2026 ICD-10-CM Diagnosis Code Q13.4Other congenital corneal malformations

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13

ICD-10-CM Q13.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q13.4 is a billable ICD-10-CM diagnosis code for other congenital corneal malformations. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q13.4
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital corneal malformations
Short Description
Other congenital corneal malformations
Same as the full description in the CMS dataset.
Parent Code
Q13
Congenital malformations of anterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ13Congenital malformations of anterior segment of eye
This CodeQ13.4Other congenital corneal malformations

Present on Admission (POA)Billing

Q13.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arcus juvenilis
  • Arcus of cornea
  • Bilateral cornea plana
  • Cataract and microcornea syndrome
  • Chorioretinal atrophy
  • Colobomatous macrophthalmia with microcornea syndrome
  • Congenital anomaly of nasal sinuses
  • Congenital anomaly of sclera
  • Congenital anterior staphyloma
  • Congenital aphakia
  • Congenital aphakia, iris hypoplasia, microphthalmia, microcornea syndrome
  • Congenital arcus juvenilis
  • Congenital cataract microcornea with corneal opacity
  • Congenital coloboma of iris
  • Congenital coloboma of optic disc
  • Congenital keratoconus
  • Congenital keratoconus posticus circumscriptus
  • Congenital keratoglobus
  • Congenital structural abnormality of bilateral corneas
  • Congenital structural abnormality of cornea
  • Congenital structural abnormality of left cornea
  • Congenital structural abnormality of right cornea
  • Cornea plana
  • Corneal size and shape anomalies
  • Corneal staphyloma
  • Corneal thinning
  • Ectasia of sclera
  • Embryotoxon
  • Familial renal glucosuria
  • Fundus coloboma
  • Glaucoma and corneal anomaly
  • Infantile and/or juvenile cataract
  • Irido-corneo-trabecular dysgenesis
  • Juvenile cataract
  • Juvenile cataract, microcornea, renal glucosuria syndrome
  • Keratoglobus
  • Lenticonus
  • Macrophthalmos
  • Megalocornea
  • Megalocornea, spherophakia, secondary glaucoma syndrome
  • Microcornea
  • Microcornea of bilateral eyes
  • Microcornea with corectopia and macular hypoplasia syndrome
  • Microcornea with glaucoma and absent frontal sinus syndrome
  • Microcornea, myopic chorioretinal atrophy, telecanthus syndrome
  • Microcornea, posterior megalolenticonus, persistent fetal vasculature, coloboma syndrome
  • Microcornea, rod-cone dystrophy, cataract, posterior staphyloma syndrome
  • Peters plus syndrome
  • Posterior embryotoxon
  • Posterior lenticonus
  • Renal glycosuria
  • Seemanova Lesny syndrome
  • Uveal prolapse

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital malformation of cornea NOS
  • Microcornea
  • Peter's anomaly

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • cornea (shape)
    • Anomaly, anomalous(congenital) (unspecified type)
      • Peter's
    • Axenfeld's
      • degeneration (calcareous)
    • Cornea
      • plana
    • Deformity
      • cornea (acquired)
        • congenital
    • Embryotoxon
    • Irregular, irregularity
      • contour of cornea (acquired)
        • congenital
    • Keratectasia
      • congenital
    • Keratoconus
      • congenital
    • Keratomegaly
    • Malformation(congenital)
      • cornea
    • Melanosis
      • cornea (presenile) (senile)
        • congenital
    • Microcornea(congenital)
    • Peter's anomaly

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Microcornea

    a congenital abnormality characterized by an abnormally small cornea. the horizontal corneal diameter is less than 10mm or less than 9mm in newborns. it is associated with an increased risk of glaucoma.

  • Congenital Aphakia

    the absence of the lens of the eye that is present at the time of birth.

  • Uveal Prolapse

    the protrusion of uveal tissue through an opening in the sclera.

  • Corneal Thinning

    progressive deformation of the corneal structure, characterized by thinning of the cornea.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q13.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.41 Anom corneal size/shape
Approximate The match is approximate rather than exact.
ICD-9-CM
743.44 Anom anter chamber-eye
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q13.4Overview

Is Q13.4 (Congenital malformations of anterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital corneal malformations on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q13.4 group to?

When other congenital corneal malformations is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q13.4 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital corneal malformations on inpatient claims.

What is the ICD-9 equivalent of Q13.4?

Under the General Equivalence Mappings, other congenital corneal malformations converts to ICD-9-CM 743.41 (anom corneal size/shape) and 743.44 (anom anter chamber-eye). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.