal aorta
  • Common arterial trunk with pulmonary dominance
  • Common arterial trunk with pulmonary dominance and aortic coarctation
  • Congenital anomaly of abdominal aorta
  • Congenital stenosis of aorta
  • Congenital stenosis of aortic arch
  • Double aortic arch with left arch dominant
  • Double aortic arch with left arch dominant and coarctation of right arch
  • Double aortic arch with right arch dominant
  • Double aortic arch with right arch dominant and coarctation of left arch
  • Endarteritis
  • Infantile hemangioma
  • Infective aortitis
  • Infective endarteritis at site of aortic coarctation
  • Juxtaductal aortic coarctation
  • Parachute malformation of mitral valve
  • PHACE syndrome
  • Postductal coarctation of aorta
  • Preductal coarctation of aorta
  • Secondary aortitis
  • Shone complex
  • Stenosis of thoracic aorta
  • Supramitral left atrial ring
  • Thoracic aortic coarctation

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25.1: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Coarctation of aorta (preductal) (postductal)
  • Stenosis of aorta

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Aortic Coarctation

    a birth defect characterized by the narrowing of the aorta that can be of varying degree and at any point from the transverse arch to the iliac bifurcation. aortic coarctation causes arterial hypertension before the point of narrowing and arterial hypotension beyond the narrowed portion.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.10 Coarctation of aorta
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25.1Overview

What is the ICD-10 code for coarctation of aorta?

The ICD-10-CM code for coarctation of aorta is Q25.1 (sometimes written as Q251). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q25.1 (Congenital malformations of great arteries) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report coarctation of aorta on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q25.1 group to?

When coarctation of aorta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.1 a CC or MCC?

CMS lists Q25.1 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 45 closely related codes in its exclusion list.

Is Q25.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for coarctation of aorta on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.