2026 ICD-10-CM Diagnosis Code Q25.1Coarctation of aorta

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.1 is a billable ICD-10-CM diagnosis code for coarctation of aorta. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.1
Billable Status
Yes — Valid for Submission
Code Describes
Coarctation of aorta
Short Description
Coarctation of aorta
Same as the full description in the CMS dataset.
Parent Code
Q25
Congenital malformations of great arteries

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.1Coarctation of aorta

Present on Admission (POA)Billing

Q25.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abdominal aortic coarctation
  • Abnormality within thorax due to coarctation of aorta
  • Abscess at site of aortic coarctation
  • Abscess of aorta
  • Coarctation of aorta
  • Coarctation of aorta between left common carotid artery and right common carotid artery
  • Coarctation of aorta between subclavian artery and common carotid artery
  • Coarctation of aortic arch
  • Coarctation of infrarenal abdominal aorta
  • Coarctation of suprarenal abdominal aorta
  • Common arterial trunk with pulmonary dominance
  • Common arterial trunk with pulmonary dominance and aortic coarctation
  • Congenital anomaly of abdominal aorta
  • Congenital stenosis of aorta
  • Congenital stenosis of aortic arch
  • Double aortic arch with left arch dominant
  • Double aortic arch with left arch dominant and coarctation of right arch
  • Double aortic arch with right arch dominant
  • Double aortic arch with right arch dominant and coarctation of left arch
  • Endarteritis
  • Infantile hemangioma
  • Infective aortitis
  • Infective endarteritis at site of aortic coarctation
  • Juxtaductal aortic coarctation
  • Parachute malformation of mitral valve
  • PHACE syndrome
  • Postductal coarctation of aorta
  • Preductal coarctation of aorta
  • Shone complex
  • Stenosis of thoracic aorta
  • Supramitral left atrial ring
  • Thoracic aortic coarctation

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Coarctation of aorta (preductal) (postductal)
  • Stenosis of aorta

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • aorta (arch) NEC
        • coarctation (preductal) (postductal)
    • Coarctation
      • aorta (preductal) (postductal)
    • Malformation(congenital)
      • aorta
        • coarctation (preductal) (postductal)
    • Malformation(congenital)
      • aorta
        • stenosis
    • Stenosis, stenotic(cicatricial)
      • aorta (ascending) (supraventricular) (congenital)
    • Stricture
      • aorta (ascending) (congenital)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Endarteritis

    inflammation of the inner endothelial lining (tunica intima) of an artery.

  • Tunica Intima

    the innermost layer of an artery or vein, made up of one layer of endothelial cells and supported by an internal elastic lamina.

  • Endarteritis

    inflammation of the arterial intima.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.10 Coarctation of aorta
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.1Overview

Is Q25.1 (Congenital malformations of great arteries) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report coarctation of aorta on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.1 group to?

When coarctation of aorta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for coarctation of aorta on inpatient claims.

What is the ICD-9 equivalent of Q25.1?

Under the General Equivalence Mappings, coarctation of aorta converts to ICD-9-CM 747.10 (coarctation of aorta). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.