2027 ICD-10-CM Diagnosis Code Q13.4Other congenital corneal malformations

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13

ICD-10-CM Q13.4
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q13.4 is a billable ICD-10-CM diagnosis code for other congenital corneal malformations. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q13.4
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital corneal malformations
Short Description
Other congenital corneal malformations
Same as the full description in the CMS dataset.
Parent Code
Q13
Congenital malformations of anterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ13Congenital malformations of anterior segment of eye
This CodeQ13.4Other congenital corneal malformations

Present on Admission (POA)Billing

Q13.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of eye, ear, face and neck (Q10-Q18).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arcus juvenilis
  • Arcus of cornea
  • Bilateral cornea plana
  • Cataract and microcornea syndrome
  • Chorioretinal atrophy
  • Colobomatous macrophthalmia with microcornea syndrome
  • Congenital anomaly of nasal sinuses
  • Congenital anomaly of sclera
  • Congenital anterior staphyloma
  • Congenital aphakia
  • Congenital aphakia, iris hypoplasia, microphthalmia, microcornea syndrome
  • Congenital arcus juvenilis
  • Congenital cataract microcornea with corneal opacity
  • Congenital coloboma of iris
  • Congenital coloboma of optic disc
  • Congenital keratoconus
  • Congenital keratoconus posticus circumscriptus
  • Congenital keratoglobus
  • Congenital structural abnormality of bilateral corneas
  • Congenital structural abnormality of cornea
  • Congenital structural abnormality of left cornea
  • Congenital structural abnormality of right cornea
  • Cornea plana
  • Corneal size and shape anomalies
  • Corneal staphyloma
  • Corneal thinning
  • Ectasia of sclera
  • Embryotoxon
  • Familial renal glucosuria
  • Fundus coloboma
  • Glaucoma and corneal anomaly
  • Infantile and/or juvenile cataract
  • Irido-corneo-trabecular dysgenesis
  • Juvenile cataract
  • Juvenile cataract, microcornea, renal glucosuria syndrome
  • Keratoglobus
  • Lenticonus
  • Macrophthalmos
  • Megalocornea
  • Megalocornea, spherophakia, secondary glaucoma syndrome
  • Microcornea
  • Microcornea of bilateral eyes
  • Microcornea with corectopia and macular hypoplasia syndrome
  • Microcornea with glaucoma and absent frontal sinus syndrome
  • Microcornea, myopic chorioretinal atrophy, telecanthus syndrome
  • Microcornea, posterior megalolenticonus, persistent fetal vasculature, coloboma syndrome
  • Microcornea, rod-cone dystrophy, cataract, posterior staphyloma syndrome
  • Peters plus syndrome
  • Posterior embryotoxon
  • Posterior lenticonus
  • Renal glycosuria
  • Seemanova Lesny syndrome
  • Uveal prolapse

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q13.4: its own notes plus those printed at block Q10-Q18 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital malformation of cornea NOS
  • Microcornea
  • Peter's anomaly

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Block Q10-Q18 Congenital malformations of eye, ear, face and neck applies to 62 codes
  • cleft lip and cleft palate (Q35-Q37)
  • congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
  • congenital malformation of larynx (Q31.-)
  • congenital malformation of lip NEC (Q38.0)
  • congenital malformation of nose (Q30.-)
  • congenital malformation of parathyroid gland (Q89.2)
  • congenital malformation of thyroid gland (Q89.2)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q13.4, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q13.4: they are not reported together with it, unless the two conditions are unrelated.

  • H18.7 Other and unspecified corneal deformities
    congenital malformations of cornea (Q13.3-Q13.4) names Q13.3-Q13.4, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q13.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.41 Anom corneal size/shape
Approximate The match is approximate rather than exact.
ICD-9-CM
743.44 Anom anter chamber-eye
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q13.4Overview

What is the ICD-10 code for other congenital corneal malformations?

The ICD-10-CM code for other congenital corneal malformations is Q13.4 (sometimes written as Q134). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q13.4 (Congenital malformations of anterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital corneal malformations on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q13.4 group to?

When other congenital corneal malformations is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q13.4 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital corneal malformations on inpatient claims. The code appears in the Congenital malformations of eye, ear, face and neck (Q10-Q18) range of the CMS exempt list.

What is the ICD-9 equivalent of Q13.4?

Under the General Equivalence Mappings, other congenital corneal malformations converts to ICD-9-CM 743.41 (anom corneal size/shape) and 743.44 (anom anter chamber-eye). The mapping is approximate, so confirm the match fits the documentation.